2024 ICD-10-CM Diagnosis Code G90.9

Disorder of the autonomic nervous system, unspecified

ICD-10-CM Code:
G90.9
ICD-10 Code for:
Disorder of the autonomic nervous system, unspecified
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Diseases of the nervous system
    (G00–G99)
    • Other disorders of the nervous system
      (G89-G99)
      • Disorders of autonomic nervous system
        (G90)

G90.9 is a billable diagnosis code used to specify a medical diagnosis of disorder of the autonomic nervous system, unspecified. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024.

Unspecified diagnosis codes like G90.9 are acceptable when clinical information is unknown or not available about a particular condition. Although a more specific code is preferable, unspecified codes should be used when such codes most accurately reflect what is known about a patient's condition. Specific diagnosis codes should not be used if not supported by the patient's medical record.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Amyotrophic lateral sclerosis plus syndrome
  • Amyotrophic lateral sclerosis with autonomic dysfunction
  • Anhidrosis
  • Autoimmune disorder of autonomic nerve
  • Autoimmune disorder of autonomic nervous system
  • Autonomic disorder caused by acrylamide
  • Autonomic disorder caused by heavy metal
  • Autonomic disorder caused by marine toxin
  • Autonomic disorder caused by organic solvent
  • Autonomic disorder caused by pyriminil
  • Autonomic disorder co-occurrent and due to Chagas disease
  • Autonomic disorder due to autoimmune encephalitis
  • Autonomic disorder due to botulism
  • Autonomic disorder due to encephalitis
  • Autonomic disorder due to HIV infection
  • Autonomic disorder due to leprosy
  • Autonomic disorder due to metabolic disorder
  • Autonomic disorder due to multiple sclerosis
  • Autonomic disorder due to Parkinson disease
  • Autonomic disorder due to prion disease
  • Autonomic disorder due to stimulant intoxication
  • Autonomic disorder due to substance withdrawal
  • Autonomic disorder due to tetanus
  • Autonomic nervous system disorder co-occurrent and due to neurodegenerative disorder
  • Autonomic neuropathy
  • Chagas' disease with nervous system involvement
  • Childhood obesity
  • Disorder of autonomic nerve due to Guillain-Barre Syndrome
  • Disorder of autonomic nerve due to impaired glucose tolerance
  • Disorder of autonomic nervous system
  • Disorder of autonomic nervous system caused by drug
  • Disorder of autonomic nervous system due to infectious disease
  • Disorder of autonomic nervous system due to infectious disease
  • Disorder of autonomic nervous system due to infectious disease
  • Disorder of autonomic nervous system due to infectious disease
  • Disorder of autonomic nervous system due to infectious disease
  • Disorder of autonomic nervous system due to infectious disease
  • Disorder of autonomic nervous system due to senile dementia of Lewy body type
  • Disorder of parasympathetic nervous system
  • Disorder of peripheral autonomic nervous system
  • Disorder of sympathetic nervous system
  • Drug-induced autonomic dysfunction
  • Hyperhidrosis due to autonomic dysregulation
  • Hypohidrosis
  • Hypohidrosis co-occurrent and due to disorder of sympathetic nervous system
  • Hypohidrosis due to neurological disorder
  • Inherited autonomic nervous system disorder
  • Paraneoplastic autonomic dysfunction
  • Paraneoplastic neuropathy
  • Primary autonomic disorder with acquired anhidrosis
  • Rapid-onset childhood obesity, hypothalamic dysfunction, hypoventilation, autonomic dysregulation syndrome

Clinical Classification

Clinical Information

  • Hypohidrosis

    abnormally diminished or absent perspiration. both generalized and segmented (reduced or absent sweating in circumscribed locations) forms of the disease are usually associated with other underlying conditions.
  • Autonomic Neuropathy

    an inherited or acquired peripheral neuropathy affecting the autonomic nervous system. it results in disruption of the involuntary body functions. inherited causes include fabry disease and porphyrias. acquired causes include diabetes, uremia, hepatic disorders, vitamin deficiencies, toxins, and drug toxicities.
  • Diabetic Autonomic Neuropathy

