2027 ICD-10-CM Diagnosis Code G90.APostural orthostatic tachycardia syndrome [POTS]

ICD-10-CM Codes›G00–G99›G89-G99›G90

ICD-10-CM G90.A
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

G90.A is a billable ICD-10-CM diagnosis code for postural orthostatic tachycardia syndrome [POTS]. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 91 through 93, 791, 793. Coders also document this condition as bier anemic spots, cyanosis, and urticaria-like eruption syndrome. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other nervous system disorders (neither hereditary nor degenerative).

Code Identity

ICD-10-CM Code
G90.A
Billable Status
Yes — Valid for Submission
Code Describes
Postural orthostatic tachycardia syndrome [POTS]
Short Description
Postural orthostatic tachycardia syndrome [POTS]
Same as the full description in the CMS dataset.
Parent Code
G90
Disorders of autonomic nervous system

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG89-G99Other disorders of the nervous system
CategoryG90Disorders of autonomic nervous system
This CodeG90.APostural orthostatic tachycardia syndrome [POTS]

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Bier anemic spots, cyanosis, and urticaria-like eruption syndrome
  • Biers spots
  • Orthostatic intolerance
  • Postural orthostatic tachycardia syndrome
  • Postural orthostatic tachycardia syndrome due to norepinephrine transporter deficiency

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to G90.A: its own notes plus those printed at G90 and Chapter 6. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Chronic orthostatic intolerance
  • Postural tachycardia syndrome

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From G90 Disorders of autonomic nervous system applies to 21 codes
  • dysfunction of the autonomic nervous system due to alcohol (G31.2)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 6 (G00-G99) Diseases of the nervous system applies to 700 codes
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS020
Other nervous system disorders (neither hereditary nor degenerative)
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Arrhythmia

An arrhythmia is a problem with the rate or rhythm of your heartbeat. Your heart beats too quickly, too slowly, or with an irregular pattern. Changes in the electrical signals that control your heartbeat cause arrhythmias.

The full article covers:

  • What is an arrhythmia?
  • What causes an arrhythmia?
  • What are the symptoms of an arrhythmia?
  • How is an arrhythmia diagnosed?
  • What are the treatments for an arrhythmia?
  • Can arrhythmias be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code History & ChangesHistory

Replacement G90.A replaces the following previously assigned code(s):

  • I49.8 - Other specified cardiac arrhythmias
FY 2023AddedAdded to the ICD-10-CM code setEffective October 1, 2022.
FY 2024–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About G90.AOverview

What is the ICD-10 code for postural orthostatic tachycardia syndrome [POTS]?

The ICD-10-CM code for postural orthostatic tachycardia syndrome [POTS] is G90.A (sometimes written as G90A). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is G90.A (Disorders of autonomic nervous system) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report postural orthostatic tachycardia syndrome [POTS] on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does G90.A group to?

When postural orthostatic tachycardia syndrome [POTS] is the principal diagnosis on an inpatient stay, it groups to MS-DRG 793, 791, 91, 92, 93, with relative weights from 0.7783 to 4.2192 depending on complications. Higher weights mean higher Medicare reimbursement.

Can G90.A be reported with G31.2?

Not as a rule. The Excludes1 note at G90, which applies to G90.A, lists "dysfunction of the autonomic nervous system due to alcohol (G31.2)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).