2026 ICD-10-CM Diagnosis Code Q27.0Congenital absence and hypoplasia of umbilical artery

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q27

ICD-10-CM Q27.0
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q27.0 is a billable ICD-10-CM diagnosis code for congenital absence and hypoplasia of umbilical artery. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 299 through 301. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q27.0
Billable Status
Yes — Valid for Submission
Code Describes
Congenital absence and hypoplasia of umbilical artery
Short Description
Congenital absence and hypoplasia of umbilical artery
Same as the full description in the CMS dataset.
Parent Code
Q27
Other congenital malformations of peripheral vascular system

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ27Other congenital malformations of peripheral vascular system
This CodeQ27.0Congenital absence and hypoplasia of umbilical artery

Present on Admission (POA)Billing

Q27.0 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Arterial anomaly of umbilical cord
  • Congenital anomaly of umbilical artery
  • Congenital hypoplasia of umbilical artery
  • Single umbilical artery
  • Single umbilical cord artery type I
  • Single umbilical cord artery type II
  • Single umbilical cord artery type III
  • Single umbilical cord artery type IV

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Single umbilical artery

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Absence(of) (organ or part) (complete or partial)
      • artery (congenital) (peripheral)
        • umbilical
    • Absence(of) (organ or part) (complete or partial)
      • umbilical artery, congenital
    • Agenesis
      • artery (peripheral)
        • umbilical
    • Anomaly, anomalous(congenital) (unspecified type)
      • artery (peripheral)
        • umbilical
    • Anomaly, anomalous(congenital) (unspecified type)
      • umbilical artery
    • Artery, arterial
      • single umbilical
    • Atresia, atretic
      • artery NEC
        • umbilical
    • Deformity
      • artery (congenital) (peripheral) NOS
        • umbilical
    • Hypoplasia, hypoplastic
      • artery (peripheral)
        • umbilical
    • Hypoplasia, hypoplastic
      • umbilical artery
    • Single
      • umbilical artery
    • Stricture
      • artery
        • congenital (peripheral)
          • umbilical

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Single Umbilical Artery

    congenital abnormality where one, instead of the usual two, umbilical artery connects the fetus to the placenta.

  • Umbilical Arteries

    specialized arterial vessels in the umbilical cord. they carry waste and deoxygenated blood from the fetus to the mother via the placenta. in humans, there are usually two umbilical arteries but sometimes one.

  • Single Umbilical Artery

    the absence of one of the two umbilical arteries.

Patient EducationClinical

Health Problems in Pregnancy

A health problem in pregnancy is any disease or condition that could affect your health or the health of your fetus. Some health problems may make it more likely that you will have a high-risk pregnancy. A high-risk pregnancy is one in which you, your fetus, or both are at higher risk for health problems than in a typical pregnancy.

The full article covers:

  • What are health problems in pregnancy?
  • What raises my risk for health problems during pregnancy?
  • Can chronic health conditions cause problems in pregnancy?
  • Can health problems in pregnancy be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q27.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.5 Umbilical artery absence
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q27.0Overview

Is Q27.0 (Other congenital malformations of peripheral vascular system) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital absence and hypoplasia of umbilical artery on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q27.0 group to?

When congenital absence and hypoplasia of umbilical artery is the principal diagnosis on an inpatient stay, it groups to MS-DRG 299, 300, 301, with relative weights from 0.7197 to 1.6327 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q27.0 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital absence and hypoplasia of umbilical artery on inpatient claims.

What is the ICD-9 equivalent of Q27.0?

Under the General Equivalence Mappings, congenital absence and hypoplasia of umbilical artery converts to ICD-9-CM 747.5 (umbilical artery absence). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.