2027 ICD-10-CM Diagnosis Code Q25.6Stenosis of pulmonary artery
ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q25
- Billable — Valid for Submission
- MCC — Major Complication or Comorbidity
- POA Exempt
- Chronic Condition
Q25.6 is a billable ICD-10-CM diagnosis code for stenosis of pulmonary artery. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 306 through 307. As a secondary diagnosis, it counts as a major complication or comorbidity (MCC) and places an inpatient stay in the highest severity level of its MS-DRG family. It does not count, however, when the principal diagnosis is one of 11 closely related codes. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q25.6 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of the circulatory system (Q20-Q28).
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Café-au-lait macules with pulmonary stenosis
- Congenital absence of abdominal muscle
- Congenital peripheral pulmonary artery stenosis
- Congenital retinal aneurysm
- Congenital stenosis of left pulmonary artery
- Congenital stenosis of pulmonary artery
- Congenital stenosis of right pulmonary artery
- Congenital supravalvular pulmonary stenosis
- Congenital vascular anomaly of eye
- Peripheral pulmonary artery stenosis
- Prune belly syndrome
- Prune belly syndrome with pulmonic stenosis, intellectual disability and deafness
- Pulmonary trunk stenosis
- Pulmonic stenosis and congenital nephrosis
- Retinal arterial macroaneurysm with supravalvular pulmonic stenosis
- Retinal macroaneurysm
- Stenosis of left pulmonary artery
- Stenosis of pulmonary artery
- Stenosis of right pulmonary artery
- Structural abnormality of abdominal wall muscle
- Supravalvar pulmonary trunk stenosis
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to Q25.6: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- Supravalvular pulmonary stenosis
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
Notes
General instructions on how these codes are used.
- Codes from this chapter are not for use on maternal records
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name Q25.6, its category, or a range that includes it.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Malformation (congenital) See Also: Anomaly;
Stenosis, stenotic (cicatricial) See Also: Stricture;
artery NEC See Also: Arteriosclerosis; I77.1
pulmonary (congenital) Q25.6
pulmonary (artery) (congenital) Q25.6
supravalvular Q25.6
Stricture See Also: Stenosis;
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Patient EducationClinical
Congenital Heart Defects
Congenital heart defects (CHDs) are problems with the structure of the heart. "Congenital" means that that the problems are present at birth. These defects happen when a fetus's heart doesn't develop normally during pregnancy. Congenital heart defects are the most common type of birth defect.
The full article covers:
- What are congenital heart defects?
- What causes congenital heart defects?
- Who is more likely to have a baby with a congenital heart defect?
- What are the symptoms of congenital heart defects?
- What other problems do congenital heart defects cause?
- How are congenital heart defects diagnosed?
- What are the treatments for congenital heart defects?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q25.6 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q25.6Overview
What is the ICD-10 code for stenosis of pulmonary artery?
The ICD-10-CM code for stenosis of pulmonary artery is Q25.6 (sometimes written as Q256). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is Q25.6 (Congenital malformations of great arteries) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report stenosis of pulmonary artery on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does Q25.6 group to?
When stenosis of pulmonary artery is the principal diagnosis on an inpatient stay, it groups to MS-DRG 306, 307, with relative weights from 0.9146 to 1.5457 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q25.6 a CC or MCC?
CMS lists Q25.6 as an MCC (major complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it places the inpatient stay in the highest-weighted DRG of its severity family. It does not count when the principal diagnosis is one of the 11 closely related codes in its exclusion list.
Is Q25.6 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for stenosis of pulmonary artery on inpatient claims. The code appears in the Congenital malformations of the circulatory system (Q20-Q28) range of the CMS exempt list.
