G90.9 - Disorder of the autonomic nervous system, unspecified

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

• Anhidrosis
• Autonomic disorder caused by toxin
• Autonomic disorder co-occurrent and due to Chagas disease
• Autonomic neuropathy
• Chagas' disease with nervous system involvement
• Childhood obesity
• Disorder of autonomic nervous system
• Disorder of autonomic nervous system caused by substance
• Disorder of autonomic nervous system due to infectious disease
• Disorder of parasympathetic nervous system
• Disorder of peripheral autonomic nervous system
• Disorder of sympathetic nervous system
• Drug-induced autonomic dysfunction
• Hyperhidrosis due to autonomic dysregulation
• Hypohidrosis
• Hypohidrosis co-occurrent and due to disorder of sympathetic nervous system
• Inherited autonomic nervous system disorder
• Paraneoplastic autonomic dysfunction
• Paraneoplastic neuropathy
• Primary autonomic disorder with acquired anhidrosis
• Rapid-onset childhood obesity, hypothalamic dysfunction, hypoventilation, autonomic dysregulation syndrome

Clinical Information

• Hypohidrosis-. abnormally diminished or absent perspiration. both generalized and segmented (reduced or absent sweating in circumscribed locations) forms of the disease are usually associated with other underlying conditions.
• Autonomic Neuropathy-. an inherited or acquired peripheral neuropathy affecting the autonomic nervous system. it results in disruption of the involuntary body functions. inherited causes include fabry disease and porphyrias. acquired causes include diabetes, uremia, hepatic disorders, vitamin deficiencies, toxins, and drug toxicities.
• Diabetic Autonomic Neuropathy-. autonomic neuropathy that is caused by diabetes mellitus.
• ELP1 wt Allele|DYS|Dysautonomia (Riley-Day Syndrome, Hereditary Sensory Autonomic Neuropathy Type III) Gene|ELP1, Yeast, Homolog of Gene|Elongator Acetyltransferase Complex Subunit 1 wt Allele|Elongator Acetyltransferase Complex, Subunit 1 Gene|FD|IKAP|IKBKAP|IKI3|Inhibitor of Kappa Light Polypeptide Gene Enhancer In B-Cells, Kinase Complex-Associated Protein Gene|TOT1-. human elp1 wild-type allele is located in the vicinity of 9q31.3 and is approximately 67 kb in length. this allele, which encodes elongator complex protein 1, plays a role in the modification of trna. mutation of the gene is associated with familial dysautonomia and predisposition for medulloblastoma.
• Familial Dysautonomia|Familial dysautonomia|HSAN 3|HSAN III|Hereditary Sensory and Autonomic Neuropathy Type III|Neuropathy, Hereditary Sensory and Autonomic, Type III|Riley- Day|Riley-Day Syndrome|hereditary sensory and autonomic neuropathy type III-. a congenital disorder caused by mutations in the ikbkap gene. it is characterized by damage of the sympathetic and parasympathetic and sensory nervous system.
• Neuropathy, Hereditary Sensory and Autonomic, Type I|HSAN1|Hereditary Sensory and Autonomic Neuropathy Type 1-. an autosomal dominant condition caused by mutation(s) in the sptlc1 gene, encoding serine palmitoyltransferase long chain base subunit 1. it is characterized by distal sensory impairment with variable autonomic and motor involvement.
• Neuropathy, Hereditary Sensory and Autonomic, Type IV|CIPA|Congenital Insensitivity to Pain with Anhidrosis|HSAN4|Hereditary Sensory and Autonomic Neuropathy Type IV-. a rare, autosomal recessive inherited disorder caused by mutations in the ntrk1 gene. it is characterized by inability to feel pain and temperature that leads to repeated unintentional self-injuries, and decreased or absent sweating that leads to hyperpyrexia and febrile seizures.
• Neuropathy, Hereditary Sensory and Autonomic, Type V|HSAN5|Hereditary Sensory and Autonomic Neuropathy Type V-. an autosomal recessive condition caused by mutation(s) in the ngf gene, encoding beta-nerve growth factor. it is characterized by loss of pain sensation, particularly in the extremities.
• Neuropathy, Hereditary Sensory and Autonomic, Type VII|HSAN7|Hereditary Sensory and Autonomic Neuropathy Type VII-. a very rare disorder caused by mutation in the scn11a gene. affected individuals are unable to experience pain since birth resulting in self-inflicted injuries.
• Grade 2 Hypohidrosis, CTCAE|Grade 2 Hypohidrosis-. symptomatic; limiting instrumental adl
• Grade 3 Hypohidrosis, CTCAE|Grade 3 Hypohidrosis-. increase in body temperature; limiting self care adl
• Grade 4 Hypohidrosis, CTCAE|Grade 4 Hypohidrosis-. heat stroke
• Grade 5 Hypohidrosis, CTCAE|Grade 5 Hypohidrosis-. death
• Hypohidrosis-. reduced sweating. causes include burns, dehydration, radiation, and leprosy.
• Hypohidrosis, CTCAE|Hypohidrosis|Hypohidrosis-. a disorder characterized by reduced sweating.

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Patient Education

Autonomic Nervous System Disorders

Your autonomic nervous system is the part of your nervous system that controls involuntary actions, such as the beating of your heart and the widening or narrowing of your blood vessels. When something goes wrong in this system, it can cause serious problems, including:

• Blood pressure problems
• Heart problems
• Trouble with breathing and swallowing
• Erectile dysfunction in men

Autonomic nervous system disorders can occur alone or as the result of another disease, such as Parkinson's disease, alcoholism and diabetes. Problems can affect either part of the system, as in complex regional pain syndromes, or all of the system. Some types are temporary, but many worsen over time. When they affect your breathing or heart function, these disorders can be life-threatening.

Some autonomic nervous system disorders get better when an underlying disease is treated. Often, however, there is no cure. In that case, the goal of treatment is to improve symptoms.

NIH: National Institute of Neurological Disorders and Stroke

Code History

• FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
• FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
• FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
• FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
• FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
• FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
• FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
• FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016 (First year ICD-10-CM implemented into the HIPAA code set)