2024 ICD-10-CM Diagnosis Code Q13.4

Other congenital corneal malformations

ICD-10-CM Code:
Q13.4
ICD-10 Code for:
Other congenital corneal malformations
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities
    (Q00-Q99)
    • Congenital malformations of eye, ear, face and neck
      (Q10-Q18)
      • Congenital malformations of anterior segment of eye
        (Q13)

Q13.4 is a billable diagnosis code used to specify a medical diagnosis of other congenital corneal malformations. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024. The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Arcus juvenilis
  • Arcus of cornea
  • Bilateral congenital anomaly of corneas
  • Bilateral cornea plana
  • Cataract and microcornea syndrome
  • Chorioretinal atrophy
  • Colobomatous macrophthalmia with microcornea syndrome
  • Congenital anomaly of cornea
  • Congenital anomaly of nasal sinuses
  • Congenital anterior staphyloma
  • Congenital arcus juvenilis
  • Congenital coloboma of iris
  • Congenital coloboma of optic disc
  • Congenital keratoconus
  • Congenital keratoconus posticus circumscriptus
  • Congenital keratoglobus
  • Cornea plana
  • Corneal size and shape anomalies
  • Corneal staphyloma
  • Embryotoxon
  • Familial renal glucosuria
  • Glaucoma and corneal anomaly
  • Glaucoma associated with anterior segment anomaly
  • Infantile and/or juvenile cataract
  • Irido-corneo-trabecular dysgenesis
  • Juvenile cataract
  • Juvenile cataract, microcornea, renal glucosuria syndrome
  • Lenticonus
  • Macrophthalmos
  • Megalocornea
  • Megalocornea
  • Megalocornea, spherophakia, secondary glaucoma syndrome
  • Microcornea
  • Microcornea
  • Microcornea
  • Microcornea
  • Microcornea
  • Microcornea
  • Microcornea
  • Microcornea
  • Microcornea
  • Microcornea of bilateral eyes
  • Microcornea with corectopia and macular hypoplasia syndrome
  • Microcornea with glaucoma and absent frontal sinus syndrome
  • Microcornea, myopic chorioretinal atrophy, telecanthus syndrome
  • Microcornea, posterior megalolenticonus, persistent fetal vasculature, coloboma syndrome
  • Microcornea, rod-cone dystrophy, cataract, posterior staphyloma syndrome
  • Peters plus syndrome
  • Posterior embryotoxon
  • Posterior lenticonus
  • Renal glycosuria
  • Seemanova Lesny syndrome

Clinical Classification

Clinical Information

  • Microcornea

    a congenital abnormality characterized by an abnormally small cornea. the horizontal corneal diameter is less than 10mm or less than 9mm in newborns. it is associated with an increased risk of glaucoma.

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Congenital malformation of cornea NOS
  • Microcornea
  • Peter's anomaly

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Present on Admission (POA)

Q13.4 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here.

CMS POA Indicator Options and Definitions

POA IndicatorReason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Convert Q13.4 to ICD-9-CM

  • ICD-9-CM Code: 743.41 - Anom corneal size/shape
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.
  • ICD-9-CM Code: 743.44 - Anom anter chamber-eye
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education


Corneal Disorders

Your cornea is the outermost layer of your eye. It is clear and shaped like a dome. The cornea helps to shield the rest of the eye from germs, dust, and other harmful matter. It also helps your eye to focus. If you wear contact lenses, they float on top of your corneas.

Problems with the cornea include:

  • Refractive errors
  • Allergies
  • Infections
  • Injuries
  • Dystrophies - conditions in which parts of the cornea lose clarity due to a buildup of cloudy material

Treatments of corneal disorders include medicines, corneal transplantation, and corneal laser surgery.

NIH: National Eye Institute


[Learn More in MedlinePlus]

Peters anomaly

Peters anomaly is characterized by eye problems that occur in an area at the front part of the eye known as the anterior segment. The anterior segment consists of structures including the lens, the colored part (iris) of the eye, and the clear covering of the eye (cornea). During development of the eye, the elements of the anterior segment form separate structures. However, in Peters anomaly, development of the anterior segment is abnormal, leading to incomplete separation of the cornea from the iris or the lens. As a result, the cornea is cloudy (opaque), which causes blurred vision. The opaque area (opacity) of the cornea varies in size and intensity from a small, faint streak to a large, white cloudy area that covers the front surface of the eye. Additionally, the location of the opacity varies; the cloudiness may be at the center of the cornea or off-center. Large, centrally located opacities tend to cause poorer vision than smaller, off-center ones.

Nearly half of the individuals affected with Peters anomaly have low vision early in life and about a quarter are legally blind. Due to a lack of visual stimulation, some individuals develop "lazy eye" (amblyopia). Peters anomaly is often associated with other eye problems, such as increased pressure within the eye (glaucoma), clouding of the lens (cataract), and unusually small eyeballs (microphthalmia). In most cases, Peters anomaly is bilateral, which means that it affects both eyes, although the level of vision impairment may be different in each eye. These individuals may have eyes that do not point in the same direction (strabismus). In some people with Peters anomaly, corneal clouding improves over time leading to improved vision.

There are two types of Peters anomaly, which are distinguished by their signs and symptoms. Peters anomaly type I is characterized by an incomplete separation of the cornea and iris and mild to moderate corneal opacity. Type II is characterized by an incomplete separation of the cornea and lens and severe corneal opacity that may involve the entire cornea.


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.