Disorders of autonomic nervous system (G90)

Browse all the diagnosis codes used for disorders of autonomic nervous system (g90). For easy navigation, the diagnosis codes are sorted in alphabetical order and grouped by sections. Each section is clearly marked with its description, and the corresponding three-digit code range. This format makes it simple to browse diagnosis codes in this chapter or section and find what you're looking for. We've also added green checkmark icons to label billable codes, and red warning icons for non-billable ones. This makes it easy to identify which codes can be billed.

Clinical Information

Autonomic Dysreflexia - A syndrome associated with damage to the spinal cord above the mid thoracic level (see SPINAL CORD INJURIES) characterized by a marked increase in the sympathetic response to minor stimuli such as bladder or rectal distention. Manifestations include HYPERTENSION; TACHYCARDIA (or reflex bradycardia); FEVER; FLUSHING; and HYPERHIDROSIS. Extreme hypertension may be associated with a STROKE. (From Adams et al., Principles of Neurology, 6th ed, pp538 and 1232; J Spinal Cord Med 1997;20(3):355-60)

Horner Syndrome - A syndrome associated with defective sympathetic innervation to one side of the face, including the eye. Clinical features include MIOSIS; mild BLEPHAROPTOSIS; and hemifacial ANHIDROSIS (decreased sweating)(see HYPOHIDROSIS). Lesions of the BRAIN STEM; cervical SPINAL CORD; first thoracic nerve root; apex of the LUNG; CAROTID ARTERY; CAVERNOUS SINUS; and apex of the ORBIT may cause this condition. (From Miller et al., Clinical Neuro-Ophthalmology, 4th ed, pp500-11)

Hypohidrosis - Abnormally diminished or absent perspiration. Both generalized and segmented (reduced or absent sweating in circumscribed locations) forms of the disease are usually associated with other underlying conditions.

Multiple System Atrophy - A syndrome complex composed of three conditions which represent clinical variants of the same disease process: STRIATONIGRAL DEGENERATION; SHY-DRAGER SYNDROME; and the sporadic form of OLIVOPONTOCEREBELLAR ATROPHIES. Clinical features include autonomic, cerebellar, and basal ganglia dysfunction. Pathologic examination reveals atrophy of the basal ganglia, cerebellum, pons, and medulla, with prominent loss of autonomic neurons in the brain stem and spinal cord. (From Adams et al., Principles of Neurology, 6th ed, p1076; Baillieres Clin Neurol 1997 Apr;6(1):187-204; Med Clin North Am 1999 Mar;83(2):381-92)

Orthostatic Intolerance - Symptoms of cerebral hypoperfusion or autonomic overaction which develop while the subject is standing, but are relieved on recumbency. Types of this include NEUROCARDIOGENIC SYNCOPE; POSTURAL ORTHOSTATIC TACHYCARDIA SYNDROME; and neurogenic ORTHOSTATIC HYPOTENSION. (From Noseworthy, JH., Neurological Therapeutics Principles and Practice, 2007, p2575-2576)

Postural Orthostatic Tachycardia Syndrome - A syndrome of ORTHOSTATIC INTOLERANCE combined with excessive upright TACHYCARDIA, and usually without associated ORTHOSTATIC HYPOTENSION. All variants have in common an excessively reduced venous return to the heart (central HYPOVOLEMIA) while upright.

Pure Autonomic Failure - A degenerative disease of the AUTONOMIC NERVOUS SYSTEM that is characterized by idiopathic ORTHOSTATIC HYPOTENSION and a greatly reduced level of CATECHOLAMINES. No other neurological deficits are present.

Serotonin Syndrome - An adverse drug interaction characterized by altered mental status, autonomic dysfunction, and neuromuscular abnormalities. It is most frequently caused by use of both serotonin reuptake inhibitors and monoamine oxidase inhibitors, leading to excess serotonin availability in the CNS at the serotonin 1A receptor.

Instructional Notations

Type 1 Excludes

A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

  • dysfunction of the autonomic nervous system due to alcohol G31.2
  • Diseases of the nervous system (G00–G99)

    • Other disorders of the nervous system (G89-G99)

        • Disorders of autonomic nervous system (G90)

        • G90 Disorders of autonomic nervous system
        • G90.0 Idiopathic peripheral autonomic neuropathy
        • G90.01 Carotid sinus syncope
        • G90.09 Other idiopathic peripheral autonomic neuropathy
        • G90.1 Familial dysautonomia [Riley-Day]
        • G90.2 Horner's syndrome
        • G90.3 Multi-system degeneration of the autonomic nervous system
        • G90.4 Autonomic dysreflexia
        • G90.5 Complex regional pain syndrome I (CRPS I)
        • G90.50 Complex regional pain syndrome I, unspecified
        • G90.51 Complex regional pain syndrome I of upper limb
        • G90.511 Complex regional pain syndrome I of right upper limb
        • G90.512 Complex regional pain syndrome I of left upper limb
        • G90.513 Complex regional pain syndrome I of upper limb, bilateral
        • G90.519 Complex regional pain syndrome I of unspecified upper limb
        • G90.52 Complex regional pain syndrome I of lower limb
        • G90.521 Complex regional pain syndrome I of right lower limb
        • G90.522 Complex regional pain syndrome I of left lower limb
        • G90.523 Complex regional pain syndrome I of lower limb, bilateral
        • G90.529 Complex regional pain syndrome I of unspecified lower limb
        • G90.59 Complex regional pain syndrome I of other specified site
        • G90.8 Other disorders of autonomic nervous system DELETED CODE
        • G90.81 Serotonin syndrome NEW CODE
        • G90.89 Other disorders of autonomic nervous system NEW CODE
        • G90.9 Disorder of the autonomic nervous system, unspecified
        • G90.A Postural orthostatic tachycardia syndrome [POTS]
        • G90.B LMNB1-related autosomal dominant leukodystrophy