2026 ICD-10-CM Diagnosis Code E83.823ABCC6 deficiency causing generalized arterial calcification of infancy
E83.823 is a billable ICD-10-CM diagnosis code for ABCC6 deficiency causing generalized arterial calcification of infancy. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 299 through 301.
Code Identity
Code Classification
Tabular List NotesGuidance
Coding notes and annotation back-references applicable to this code.
Code Also
A "code also" note instructs that two codes may be required to fully describe a condition, but this note does not provide sequencing direction.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
- arterial
- generalized, of infancy - E83.820
- with
- ABCC6 deficiency - E83.823
External Cause of Injuries IndexGuidance
References for this code in the External Cause of Injuries Index.
- Calcification
- arterial
- generalized, of infancy
- with
- ABCC6 deficiency
- Deficiency, deficient
- ABCC6
- causing generalized arterial calcification of infancy
Code History & ChangesHistory
New Code E83.823 was added to the ICD-10-CM code set for FY 2026, effective October 1, 2025.
Replacement E83.823 replaces the following previously assigned code(s):
- E83.89 - Other disorders of mineral metabolism
Questions About E83.823Overview
Is E83.823 (Disorders of pyrophosphate metabolism) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report ABCC6 deficiency causing generalized arterial calcification of infancy on HIPAA-covered claims from October 1, 2025 through September 30, 2026.
What MS-DRG does E83.823 group to?
When ABCC6 deficiency causing generalized arterial calcification of infancy is the principal diagnosis on an inpatient stay, it groups to MS-DRG 299, 300, 301, with relative weights from 0.7197 to 1.6327 depending on complications. Higher weights mean higher Medicare reimbursement.
