ICD-10-CM Code G90.09

Other idiopathic peripheral autonomic neuropathy

Version 2020 Billable Code

Valid for Submission

G90.09 is a billable code used to specify a medical diagnosis of other idiopathic peripheral autonomic neuropathy. The code is valid for the year 2020 for the submission of HIPAA-covered transactions. The ICD-10-CM code G90.09 might also be used to specify conditions or terms like cervical sympathetic paralysis, congenital degeneration of nervous system, congenital malformation of autonomic nervous system, facial neuralgia, familial visceral neuropathy, idiopathic peripheral autonomic neuropathy, etc

Short Description:Other idiopathic peripheral autonomic neuropathy
Long Description:Other idiopathic peripheral autonomic neuropathy

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code G90.09:

Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Idiopathic peripheral autonomic neuropathy NOS

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code G90.09 are found in the index:


The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Cervical sympathetic paralysis
  • Congenital degeneration of nervous system
  • Congenital malformation of autonomic nervous system
  • Facial neuralgia
  • Familial visceral neuropathy
  • Idiopathic peripheral autonomic neuropathy
  • Intestinal autonomic neuropathy
  • Paroxysmal extreme pain disorder
  • Sphenopalatine neuralgia
  • Visceral neuropathy and brain anomaly with facial dysmorphism and developmental delay syndrome

Convert G90.09 to ICD-9

  • 337.00 - Idio perph auto neur NOS (Approximate Flag)
  • 337.09 - Idio perph auto neur NEC (Approximate Flag)

Code Classification

  • Diseases of the nervous system (G00–G99)
    • Other disorders of the nervous system (G89-G99)
      • Disorders of autonomic nervous system (G90)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Patients

Autonomic Nervous System Disorders

Your autonomic nervous system is the part of your nervous system that controls involuntary actions, such as the beating of your heart and the widening or narrowing of your blood vessels. When something goes wrong in this system, it can cause serious problems, including

  • Blood pressure problems
  • Heart problems
  • Trouble with breathing and swallowing
  • Erectile dysfunction in men

Autonomic nervous system disorders can occur alone or as the result of another disease, such as Parkinson's disease, alcoholism and diabetes. Problems can affect either part of the system, as in complex regional pain syndromes, or all of the system. Some types are temporary, but many worsen over time. When they affect your breathing or heart function, these disorders can be life-threatening.

Some autonomic nervous system disorders get better when an underlying disease is treated. Often, however, there is no cure. In that case, the goal of treatment is to improve symptoms.

NIH: National Institute of Neurological Disorders and Stroke

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