2026 ICD-10-CM Diagnosis Code G91Hydrocephalus
G91 is a non-billable ICD-10-CM category code for hydrocephalus, so it cannot be submitted on claims. Use a more specific code from this category instead, such as G91.0, G91.1, G91.2, and G91.3.
Code Identity
Code Classification
Specific Coding for HydrocephalusOverview
Non-specific codes like G91 require more characters. Use one of these billable codes instead:
Use G91.0 for Communicating hydrocephalus
Use G91.1 for Obstructive hydrocephalus
Use G91.2 for (Idiopathic) normal pressure hydrocephalus
Use G91.3 for Post-traumatic hydrocephalus, unspecified
Use G91.4 for Hydrocephalus in diseases classified elsewhere
Use G91.8 for Other hydrocephalus
Use G91.9 for Hydrocephalus, unspecified
Tabular List NotesGuidance
Coding notes and annotation back-references applicable to this code.
Includes
- acquired hydrocephalus
Type 1 Excludes
- Arnold-Chiari syndrome with hydrocephalus Q07
- congenital hydrocephalus Q03
- spina bifida with hydrocephalus Q05
This note appears immediately under a three character code title to further define, or give examples of, the content of the category.
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Clinical InformationClinical
Dandy-Walker Syndrome
a congenital abnormality of the central nervous system marked by failure of the midline structures of the cerebellum to develop, dilation of the fourth ventricle, and upward displacement of the transverse sinuses, tentorium, and torcula. clinical features include occipital bossing, progressive head enlargement, bulging of anterior fontanelle, papilledema, ataxia, gait disturbances, nystagmus, and intellectual compromise. (from menkes, textbook of child neurology, 5th ed, pp294-5)Hydrocephalus
excessive accumulation of cerebrospinal fluid within the cranium which may be associated with dilation of cerebral ventricles, intracranial hypertension; headache; lethargy; urinary incontinence; and ataxia.Hydrocephalus, Normal Pressure
a form of compensated hydrocephalus characterized clinically by a slowly progressive gait disorder (see gait disorders, neurologic), progressive intellectual decline, and urinary incontinence. spinal fluid pressure tends to be in the high normal range. this condition may result from processes which interfere with the absorption of csf including subarachnoid hemorrhage, chronic meningitis, and other conditions. (from adams et al., principles of neurology, 6th ed, pp631-3)Walker-Warburg Syndrome
rare autosomal recessive lissencephaly type 2 associated with congenital muscular dystrophy and eye anomalies (e.g., retinal detachment; cataract; microphthalmos). it is often associated with additional brain malformations such as hydrocephaly and cerebellar hypoplasia and is the most severe form of the group of related syndromes (alpha-dystroglycanopathies) with common congenital abnormalities in the brain, eye and muscle development.
Patient EducationClinical
Hydrocephalus
Hydrocephalus is the buildup of too much cerebrospinal fluid in the brain. Normally, this fluid cushions your brain. When you have too much, though, it puts harmful pressure on your brain.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
