Anophthalmos, microphthalmos and macrophthalmos (Q11) ICD-10-CM
The Q11 code range covers anophthalmos, microphthalmos and macrophthalmos with 5 ICD-10-CM diagnosis codes. 4 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Codes in the Q11 Range 5 codes · 4 billable
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q11 range.
Anophthalmos
Congenital absence of the eye or eyes.
Microphthalmos
Congenital or developmental anomaly in which the eyeballs are abnormally small.
About the Q11 Code Range
The ICD-10 code Q11 series covers congenital conditions affecting eye size and development, including anophthalmos, microphthalmos, and macrophthalmos. These codes are used to classify specific malformations where one or both eyes are absent, abnormally small, or abnormally large.
The code Q11.0 identifies the cystic eyeball, also known as congenital cystic eyeball or congenital cyst of orbit, representing a rare congenital malformation. Code Q11.1 covers other forms of anophthalmos, which is the complete absence of ocular tissue, including cases described by synonyms such as SOX2 anophthalmia syndrome or bilateral anophthalmos. Q11.2 classifies microphthalmos, a condition of abnormally small eyes, linked with numerous syndromes like Delleman and Fryns syndrome; synonyms include microphthalmia and syndromic nanophthalmos. Lastly, Q11.3 refers to macrophthalmos, which denotes abnormally large eyes, sometimes associated with conditions like congenital coloboma of the optic disc or iris. Medical coders can rely on these ICD-10 codes to accurately document and distinguish these developmental eye disorders.
Questions About This Page
How many billable codes are in the Q11 range?
Of the 5 codes in this range, 4 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the Q11 range classify?
The range classifies anophthalmos, microphthalmos and macrophthalmos. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
