2026 ICD-10-CM Diagnosis Code Q44.79Other congenital malformations of liver

ICD-10-CM Codes›Q00-Q99›Q38-Q45›Q44

ICD-10-CM Q44.79
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q44.79 is a billable ICD-10-CM diagnosis code for other congenital malformations of liver. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 441 through 443. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Digestive congenital anomalies.

Code Identity

ICD-10-CM Code
Q44.79
Billable Status
Yes — Valid for Submission
Code Describes
Other congenital malformations of liver
Short Description
Other congenital malformations of liver
Same as the full description in the CMS dataset.
Parent Code
Q44.7
Other congenital malformations of liver

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ38-Q45Other congenital malformations of the digestive system
CategoryQ44Congenital malformations of gallbladder, bile ducts and liver
This CodeQ44.79Other congenital malformations of liver

Present on Admission (POA)Billing

Q44.79 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Abnormal liver lobulation
  • Absence of liver
  • Accessory liver
  • Agenesis of liver
  • Atrophy of liver
  • Congenital abnormal fusion of liver lobes
  • Congenital abnormal shape of liver
  • Congenital absence of liver
  • Congenital absence of liver and/or gallbladder
  • Congenital absence of lobe of liver
  • Congenital atrophy of left lobe of liver
  • Congenital duplication of liver
  • Congenital floating liver
  • Congenital hepatic fibrosis
  • Congenital hepatomegaly
  • Congenital hyperplasia of muscle
  • Congenital liver grooves
  • Congenital malposition of liver
  • Congenital microhepatia
  • Congenital syphilitic hepatomegaly
  • Ectopic liver
  • Familial aplasia of the vermis
  • Fibrosis of pancreas
  • Floating liver
  • Focal nodular hypoplasia of liver
  • Hepatic fibrosis, renal cyst, intellectual disability syndrome
  • Joubert syndrome
  • Joubert syndrome with congenital hepatic fibrosis
  • Liver and/or biliary duplication
  • Liver hyperplasia
  • Liver in central position
  • Liver in left sided position
  • Microhepatia
  • Muscular hypertrophy, hepatomegaly, polyhydramnios syndrome
  • NPHP3-related Meckel-like syndrome
  • Renal hepatic pancreatic dysplasia
  • Riedel's lobe of liver
  • Supernumerary liver lobe
  • Trilobular liver

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Accessory liver
  • Congenital absence of liver
  • Congenital hepatomegaly

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Absence(of) (organ or part) (complete or partial)
      • liver (congenital)
    • Accessory(congenital)
      • liver
    • Agenesis
      • hepatic
    • Agenesis
      • liver
    • Distortion(s) (congenital)
      • liver
    • Duplication, duplex
      • liver
    • Hepatomegaly
      • congenital
    • Hyperplasia, hyperplastic
      • liver (congenital)
    • Hypertrophy, hypertrophic
      • liver
        • congenital
    • Hypoplasia, hypoplastic
      • liver
    • Lobulation(congenital)
      • liver, abnormal
    • Malposition
      • congenital
        • liver
    • Riedel's
      • lobe, liver

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL002
Digestive congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Joubert Syndrome

    a rare genetic syndrome characterized by the hypoplasia or absence of the cerebellar vermis. signs and symptoms include rapid breathing (hyperpnea), sleep apnea, abnormal eye movements, mental retardation, and ataxia.

  • Joubert Syndrome 17|JBTS17

    an autosomal recessive subtype of joubert syndrome caused by mutation(s) in the cplane1 gene, encoding ciliogenesis and planar polarity effector 1.

  • Joubert Syndrome 3|JBTS3

    an autosomal recessive subtype of joubert syndrome caused by mutation(s) in the ahi1 gene, encoding jouberin.

  • Joubert Syndrome 4

    a rare genetic syndrome caused by mutations in the nphp1 gene. it is characterized by the hypoplasia or absence of the cerebellar vermis. signs and symptoms include rapid breathing (hyperpnea), sleep apnea, abnormal eye movements, mental retardation, and ataxia.

  • Joubert Syndrome 7|JBTS7

    an autosomal recessive sub-type of joubert syndrome caused by mutation(s) in the rpgrip1l gene, encoding a protein thought to function in programmed cell death. it is characterized by cerebellar and oculomotor apraxia, hypotonia and psychomotor delay, neonatal respiratory abnormalities, renal abnormalities, and retinal dystrophy.

  • Joubert Syndrome 9|JBTS9

    an autosomal recessive subtype of joubert syndrome caused by mutation(s) in the cc2d2a gene, encoding coiled-coil and c2 domain-containing protein 2a.

  • Congenital Hepatic Fibrosis

    a congenital disorder usually inherited in an autosomal recessive pattern. it affects the hepatobiliary system and the kidneys. it is characterized by liver fibrosis, portal hypertension, and renal cysts.

Code History & ChangesHistory

Replacement Q44.79 replaces the following previously assigned code(s):

  • Q44.7 - Other congenital malformations of liver
FY 2024AddedAdded to the ICD-10-CM code setEffective October 1, 2023.
FY 2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q44.79Overview

Is Q44.79 (Other congenital malformations of liver) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other congenital malformations of liver on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q44.79 group to?

When other congenital malformations of liver is the principal diagnosis on an inpatient stay, it groups to MS-DRG 441, 442, 443, with relative weights from 0.6997 to 1.7947 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q44.79 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other congenital malformations of liver on inpatient claims.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.