Congenital malformations of posterior segment of eye (Q14) ICD-10-CM
The Q14 code range covers congenital malformations of posterior segment of eye with 7 ICD-10-CM diagnosis codes. 6 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
- optic nerve hypoplasia H47.03
Codes in the Q14 Range 7 codes · 6 billable
- Q14 Congenital malformations of posterior segment of eyeNon-billable
- Q14.0 Congenital malformation of vitreous humor
- Q14.1 Congenital malformation of retina
- Q14.2 Congenital malformation of optic disc
- Q14.3 Congenital malformation of choroid
- Q14.8 Other congenital malformations of posterior segment of eye
- Q14.9 Congenital malformation of posterior segment of eye, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q14 range.
Persistent Hyperplastic Primary Vitreous
A developmental ocular anomaly in which the primary VITREOUS BODY and its surrounding hyaloid vasculature failed to regress. It is usually unilateral and characterized by CATARACT; MICROPHTHALMOS (small eyeballs), and retrolenticular fibrovascular tissue. (from Yanoff: Ophthalmology, 2nd ed.)
Retinal Dysplasia
Congenital, often bilateral, retinal abnormality characterized by the arrangement of outer nuclear retinal cells in a palisading or radiating pattern surrounding a central ocular space. This disorder is sometimes hereditary.
About the Q14 Code Range
The ICD-10 code Q14 category covers congenital malformations affecting the posterior segment of the eye, including abnormalities of the vitreous humor, retina, optic disc, and choroid. These codes are used to specify and classify various birth defects related to the back part of the eye structure.
Within this category, codes such as Q14.0 describe malformations of the vitreous humor, known by terms like persistent hyperplastic primary vitreous and vitreous opacity. Codes like Q14.1 relate to congenital retinal malformations, covering conditions such as congenital retinal folds and macular coloboma. Q14.2 addresses optic disc malformations, including optic disc coloboma and congenital pits, while Q14.3 refers to choroidal malformations like choroidal folds and coloboma of the choroid. Q14.8 includes other specified congenital posterior eye segment anomalies, often linked to colobomas and vitreoretinal dysplasia, and Q14.9 denotes unspecified congenital malformation of the posterior eye segment. These specific ICD-10 codes assist healthcare providers and coders in accurately documenting congenital eye defects important for diagnosis and treatment planning.
Questions About This Page
How many billable codes are in the Q14 range?
Of the 7 codes in this range, 6 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the Q14 range classify?
The range classifies congenital malformations of posterior segment of eye. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
