2027 ICD-10-CM Diagnosis Code Q27.0Congenital absence and hypoplasia of umbilical artery

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q27

ICD-10-CM Q27.0
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q27.0 is a billable ICD-10-CM diagnosis code for congenital absence and hypoplasia of umbilical artery. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 299 through 301. The code is exempt from POA reporting. Coders also document this condition as arterial anomaly of umbilical cord. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q27.0
Billable Status
Yes — Valid for Submission
Code Describes
Congenital absence and hypoplasia of umbilical artery
Short Description
Congenital absence and hypoplasia of umbilical artery
Same as the full description in the CMS dataset.
Parent Code
Q27
Other congenital malformations of peripheral vascular system

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ27Other congenital malformations of peripheral vascular system
This CodeQ27.0Congenital absence and hypoplasia of umbilical artery

Present on Admission (POA)Billing

Q27.0 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of the circulatory system (Q20-Q28).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Arterial anomaly of umbilical cord
  • Congenital anomaly of umbilical artery
  • Congenital hypoplasia of umbilical artery
  • Single umbilical artery
  • Single umbilical cord artery type I
  • Single umbilical cord artery type II
  • Single umbilical cord artery type III
  • Single umbilical cord artery type IV

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q27.0: its own notes plus those printed at Q27 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Single umbilical artery

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Q27 Other congenital malformations of peripheral vascular system applies to 12 codes
  • anomalies of cerebral and precerebral vessels (Q28.0-Q28.3)
  • anomalies of coronary vessels (Q24.5)
  • anomalies of pulmonary artery (Q25.5-Q25.7)
  • congenital retinal aneurysm (Q14.1)
  • hemangioma and lymphangioma (D18.-)
From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q27.0, its category, or a range that includes it.

Excludes1 1

These codes carry an Excludes1 note naming Q27.0: they are not reported together with it, unless the two conditions are unrelated.

  • P02.69 Newborn affected by other conditions of umbilical cord
    newborn affected by single umbilical artery (Q27.0)

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Health Problems in Pregnancy

A health problem in pregnancy is any disease or condition that could affect your health or the health of your fetus. Some health problems may make it more likely that you will have a high-risk pregnancy. A high-risk pregnancy is one in which you, your fetus, or both are at higher risk for health problems than in a typical pregnancy.

The full article covers:

  • What are health problems in pregnancy?
  • What raises my risk for health problems during pregnancy?
  • Can chronic health conditions cause problems in pregnancy?
  • Can health problems in pregnancy be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q27.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.5 Umbilical artery absence
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q27.0Overview

What is the ICD-10 code for congenital absence and hypoplasia of umbilical artery?

The ICD-10-CM code for congenital absence and hypoplasia of umbilical artery is Q27.0 (sometimes written as Q270). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q27.0 (Other congenital malformations of peripheral vascular system) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital absence and hypoplasia of umbilical artery on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q27.0 group to?

When congenital absence and hypoplasia of umbilical artery is the principal diagnosis on an inpatient stay, it groups to MS-DRG 301, 300, 299, with relative weights from 0.7132 to 1.5840 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q27.0 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital absence and hypoplasia of umbilical artery on inpatient claims. The code appears in the Congenital malformations of the circulatory system (Q20-Q28) range of the CMS exempt list.

What is the ICD-9 equivalent of Q27.0?

Under the General Equivalence Mappings, congenital absence and hypoplasia of umbilical artery converts to ICD-9-CM 747.5 (umbilical artery absence). The mapping is a direct match.