2026 ICD-10-CM Diagnosis Code Q74.9Unspecified congenital malformation of limb(s)

ICD-10-CM Codes›Q00-Q99›Q65-Q79›s

ICD-10-CM Q74.9
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q74.9 is a billable ICD-10-CM diagnosis code for unspecified congenital malformation of limb(s). It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 564 through 566. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Musculoskeletal congenital conditions.

Code Identity

ICD-10-CM Code
Q74.9
Billable Status
Yes — Valid for Submission
Code Describes
Unspecified congenital malformation of limb(s)
Short Description
Unspecified congenital malformation of limb(s)
Same as the full description in the CMS dataset.
Parent Code
Q74
Other congenital malformations of limb(s)

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ65-Q79Congenital malformations and deformations of the musculoskeletal system
CategorysOther congenital malformations of limb (Q74)
This CodeQ74.9Unspecified congenital malformation of limb(s)

Present on Admission (POA)Billing

Q74.9 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Abnormally short little finger
  • Acrofacial dysostosis Catania type
  • Acrorenal mandibular syndrome
  • Akinesia
  • Arachnodactyly
  • Autosomal recessive facio-digito-genital syndrome
  • B-cell immunodeficiency, limb anomaly, urogenital malformation syndrome
  • Bifid nose
  • Brachymesophalangia
  • Brachytelephalangy, facial dysmorphism, Kallmann syndrome
  • Cardio-acral-facial syndrome
  • Charlie M syndrome
  • Congenital abnormal shape of frontal bone
  • Congenital anomaly of digit
  • Congenital anomaly of joint
  • Congenital anomaly of limb
  • Congenital cleft nose
  • Congenital diaphragmatic hernia
  • Congenital dysplasia of limb
  • Congenital hypotrichia
  • Congenital splenomegaly
  • Craniofacial deafness hand syndrome
  • Disproportionate short stature
  • DONSON-related microcephaly, short stature, limb abnormalities spectrum
  • Early-onset seizures, distal limb anomalies, facial dysmorphism, global developmental delay syndrome
  • Emery Nelson syndrome
  • Epileptic encephalopathy
  • Feingold syndrome
  • Fryns syndrome
  • Harrod syndrome
  • Hypertelorism
  • Hypoplasia of distal phalanx of foot
  • Ichthyosis, oral and digital anomalies syndrome
  • Lethal congenital disproportionate short limbed short stature
  • Linear hypopigmentation and craniofacial asymmetry with acral, ocular and brain anomalies
  • Macrocytosis - no anemia
  • Mammary digital nail syndrome
  • Mesomelic dysplasia, digital anomalies, intellectual disability syndrome
  • Microphthalmia with brain and digit anomaly
  • Microphthalmos due to Fryns syndrome
  • Mullerian duct and limb anomalies syndrome
  • Multiple pterygium syndrome
  • Nephrosis, deafness, urinary tract, digital malformation syndrome
  • Neurofaciodigitorenal syndrome
  • Non-anemic red cell disorder
  • Oral-facial-digital syndrome with short stature and brachymesophalangia
  • Oro-facial digital syndrome type 10
  • Oro-facial digital syndrome type 11
  • Oro-facial digital syndrome type 14
  • Oro-facial digital syndrome type 5
  • Oro-facial digital syndrome type 9
  • Oromandibular-limb hypogenesis spectrum
  • Osteosarcoma, limb anomalies, erythroid macrocytosis syndrome
  • Pierre Robin sequence faciodigital anomaly syndrome
  • Platelet count above reference range
  • Robin sequence
  • Splenogonadal fusion
  • Splenogonadal fusion, limb defect, micrognathia syndrome
  • Thrombocythemia with distal limb defect
  • Thrombocytosis
  • TRAF7-associated heart defect, digital anomalies, facial dysmorphism, motor and speech delay syndrome
  • Trigonocephaly
  • Trigonocephaly with bifid nose and acral anomaly syndrome
  • Ulbright Hodes syndrome
  • VACTEL syndrome
  • VACTERL syndrome with hydrocephalus
  • Verloove Vanhorick Brubakk syndrome
  • Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-esophageal fistula, renal anomalies, limb defects syndrome

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Congenital anomaly of limb(s) NOS

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Anomaly, anomalous(congenital) (unspecified type)
      • flexion (joint) NOS
    • Anomaly, anomalous(congenital) (unspecified type)
      • joint
    • Anomaly, anomalous(congenital) (unspecified type)
      • limb
    • Arthrodysplasia
    • Deformity
      • flexion (joint) (acquired)
        • congenital NOS
    • Deformity
      • limb (acquired)
        • congenital, except reduction deformity
    • Deformity
      • rotation (joint) (acquired)
        • congenital
    • Malformation(congenital)
      • joint

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL008
Musculoskeletal congenital conditions
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Hypertelorism

    abnormal increase in the interorbital distance due to overdevelopment of the lesser wings of the sphenoid.

  • Arachnodactyly

    an abnormal bone development that is characterized by extra long and slender hands and fingers, such that the clenched thumb extends beyond the ulnar side of the hand. arachnodactyly can include feet and toes. arachnodactyly has been associated with several gene mutations and syndromes.

  • Thrombocythemia, Essential

    a clinical syndrome characterized by repeated spontaneous hemorrhages and a remarkable increase in the number of circulating platelets.

  • Thrombocytosis

    increased numbers of platelets in the peripheral blood. (dorland, 27th ed)

  • Congenital Diaphragmatic Hernia

    diaphragmatic hernia that is present at birth.

  • Akinesia

    lack of movement.

  • Fetal Akinesia Deformation Sequence|FADS|Pena-Shokeir syndrome, Type 1

    a condition characterized by fetal akinesia and intrauterine growth restriction, that may be associated with mutation(s) in the rapsn or dok7 genes, encoding 43 kda receptor-associated protein of the synapse and protein dok-7, respectively.

  • Feingold Syndrome

    a rare autosomal dominant syndrome caused by mutations in the mycn oncogene. it is characterized by microcephaly, limb abnormalities, esophageal and/or duodenal atresia.

  • Fryns Syndrome

    a rare syndrome inherited in an autosomal recessive pattern. it is characterized by the presence of diaphragmatic defects, distinctive facial features (hypertelorism, low-set ears, flat nasal bridge, and micrognathia), distal digital hypoplasia, lung hypoplasia, and brain, gastrointestinal, and cardiovascular malformations.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q74.9 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
755.50 Upper limb anomaly NOS
Approximate The match is approximate rather than exact.
ICD-9-CM
755.9 Congen limb anomaly NOS
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q74.9Overview

Is Q74.9 (Other congenital malformations of limb(s)) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report unspecified congenital malformation of limb(s) on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q74.9 group to?

When unspecified congenital malformation of limb(s) is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 565, 566, with relative weights from 0.7493 to 1.5436 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q74.9 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for unspecified congenital malformation of limb(s) on inpatient claims.

What is the ICD-9 equivalent of Q74.9?

Under the General Equivalence Mappings, unspecified congenital malformation of limb(s) converts to ICD-9-CM 755.50 (upper limb anomaly NOS) and 755.9 (congen limb anomaly NOS). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.