2026 ICD-10-CM Diagnosis Code Q75.9Congenital malformation of skull and face bones, unspecified

ICD-10-CM Codes›Q00-Q99›Q65-Q79›Q75

ICD-10-CM Q75.9
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q75.9 is a billable ICD-10-CM diagnosis code for congenital malformation of skull and face bones, unspecified. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 564 through 566. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Musculoskeletal congenital conditions.

Code Identity

ICD-10-CM Code
Q75.9
Billable Status
Yes — Valid for Submission
Code Describes
Congenital malformation of skull and face bones, unspecified
Short Description
Congenital malformation of skull and face bones, unspecified
Same as the full description in the CMS dataset.
Parent Code
Q75
Other congenital malformations of skull and face bones

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ65-Q79Congenital malformations and deformations of the musculoskeletal system
CategoryQ75Other congenital malformations of skull and face bones
This CodeQ75.9Congenital malformation of skull and face bones, unspecified

Present on Admission (POA)Billing

Q75.9 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Athetoid cerebral palsy
  • Autosomal dominant intellectual disability, craniofacial anomalies, cardiac defects syndrome
  • Autosomal dominant intellectual disability, craniofacial dysmorphism, macrocephaly, hypotonia syndrome due to H1-4 mutation
  • Body height below reference range
  • Brachycephaly
  • Cardiocranial syndrome Pfeiffer type
  • Cleft lip and palate, craniofacial dysmorphism, congenital heart defect, hearing loss syndrome
  • Congenital abnormality of skull and face bones
  • Congenital anomaly of alisphenoid bone
  • Congenital anomaly of basisphenoid bone
  • Congenital anomaly of face bones
  • Congenital anomaly of fetal head bones
  • Congenital anomaly of head
  • Congenital anomaly of skull
  • Congenital anomaly of supraoccipital bone
  • Congenital diaphragmatic hernia
  • Congenital dilatation of colon
  • Congenital facial asymmetry
  • Congenital hypoplasia of nail unit
  • Congenital malformation of sphenoid wing
  • Congenital posterolateral diaphragmatic hernia
  • Craniofacial deafness hand syndrome
  • Craniofacial dysplasia, short stature, ectodermal anomalies, intellectual disability syndrome
  • Craniofacial microsomia
  • Deafness craniofacial syndrome
  • Diaphragmatic defect, limb deficiency, skull defect syndrome
  • Dyskinetic cerebral palsy
  • Haspeslagh Fryns Muelenaere syndrome
  • Hirschsprung disease with nail hypoplasia and dysmorphism
  • Intellectual disability, autism, speech apraxia, craniofacial dysmorphism syndrome
  • Localized congenital skull defect
  • Mitochondrial DNA depletion syndrome encephalomyopathic form
  • Mitochondrial DNA depletion syndrome, encephalomyopathic form with variable craniofacial anomalies
  • Neurodevelopmental disorder, craniofacial dysmorphism, cardiac defect, skeletal anomalies syndrome
  • Non-spastic cerebral palsy
  • Oculo-auriculo-vertebral spectrum
  • Sagittal craniosynostosis
  • Severe microbrachycephaly, intellectual disability, athetoid cerebral palsy syndrome
  • Skull congenital deformities

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Congenital anomaly of face bones NOS
  • Congenital anomaly of skull NOS

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Anomaly, anomalous(congenital) (unspecified type)
      • bone
        • face
    • Anomaly, anomalous(congenital) (unspecified type)
      • bone
        • skull
    • Anomaly, anomalous(congenital) (unspecified type)
      • face
        • bone (s)
    • Anomaly, anomalous(congenital) (unspecified type)
      • skull
    • Malformation(congenital)
      • bone
        • face
    • Malformation(congenital)
      • bone
        • skull

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL008
Musculoskeletal congenital conditions
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Congenital Diaphragmatic Hernia

    diaphragmatic hernia that is present at birth.

Patient EducationClinical

Craniofacial Abnormalities

Craniofacial is a medical term that relates to the bones of the skull and face. Craniofacial abnormalities are birth defects of the face or head. Some, like cleft lip and palate, are among the most common of all birth defects. Others are very rare. Most of them affect how a person's face or head looks.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q75.9 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
756.0 Anomal skull/face bones
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q75.9Overview

Is Q75.9 (Other congenital malformations of skull and face bones) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital malformation of skull and face bones, unspecified on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q75.9 group to?

When congenital malformation of skull and face bones, unspecified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 565, 566, with relative weights from 0.7493 to 1.5436 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q75.9 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital malformation of skull and face bones, unspecified on inpatient claims.

What is the ICD-9 equivalent of Q75.9?

Under the General Equivalence Mappings, congenital malformation of skull and face bones, unspecified converts to ICD-9-CM 756.0 (anomal skull/face bones). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.