    autonomic neuropathy that is caused by diabetes mellitus.
  • ELP1 wt Allele|DYS|Dysautonomia (Riley-Day Syndrome, Hereditary Sensory Autonomic Neuropathy Type III) Gene|ELP1, Yeast, Homolog of Gene|Elongator Acetyltransferase Complex Subunit 1 wt Allele|Elongator Acetyltransferase Complex, Subunit 1 Gene|FD|IKAP|IKBKAP|IKI3|Inhibitor of Kappa Light Polypeptide Gene Enhancer In B-Cells, Kinase Complex-Associated Protein Gene|TOT1

    human elp1 wild-type allele is located in the vicinity of 9q31.3 and is approximately 67 kb in length. this allele, which encodes elongator complex protein 1, plays a role in the modification of trna. mutation of the gene is associated with familial dysautonomia and predisposition for medulloblastoma.
  • Familial Dysautonomia|Familial dysautonomia|HSAN 3|HSAN III|Hereditary Sensory and Autonomic Neuropathy Type III|Neuropathy, Hereditary Sensory and Autonomic, Type III|Riley- Day|Riley-Day Syndrome|hereditary sensory and autonomic neuropathy type III

    a congenital disorder caused by mutations in the ikbkap gene. it is characterized by damage of the sympathetic and parasympathetic and sensory nervous system.
  • Neuropathy, Hereditary Sensory and Autonomic, Type I|HSAN1|Hereditary Sensory and Autonomic Neuropathy Type 1

    an autosomal dominant condition caused by mutation(s) in the sptlc1 gene, encoding serine palmitoyltransferase long chain base subunit 1. it is characterized by distal sensory impairment with variable autonomic and motor involvement.
  • Neuropathy, Hereditary Sensory and Autonomic, Type IV|CIPA|Congenital Insensitivity to Pain with Anhidrosis|HSAN4|Hereditary Sensory and Autonomic Neuropathy Type IV

    a rare, autosomal recessive inherited disorder caused by mutations in the ntrk1 gene. it is characterized by inability to feel pain and temperature that leads to repeated unintentional self-injuries, and decreased or absent sweating that leads to hyperpyrexia and febrile seizures.
  • Neuropathy, Hereditary Sensory and Autonomic, Type V|HSAN5|Hereditary Sensory and Autonomic Neuropathy Type V

    an autosomal recessive condition caused by mutation(s) in the ngf gene, encoding beta-nerve growth factor. it is characterized by loss of pain sensation, particularly in the extremities.
  • Neuropathy, Hereditary Sensory and Autonomic, Type VII|HSAN7|Hereditary Sensory and Autonomic Neuropathy Type VII

    a very rare disorder caused by mutation in the scn11a gene. affected individuals are unable to experience pain since birth resulting in self-inflicted injuries.
  • Grade 2 Hypohidrosis, CTCAE|Grade 2 Hypohidrosis

    symptomatic; limiting instrumental adl
  • Grade 3 Hypohidrosis, CTCAE|Grade 3 Hypohidrosis

    increase in body temperature; limiting self care adl
  • Grade 4 Hypohidrosis, CTCAE|Grade 4 Hypohidrosis

    heat stroke
  • Grade 5 Hypohidrosis, CTCAE|Grade 5 Hypohidrosis

    death
  • Hypohidrosis

    reduced sweating. causes include burns, dehydration, radiation, and leprosy.
  • Hypohidrosis, CTCAE|Hypohidrosis|Hypohidrosis

    a disorder characterized by reduced sweating.

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Convert G90.9 to ICD-9-CM

  • ICD-9-CM Code: 337.9 - Autonomic nerve dis NEC
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education


Autonomic Nervous System Disorders

Your autonomic nervous system is the part of your nervous system that controls involuntary actions, such as the beating of your heart and the widening or narrowing of your blood vessels. When something goes wrong in this system, it can cause serious problems, including:

  • Blood pressure problems
  • Heart problems
  • Trouble with breathing and swallowing
  • Erectile dysfunction in men

Autonomic nervous system disorders can occur alone or as the result of another disease, such as Parkinson's disease, alcoholism and diabetes. Problems can affect either part of the system, as in complex regional pain syndromes, or all of the system. Some types are temporary, but many worsen over time. When they affect your breathing or heart function, these disorders can be life-threatening.

Some autonomic nervous system disorders get better when an underlying disease is treated. Often, however, there is no cure. In that case, the goal of treatment is to improve symptoms.

NIH: National Institute of Neurological Disorders and Stroke


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.