ICD-10-CM Code Q74.0

Other congenital malformations of upper limb(s), including shoulder girdle

Version 2020 Billable Code POA Exempt

Valid for Submission

Q74.0 is a billable code used to specify a medical diagnosis of other congenital malformations of upper limb(s), including shoulder girdle. The code is valid for the year 2020 for the submission of HIPAA-covered transactions. The ICD-10-CM code Q74.0 might also be used to specify conditions or terms like aberrant forearm extensor muscle, aberrant intrinsic muscles of hand, aberrant muscle of the upper limb, absence of clavicle, absence of scapula, absence of upper arm, etc The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Short Description:Oth congen malform of upper limb(s), inc shoulder girdle
Long Description:Other congenital malformations of upper limb(s), including shoulder girdle

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code Q74.0:

Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Accessory carpal bones
  • Cleidocranial dysostosis
  • Congenital pseudarthrosis of clavicle
  • Macrodactylia (fingers)
  • Madelung's deformity
  • Radioulnar synostosis
  • Sprengel's deformity
  • Triphalangeal thumb

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code Q74.0 are found in the index:


The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Aberrant forearm extensor muscle
  • Aberrant intrinsic muscles of hand
  • Aberrant muscle of the upper limb
  • Absence of clavicle
  • Absence of scapula
  • Absence of upper arm
  • Accessory carpal bones
  • Acrodysplasia scoliosis
  • Adducted thumbs and arthrogryposis syndrome Christian type
  • Agenesis of clavicle
  • Amegakaryocytic thrombocytopenia
  • Amegakaryocytic thrombocytopenia with congenital malformation
  • Atrioventricular septal defect, blepharophimosis, radial and anal defect syndrome
  • Bifid digit
  • Bifid thumb
  • Bilateral congenital deformity of upper limbs
  • Bilateral congenital trigger thumb of hand
  • Bilateral radioulnar synostosis of upper limbs
  • Brachydactyly of hand
  • Brachymesophalangia
  • Capitate-hamate synostosis
  • Carpal synostosis
  • Char syndrome
  • Cleft mandible
  • Cleidocranial dysostosis
  • Congenital abnormal fusion of carpal bone
  • Congenital abnormal fusion of humerus
  • Congenital abnormal fusion of metacarpal bone
  • Congenital abnormal fusion of radius
  • Congenital abnormal fusion of ulna
  • Congenital abnormal shape of carpal bone
  • Congenital abnormal shape of clavicle
  • Congenital abnormal shape of humerus
  • Congenital abnormal shape of metacarpal bone
  • Congenital abnormal shape of radius
  • Congenital abnormal shape of scapula
  • Congenital abnormal shape of ulna
  • Congenital absence of carpal bone
  • Congenital absence of scapula
  • Congenital anomalies of elbow and upper arm
  • Congenital anomaly of bone of shoulder girdle
  • Congenital anomaly of carpal bone
  • Congenital anomaly of finger
  • Congenital anomaly of humerus
  • Congenital anomaly of ilium
  • Congenital anomaly of metacarpal bone
  • Congenital anomaly of ossicles of ear
  • Congenital anomaly of radius
  • Congenital anomaly of scapula
  • Congenital anomaly of ulna
  • Congenital anomaly of upper limb
  • Congenital bent humerus
  • Congenital bent radius
  • Congenital bent scapula
  • Congenital cubitus varus
  • Congenital deformity of left finger
  • Congenital deformity of left upper limb
  • Congenital deformity of right finger
  • Congenital deformity of right upper limb
  • Congenital deformity of scapula
  • Congenital dislocation of elbow
  • Congenital dislocation of knee
  • Congenital dislocation of patella
  • Congenital dislocation of radial head
  • Congenital elevation of left scapula
  • Congenital elevation of right scapula
  • Congenital elevation of scapula
  • Congenital elevation of scapula
  • Congenital glenoid dysplasia
  • Congenital humeral varus
  • Congenital hypoplasia of cerebrum
  • Congenital hypoplasia of clavicle
  • Congenital hypoplasia of clavicle
  • Congenital hypoplasia of radius
  • Congenital macrodactyly
  • Congenital malformation of thumb
  • Congenital malposition of carpal bone
  • Congenital malposition of humerus
  • Congenital malposition of metacarpal bone
  • Congenital malposition of radius
  • Congenital malposition of ulna
  • Congenital negative ulnar variant of wrist
  • Congenital positive ulnar variant of wrist
  • Congenital pseudoarthrosis of clavicle
  • Congenital subluxation of carpus
  • Congenital thickening of humerus
  • Congenital thickening of radius
  • Congenital thickening of scapula
  • Congenital thickening of ulna
  • Congenital trigger finger and trigger thumb
  • Congenital trigger finger of left hand
  • Congenital trigger finger of right hand
  • Congenital trigger thumb
  • Congenital trigger thumb of left hand
  • Congenital trigger thumb of right hand
  • Congenital ulnar positive variant of left wrist
  • Congenital ulnar positive variant of right wrist
  • Constricting band of extremity
  • Constriction ring of upper limb with acrosyndactyly and amputation
  • Constriction ring of upper limb with lymphedema
  • Constriction ring syndrome
  • Constriction ring syndrome of upper limb
  • Craniolacunia
  • Deformity of humerus
  • Deformity of humerus
  • Deformity of radius
  • Deformity of scapula
  • Delta phalanx of finger
  • Distal radioulnar synostosis
  • Duane-radial ray syndrome
  • Duane's syndrome
  • Duplication of humerus
  • Duplication of radius
  • Duplication of upper limb
  • Duplication of whole hand
  • Duplication of whole limb
  • Duplication of whole upper limb
  • Ectodermal dysplasia with nail defect
  • Failure of differentiation of bones of forearm
  • Form of clavicle - finding
  • Generalized spacing of maxillary teeth
  • Hand-foot-genital syndrome
  • Hemifacial microsomia
  • Hemifacial microsomia with radial defect syndrome
  • Hitch-hiker thumb
  • Humeroradial synostosis
  • Humeroradioulnar synostosis
  • Humerus trochlea aplasia
  • Hydrocephalus, costovertebral dysplasia, Sprengel anomaly syndrome
  • Hyperphalangy
  • Hyperphalangy
  • Hypoplasia of corpus callosum
  • Hypoplasia of radius
  • Incomplete ossification of carpal bone
  • Incomplete ossification of humerus
  • Incomplete ossification of metacarpal bone
  • Incomplete ossification of radius
  • Incomplete ossification of scapula
  • Incomplete ossification of ulna
  • L1 syndrome
  • Lack of ossification of carpal bone
  • Lack of ossification of humerus
  • Lack of ossification of metacarpal bone
  • Lack of ossification of radius
  • Lack of ossification of scapula
  • Lack of ossification of ulna
  • Liebenberg syndrome
  • Localized congenital skull defect
  • Lunate-triquetrum synostosis
  • Lymphedema of upper limb
  • Macrodactylia of fingers
  • Macrodactylia of fingers
  • Macrodactyly of fingers - simple
  • Macrodactyly of fingers- fatty nerve tumor
  • Macrodactyly of hand
  • Macrodactyly of hand
  • Macrodactyly of thumb
  • Madelung's deformity
  • Manus plana
  • Mirror hands
  • Morava Mehes syndrome
  • Ophthalmo-acromelic syndrome
  • Oto-onycho-peroneal syndrome
  • Overgrowth of partial upper limb
  • Overgrowth of upper limb
  • Overgrowth of whole upper limb
  • Parietal foramina with clavicular hypoplasia
  • Partial radial absence
  • Pelvis shoulder dysplasia
  • PHAVER syndrome
  • Polydactyly of thumb
  • Polydactyly of thumb
  • Polysyndactyly
  • Polysyndactyly syndrome
  • Proximal radioulnar synostosis
  • Radioulnar dysostosis
  • Radioulnar synostosis
  • Radioulnar synostosis and dislocation of radial head
  • Radioulnar synostosis of left arm
  • Radioulnar synostosis of right arm
  • Radioulnar synostosis with amegakaryocytic thrombocytopenia syndrome
  • Radioulnar synostosis with developmental delay and hypotonia syndrome
  • Radioulnar synostosis with microcephaly and scoliosis syndrome
  • Robin sequence
  • Scaphoid-lunate synostosis
  • Schmitt Gillenwater Kelly syndrome
  • Short stature, Pierre Robin sequence, cleft mandible, hand anomalies, clubfoot syndrome
  • Stapes ankylosis with broad thumb and toe syndrome
  • Supernumerary metacarpal bone
  • Thin clavicle
  • Tibial hemimelia, polysyndactyly, triphalangeal thumb syndrome
  • Triphalangeal thumb
  • Triphalangeal thumb
  • Triphalangeal thumb and dislocation of patella syndrome
  • Triphalangeal thumb and polysyndactyly syndrome
  • Triphalangeal thumb with brachyectrodactyly syndrome
  • Triphalangeal thumbs with onychodystrophy
  • Ulnar dimelia
  • Ulnar mammary syndrome
  • Undergrowth of whole hand
  • Upper limb defect with eye and ear abnormalities syndrome
  • Windblown hand

