Other congenital malformations of face and neck (Q18) ICD-10-CM
The Q18 code range covers other congenital malformations of face and neck with 11 ICD-10-CM diagnosis codes. 10 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Codes in the Q18 Range 11 codes · 10 billable
- Q18 Other congenital malformations of face and neckNon-billable
- Q18.0 Sinus, fistula and cyst of branchial cleft
- Q18.1 Preauricular sinus and cyst
- Q18.2 Other branchial cleft malformations
- Q18.3 Webbing of neck
- Q18.4 Macrostomia
- Q18.5 Microstomia
- Q18.6 Macrocheilia
- Q18.7 Microcheilia
- Q18.8 Other specified congenital malformations of face and neck
- Q18.9 Congenital malformation of face and neck, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q18 range.
Macrostomia
Greatly exaggerated width of the mouth, resulting from failure of union of the maxillary and mandibular processes, with extension of the oral orifice toward the ear. The defect may be unilateral or bilateral. (Dorland, 27th ed)
Microstomia
A congenital defect in which the mouth is unusually small. (Dorland, 27th ed)
About the Q18 Code Range
These conditions are present at birth and affect the face or neck. The subdivisions separate branchial cleft conditions, findings in front of the ear, neck webbing, and differences in mouth or lip size.
Q18.0 covers branchial cleft sinuses, fistulas, and cysts; Q18.2 covers other branchial cleft malformations. Q18.1 identifies sinuses and cysts in front of the ear, while Q18.3 identifies neck webbing. Q18.4 and Q18.5 distinguish larger and smaller mouths; Q18.6 and Q18.7 make that distinction for lips. Q18.8 covers other specified malformations, and Q18.9 covers unspecified malformations of the face and neck.
Questions About This Page
How many billable codes are in the Q18 range?
Of the 11 codes in this range, 10 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the Q18 range classify?
The range classifies other congenital malformations of face and neck. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
