2026 ICD-10-CM Diagnosis Code G90.APostural orthostatic tachycardia syndrome [POTS]

ICD-10-CM Codes›G00–G99›G89-G99›G90

ICD-10-CM G90.A
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

G90.A is a billable ICD-10-CM diagnosis code for postural orthostatic tachycardia syndrome [POTS]. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). Coders also document this condition as bier anemic spots, cyanosis, and urticaria-like eruption syndrome. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other nervous system disorders (neither hereditary nor degenerative).

Code Identity

ICD-10-CM Code
G90.A
Billable Status
Yes — Valid for Submission
Code Describes
Postural orthostatic tachycardia syndrome [POTS]
Short Description
Postural orthostatic tachycardia syndrome [POTS]
Same as the full description in the CMS dataset.
Parent Code
G90
Disorders of autonomic nervous system

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG89-G99Other disorders of the nervous system
CategoryG90Disorders of autonomic nervous system
This CodeG90.APostural orthostatic tachycardia syndrome [POTS]

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Bier anemic spots, cyanosis, and urticaria-like eruption syndrome
  • Biers spots
  • Orthostatic intolerance
  • Postural orthostatic tachycardia syndrome
  • Postural orthostatic tachycardia syndrome due to norepinephrine transporter deficiency

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Chronic orthostatic intolerance
  • Postural tachycardia syndrome

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Intolerance
      • orthostatic, chronic
    • POTS(postural orthostatic tachycardia syndrome)
    • Syndrome
      • postural
        • orthostatic tachycardia [POTS]
    • Syndrome
      • postural
        • tachycardia

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS020
Other nervous system disorders (neither hereditary nor degenerative)
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Postural Orthostatic Tachycardia Syndrome

    a syndrome of orthostatic intolerance combined with excessive upright tachycardia, and usually without associated orthostatic hypotension. all variants have in common an excessively reduced venous return to the heart (central hypovolemia) while upright.

  • Orthostatic Intolerance

    symptoms of cerebral hypoperfusion or autonomic overaction which develop while the subject is standing, but are relieved on recumbency. types of this include neurocardiogenic syncope; postural orthostatic tachycardia syndrome; and neurogenic orthostatic hypotension. (from noseworthy, jh., neurological therapeutics principles and practice, 2007, p2575-2576)

Patient EducationClinical

Arrhythmia

An arrhythmia is a problem with the rate or rhythm of your heartbeat. Your heart beats too quickly, too slowly, or with an irregular pattern. Changes in the electrical signals that control your heartbeat cause arrhythmias.

The full article covers:

  • What is an arrhythmia?
  • What causes an arrhythmia?
  • What are the symptoms of an arrhythmia?
  • How is an arrhythmia diagnosed?
  • What are the treatments for an arrhythmia?
  • Can arrhythmias be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code History & ChangesHistory

Replacement G90.A replaces the following previously assigned code(s):

  • I49.8 - Other specified cardiac arrhythmias
FY 2023AddedAdded to the ICD-10-CM code setEffective October 1, 2022.
FY 2024–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About G90.AOverview

Is G90.A (Disorders of autonomic nervous system) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report postural orthostatic tachycardia syndrome [POTS] on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.