Congenital malformations of anterior segment of eye (Q13) ICD-10-CM
The Q13 code range covers congenital malformations of anterior segment of eye with 11 ICD-10-CM diagnosis codes. 9 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Codes in the Q13 Range 11 codes · 9 billable
- Q13 Congenital malformations of anterior segment of eyeNon-billable
- Q13.0 Coloboma of iris
- Q13.1 Absence of iris
- Q13.2 Other congenital malformations of iris
- Q13.3 Congenital corneal opacity
- Q13.4 Other congenital corneal malformations
- Q13.5 Blue sclera
- Q13.8 Other congenital malformations of anterior segment of eyeNon-billable
- Q13.81 Rieger anomaly
- Q13.89 Other congenital malformations of anterior segment of eye
- Q13.9 Congenital malformation of anterior segment of eye, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q13 range.
Anisocoria
Unequal pupil size, which may represent a benign physiologic variant or a manifestation of disease. Pathologic anisocoria reflects an abnormality in the musculature of the iris (IRIS DISEASES) or in the parasympathetic or sympathetic pathways that innervate the pupil. Physiologic anisocoria refers to an asymmetry of pupil diameter, usually less than 2mm, that is not associated with disease.
Dentinogenesis Imperfecta
An autosomal dominant disorder of tooth development characterized by opalescent dentin resulting in discoloration of the teeth. The dentin develops poorly with low mineral content while the pulp canal is obliterated.
Iris Diseases
Diseases, dysfunctions, or disorders of or located in the iris.
WAGR Syndrome
A contiguous gene syndrome associated with hemizygous deletions of chromosome region 11p13. The condition is marked by the combination of WILMS TUMOR; ANIRIDIA; GENITOURINARY ABNORMALITIES; and INTELLECTUAL DISABILITY.
About the Q13 Code Range
ICD-10 code Q13 covers a group of rare congenital malformations affecting the anterior segment of the eye. These codes are specifically used to identify birth defects involving key eye structures such as the iris, cornea, and sclera, helping healthcare providers accurately document conditions like coloboma of the iris (Q13.0) and absence of iris (Q13.1).
The detailed codes within the Q13 category correspond to distinct congenital abnormalities. For example, Q13.0 is used for iris coloboma, also known by terms like "congenital coloboma of iris," while Q13.1 refers to congenital absence of the iris, or aniridia, which may be linked with syndromes such as WAGR. Other codes include Q13.3 for congenital corneal opacity and Q13.5 for blue sclera, which can relate to osteogenesis imperfecta. More complex conditions like Rieger anomaly (Q13.81) and various anterior segment dysgenesis syndromes fall under Q13.8 or Q13.89. Coders seeking the ICD-10 code for congenital malformations of anterior eye segment can refer to these specific subcodes to capture precise diagnoses involving structural and developmental eye defects.
Questions About This Page
How many billable codes are in the Q13 range?
Of the 11 codes in this range, 9 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the Q13 range classify?
The range classifies congenital malformations of anterior segment of eye. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