Diagnostic Related Groups

The ICD-10 code Q74.0 is grouped in the following groups for version MS-DRG V37.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC).
applicable from 10/01/2019 through 09/30/2020.


Present on Admission (POA)

Q74.0 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here .

CMS POA Indicator Options and Definitions
POA Indicator CodePOA Reason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Convert Q74.0 to ICD-9

  • 755.53 - Radioulnar synostosis (Approximate Flag)
  • 755.54 - Madelung's deformity (Approximate Flag)
  • 755.56 - Accessory carpal bones (Approximate Flag)
  • 755.57 - Macrodactylia (fingers) (Approximate Flag)
  • 755.59 - Upper limb anomaly NEC (Approximate Flag)

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Congenital malformations and deformations of the musculoskeletal system (Q65-Q79)
      • Other congenital malformations of limb (Q74) (s)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Patients

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

A birth defect may affect how the body looks, works or both. Some birth defects like cleft lip or neural tube defects are structural problems that can be easy to see. To find others, like heart defects, doctors use special tests. Birth defects can range from mild to severe. Causes can include

  • Genetics
  • Exposures to medicines or chemicals. For example, alcohol abuse can cause fetal alcohol syndrome.
  • Infections during pregnancy
  • Certain medicines. Before you get pregnant, talk to your health care provider about any medicines you take.
  • Not getting enough of certain nutrients. For example, not getting enough folic acid before and during pregnancy is a key factor in causing neural tube defects.

For most birth defects, the cause is unknown.

Health care providers can diagnose certain birth defects during pregnancy, with prenatal tests. That's why it important to get regular prenatal care. Other birth defects may not be found until after the baby is born. Sometimes the defect is obvious right away. Other times, the health care provider may not discover it until later in life.

Babies with birth defects often need special care and treatments. The treatments may include surgery, medicines, assistive devices, and therapies.

Centers for Disease Control and Prevention

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