2026 ICD-10-CM Diagnosis Code Q27.9Congenital malformation of peripheral vascular system, unspecified

ICD-10-CM CodesQ00-Q99Q20-Q28Q27

ICD-10-CM Q27.9
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q27.9 is a billable ICD-10-CM diagnosis code for congenital malformation of peripheral vascular system, unspecified. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 299 through 301. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q27.9
Billable Status
Yes — Valid for Submission
Code Describes
Congenital malformation of peripheral vascular system, unspecified
Short Description
Congenital malformation of peripheral vascular system, unsp
Parent Code
Other congenital malformations of peripheral vascular system

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ27Other congenital malformations of peripheral vascular system
This CodeQ27.9Congenital malformation of peripheral vascular system, unspecified

Present on Admission (POA)Billing

Q27.9 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Abnormal umbilical cord
  • Agenesis of artery
  • Angio-osteohypertrophic syndrome
  • Angioosteohypotrophic syndrome
  • Arterial anomaly of umbilical cord
  • Arterial malformation
  • Bilateral congenital anomaly of blood vessels of lower limbs
  • Bilateral congenital anomaly of blood vessels of upper limbs
  • Blue rubber bleb nevus
  • Capillary malformation
  • Capillary malformation-arteriovenous malformation syndrome
  • Capillary-venous malformation
  • Capillary-venous-lymphatic malformation
  • CLOVE syndrome
  • Congenital abnormality of systemic artery
  • Congenital abnormality of systemic vein
  • Congenital abnormality of vein
  • Congenital anomaly of blood vessel of left lower limb
  • Congenital anomaly of blood vessel of left upper limb
  • Congenital anomaly of blood vessel of limb
  • Congenital anomaly of blood vessel of lower limb
  • Congenital anomaly of blood vessel of right lower limb
  • Congenital anomaly of blood vessel of right upper limb
  • Congenital anomaly of blood vessel of upper limb
  • Congenital anomaly of gastrointestinal vessel
  • Congenital anomaly of peripheral blood vessel
  • Congenital dysplasia of left lobe of lung co-occurrent with congenital vascular malformation
  • Congenital dysplasia of right lobe of lung co-occurrent with congenital vascular malformation
  • Congenital vascular malformation
  • Congenital vascular nevus
  • Congenital venous malformation of skin
  • Cutaneous capillary malformation
  • Cutaneous vascular malformation
  • Diffuse capillary malformation with overgrowth
  • Diffuse lymphatic malformation
  • Dysplasia of lung
  • Four vessels in umbilical cord
  • Hereditary vascular fragility
  • Infantile hemangioma
  • Infantile hemangioma of rare localization
  • Microcephaly-capillary malformation syndrome
  • Mixed vascular malformation
  • Peripheral venous malformation
  • PHACE syndrome
  • Posterior cord syndrome due to vascular malformation
  • Primary intraosseous venous malformation
  • Short umbilical cord
  • Vascular anomaly of umbilical cord
  • Vascular disorder of inner ear
  • Vascular malformation of inner ear
  • Venous anomaly of umbilical cord
  • Venous malformation
  • Venous remnant
  • Venous valvular anomaly
  • Venous-lymphatic malformation

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Anomaly of artery or vein NOS

Index to Diseases and InjuriesGuidance

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Accessory(congenital)
      • blood vessels NEC
    • Agenesis
      • artery (peripheral)
    • Agenesis
      • vein (s) (peripheral)
    • Anomaly, anomalous(congenital) (unspecified type)
      • artery (peripheral)
    • Anomaly, anomalous(congenital) (unspecified type)
      • artery (peripheral)
        • peripheral
    • Anomaly, anomalous(congenital) (unspecified type)
      • capillary
    • Anomaly, anomalous(congenital) (unspecified type)
      • peripheral vascular system
    • Anomaly, anomalous(congenital) (unspecified type)
      • vascular
    • Anomaly, anomalous(congenital) (unspecified type)
      • vein (s) (peripheral)
    • Anomaly, anomalous(congenital) (unspecified type)
      • vessel (s)
    • Defect, defective
      • vascular (local)
        • congenital
    • Deformity
      • artery (congenital) (peripheral) NOS
    • Deformity
      • vein (congenital)
    • Distribution vessel, atypical
    • Malformation(congenital)
      • peripheral vascular system
    • Malformation(congenital)
      • vascular system, peripheral

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Short Umbilical Cord

    an umbilical cord at term that is less than 35 cm in length.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q27.9 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.60 Unsp prpherl vasc anomal
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q27.9Overview

Is Q27.9 (Other congenital malformations of peripheral vascular system) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital malformation of peripheral vascular system, unspecified on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q27.9 group to?

When congenital malformation of peripheral vascular system, unspecified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 299, 300, 301, with relative weights from 0.7197 to 1.6327 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q27.9 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital malformation of peripheral vascular system, unspecified on inpatient claims.

What is the ICD-9 equivalent of Q27.9?

Under the General Equivalence Mappings, congenital malformation of peripheral vascular system, unspecified converts to ICD-9-CM 747.60 (unsp prpherl vasc anomal). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.