2027 ICD-10-CM Diagnosis Code Q75.9Congenital malformation of skull and face bones, unspecified
ICD-10-CM Codes›Q00-Q99›Q65-Q79›Q75
- Billable — Valid for Submission
- POA Exempt
- Chronic Condition
Q75.9 is a billable ICD-10-CM diagnosis code for congenital malformation of skull and face bones, unspecified. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 564 through 566. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Musculoskeletal congenital conditions.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q75.9 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations and deformations of the musculoskeletal system (Q65-Q79).
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Athetoid cerebral palsy
- Autosomal dominant intellectual disability, craniofacial anomalies, cardiac defects syndrome
- Autosomal dominant intellectual disability, craniofacial dysmorphism, macrocephaly, hypotonia syndrome due to H1-4 mutation
- Brachycephaly
- Cardiocranial syndrome Pfeiffer type
- Cleft lip and palate, craniofacial dysmorphism, congenital heart defect, hearing loss syndrome
- Congenital abnormality of skull and face bones
- Congenital anomaly of alisphenoid bone
- Congenital anomaly of basisphenoid bone
- Congenital anomaly of bone of head
- Congenital anomaly of face bones
- Congenital anomaly of head
- Congenital anomaly of skull
- Congenital anomaly of supraoccipital bone
- Congenital diaphragmatic hernia
- Congenital dilatation of colon
- Congenital facial asymmetry
- Congenital hypoplasia of nail unit
- Congenital malformation of sphenoid wing
- Congenital posterolateral diaphragmatic hernia
- Craniofacial deafness hand syndrome
- Craniofacial dysplasia, short stature, ectodermal anomalies, intellectual disability syndrome
- Craniofacial microsomia
- Deafness craniofacial syndrome
- Diaphragmatic defect, limb deficiency, skull defect syndrome
- Dyskinetic cerebral palsy
- Facial dysmorphism, global developmental delay, hypotonia, polymicrogyria syndrome
- Haspeslagh Fryns Muelenaere syndrome
- Hirschsprung disease with nail hypoplasia and dysmorphism
- Intellectual disability, autism, speech apraxia, craniofacial dysmorphism syndrome
- Localized congenital skull defect
- Mitochondrial DNA depletion syndrome encephalomyopathic form
- Mitochondrial DNA depletion syndrome, encephalomyopathic form with variable craniofacial anomalies
- Neurodevelopmental disorder, craniofacial dysmorphism, cardiac defect, skeletal anomalies syndrome
- Non-spastic cerebral palsy
- Oculo-auriculo-vertebral spectrum
- Sagittal craniosynostosis
- Severe microbrachycephaly, intellectual disability, athetoid cerebral palsy syndrome
- Skull congenital deformities
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to Q75.9: its own notes plus those printed at Q75 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- Congenital anomaly of face bones NOS
- Congenital anomaly of skull NOS
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
- congenital malformation of face NOS (Q18.-)
- congenital malformation syndromes classified to Q87.-
- dentofacial anomalies [including malocclusion] (M26.-)
- musculoskeletal deformities of head and face (Q67.0-Q67.4)
- skull defects associated with congenital anomalies of brain such as:
- anencephaly (Q00.0)
- encephalocele (Q01.-)
- hydrocephalus (Q03.-)
- microcephaly (Q02)
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
Notes
General instructions on how these codes are used.
- Codes from this chapter are not for use on maternal records
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name Q75.9, its category, or a range that includes it.
Index to Diseases and InjuriesGuidance
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Patient EducationClinical
Craniofacial Abnormalities
Craniofacial is a medical term that relates to the bones of the skull and face. Craniofacial abnormalities are birth defects of the face or head. Some, like cleft lip and palate, are among the most common of all birth defects. Others are very rare. Most of them affect how a person's face or head looks.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q75.9 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q75.9Overview
What is the ICD-10 code for congenital malformation of skull and face bones, unspecified?
The ICD-10-CM code for congenital malformation of skull and face bones, unspecified is Q75.9 (sometimes written as Q759). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is Q75.9 (Other congenital malformations of skull and face bones) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report congenital malformation of skull and face bones, unspecified on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does Q75.9 group to?
When congenital malformation of skull and face bones, unspecified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 566, 565, with relative weights from 0.7374 to 1.4909 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q75.9 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital malformation of skull and face bones, unspecified on inpatient claims. The code appears in the Congenital malformations and deformations of the musculoskeletal system (Q65-Q79) range of the CMS exempt list.
Can Q75.9 be reported with a code from Q18?
Not as a rule. The Excludes1 note at Q75, which applies to Q75.9, lists "congenital malformation of face NOS (Q18.-)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).
