2022 ICD-10-CM Code G91

Specific Coding for Hydrocephalus

Non-specific codes like G91 require more digits to indicate the appropriate level of specificity. Consider using any of the following ICD-10 codes with a higher level of specificity when coding for hydrocephalus:

Clinical Information

• DANDY WALKER SYNDROME-. a congenital abnormality of the central nervous system marked by failure of the midline structures of the cerebellum to develop dilation of the fourth ventricle and upward displacement of the transverse sinuses tentorium and torcula. clinical features include occipital bossing progressive head enlargement bulging of anterior fontanelle papilledema ataxia gait disturbances nystagmus and intellectual compromise. from menkes textbook of child neurology 5th ed pp294 5
• HYDROCEPHALUS-. excessive accumulation of cerebrospinal fluid within the cranium which may be associated with dilation of cerebral ventricles intracranial hypertension; headache; lethargy; urinary incontinence; and ataxia.
• HYDROCEPHALUS NORMAL PRESSURE-. a form of compensated hydrocephalus characterized clinically by a slowly progressive gait disorder see gait disorders neurologic progressive intellectual decline and urinary incontinence. spinal fluid pressure tends to be in the high normal range. this condition may result from processes which interfere with the absorption of csf including subarachnoid hemorrhage chronic meningitis and other conditions. from adams et al. principles of neurology 6th ed pp631 3
• WALKER WARBURG SYNDROME-. rare autosomal recessive lissencephaly type 2 associated with congenital muscular dystrophy and eye anomalies e.g. retinal detachment; cataract; microphthalmos. it is often associated with additional brain malformations such as hydrocephaly and cerebellar hypoplasia and is the most severe form of the group of related syndromes alpha dystroglycanopathies with common congenital abnormalities in the brain eye and muscle development.