2027 ICD-10-CM Diagnosis Code Q79.0Congenital diaphragmatic hernia

ICD-10-CM Codes›Q00-Q99›Q65-Q79›Q79

ICD-10-CM Q79.0
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q79.0 is a billable ICD-10-CM diagnosis code for congenital diaphragmatic hernia. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 205 through 206. As a secondary diagnosis, it counts as a major complication or comorbidity (MCC) and places an inpatient stay in the highest severity level of its MS-DRG family. It does not count, however, when the principal diagnosis is one of 3 closely related codes. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Musculoskeletal congenital conditions.

Code Identity

ICD-10-CM Code
Q79.0
Billable Status
Yes — Valid for Submission
Code Describes
Congenital diaphragmatic hernia
Short Description
Congenital diaphragmatic hernia
Same as the full description in the CMS dataset.
Parent Code
Congenital malformations of musculoskeletal system, not elsewhere classified

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ65-Q79Congenital malformations and deformations of the musculoskeletal system
CategoryQ79Congenital malformations of musculoskeletal system, not elsewhere classified
This CodeQ79.0Congenital diaphragmatic hernia

Present on Admission (POA)Billing

Q79.0 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations and deformations of the musculoskeletal system (Q65-Q79).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Asplenia
  • Combined malformation of central nervous system and skeletal muscle
  • Congenital absence of spleen
  • Congenital diaphragmatic hernia
  • Congenital hernia of foramen of Morgagni
  • Congenital omphalocele
  • Congenital omphalocele, diaphragmatic hernia, cardiovascular anomalies, radial ray defect syndrome
  • Congenital posterolateral diaphragmatic hernia
  • Congenital short bowel syndrome
  • Congenital umbilical hernia
  • Diaphragmatic hernia, short bowel, asplenia syndrome
  • Donnai-Barrow syndrome
  • Fryns syndrome
  • Hydranencephaly
  • Lethal hydranencephaly, diaphragmatic hernia syndrome
  • Microphthalmos due to Fryns syndrome
  • PAGOD syndrome
  • Short bowel syndrome

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q79.0: its own notes plus those printed at Q79 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

  • congenital hiatus hernia (Q40.1)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Q79 Congenital malformations of musculoskeletal system, not elsewhere classified applies to 14 codes
  • congenital (sternomastoid) torticollis (Q68.0)
From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q79.0, its category, or a range that includes it.

Excludes1 3

These codes carry an Excludes1 note naming Q79.0: they are not reported together with it, unless the two conditions are unrelated.

  • J98.6 Disorders of diaphragm
    congenital diaphragmatic hernia (Q79.0)
  • K44 Diaphragmatic hernia
    congenital diaphragmatic hernia (Q79.0)
  • Q40.1 Congenital hiatus hernia
    congenital diaphragmatic hernia (Q79.0)

Excludes2 1

These codes carry an Excludes2 note naming Q79.0: its condition is not part of those codes, and both may be reported when the patient has both.

  • Q45 Other congenital malformations of digestive system
    congenital diaphragmatic hernia (Q79.0)

Index to Diseases and InjuriesGuidance

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL008
Musculoskeletal congenital conditions
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Hernias, Diaphragmatic, Congenital

    protrusion of abdominal structures into the thorax as a result of embryologic defects in the diaphragm often present in the neonatal period. it can be isolated, syndromic, non-syndromic or be a part of chromosome abnormality. associated pulmonary hypoplasia and pulmonary hypertension can further complicate stabilization and surgical intervention.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q79.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
756.6 Anomalies of diaphragm
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q79.0Overview

What is the ICD-10 code for congenital diaphragmatic hernia?

The ICD-10-CM code for congenital diaphragmatic hernia is Q79.0 (sometimes written as Q790). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q79.0 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital diaphragmatic hernia on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q79.0 group to?

When congenital diaphragmatic hernia is the principal diagnosis on an inpatient stay, it groups to MS-DRG 206, 205, with relative weights from 0.9255 to 1.8244 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q79.0 a CC or MCC?

CMS lists Q79.0 as an MCC (major complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it places the inpatient stay in the highest-weighted DRG of its severity family. It does not count when the principal diagnosis is one of the 3 closely related codes in its exclusion list.

Is Q79.0 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital diaphragmatic hernia on inpatient claims. The code appears in the Congenital malformations and deformations of the musculoskeletal system (Q65-Q79) range of the CMS exempt list.