2026 ICD-10-CM Diagnosis Code Q25.6Stenosis of pulmonary artery

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q25

ICD-10-CM Q25.6
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q25.6 is a billable ICD-10-CM diagnosis code for stenosis of pulmonary artery. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 306 through 307. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q25.6
Billable Status
Yes — Valid for Submission
Code Describes
Stenosis of pulmonary artery
Short Description
Stenosis of pulmonary artery
Same as the full description in the CMS dataset.
Parent Code
Q25
Congenital malformations of great arteries

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ25Congenital malformations of great arteries
This CodeQ25.6Stenosis of pulmonary artery

Present on Admission (POA)Billing

Q25.6 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Café-au-lait macules with pulmonary stenosis
  • Congenital absence of abdominal muscle
  • Congenital peripheral pulmonary artery stenosis
  • Congenital retinal aneurysm
  • Congenital stenosis of left pulmonary artery
  • Congenital stenosis of pulmonary artery
  • Congenital stenosis of right pulmonary artery
  • Congenital supravalvular pulmonary stenosis
  • Congenital vascular anomaly of eye
  • Peripheral pulmonary artery stenosis
  • Prune belly syndrome
  • Prune belly syndrome with pulmonic stenosis, intellectual disability and deafness
  • Pulmonary artery stenosis
  • Pulmonary trunk stenosis
  • Pulmonic stenosis and congenital nephrosis
  • Retinal arterial macroaneurysm with supravalvular pulmonic stenosis
  • Retinal macroaneurysm
  • Stenosis of left pulmonary artery
  • Stenosis of right pulmonary artery
  • Supravalvar pulmonary trunk stenosis

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Supravalvular pulmonary stenosis

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Malformation(congenital)
      • pulmonary
        • artery
          • stenosis
    • Stenosis, stenotic(cicatricial)
      • artery NEC
        • pulmonary (congenital)
    • Stenosis, stenotic(cicatricial)
      • pulmonary (artery) (congenital)
    • Stenosis, stenotic(cicatricial)
      • pulmonary (artery) (congenital)
        • supravalvular
    • Stricture
      • artery
        • pulmonary (congenital)
    • Stricture
      • pulmonary, pulmonic
        • artery (congenital)

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Prune Belly Syndrome

    a syndrome characterized by abdominal wall musculature deficiency, cryptorchism, and urinary tract abnormalities. the syndrome derives its name from its characteristic distended abdomen with wrinkled skin.

  • Branch Pulmonary Artery Stenosis|Pulmonary Artery Stenosis, Branch (not PPS)

    narrowing of the lumen of the right or left pulmonary artery branch.

  • Congenital Pulmonary Artery Stenosis

    a congenital cardiovascular abnormality characterized by the narrowing of the lumen of the main pulmonary artery or its branches. it may be associated with other congenital heart malformations. signs and symptoms include dyspnea, tachypnea, tachycardia, fatigue, and edema.

  • Physiologic Pulmonary Artery Stenosis Murmur|Physiologic pulmonary artery stenosis

    an innocent murmur with a medium or high pitched, blowing character heard at the left middle sternal border that can also be heard at the same volume across the precordium and back that does not disappear with maneuvers but is only heard in infants less than six months of age. (acc/aha)

  • Pulmonary Artery Stenosis

    a congenital or acquired cardiovascular abnormality characterized by the narrowing of the lumen of the main pulmonary artery or its branches. signs and symptoms include dyspnea, tachypnea, tachycardia, fatigue, and edema.

  • Supravalvular Pulmonary Artery Stenosis|Pulmonary Artery Stenosis, Supravalvar

    stenosis of the pulmonary artery that occurs above the valve.

Patient EducationClinical

Congenital Heart Defects

Congenital heart defects (CHDs) are problems with the structure of the heart. "Congenital" means that that the problems are present at birth. These defects happen when a fetus's heart doesn't develop normally during pregnancy. Congenital heart defects are the most common type of birth defect.

The full article covers:

  • What are congenital heart defects?
  • What causes congenital heart defects?
  • Who is more likely to have a baby with a congenital heart defect?
  • What are the symptoms of congenital heart defects?
  • What other problems do congenital heart defects cause?
  • How are congenital heart defects diagnosed?
  • What are the treatments for congenital heart defects?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q25.6 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.39 Oth anom pul artery/circ
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q25.6Overview

Is Q25.6 (Congenital malformations of great arteries) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report stenosis of pulmonary artery on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q25.6 group to?

When stenosis of pulmonary artery is the principal diagnosis on an inpatient stay, it groups to MS-DRG 306, 307, with relative weights from 0.9132 to 1.5758 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q25.6 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for stenosis of pulmonary artery on inpatient claims.

What is the ICD-9 equivalent of Q25.6?

Under the General Equivalence Mappings, stenosis of pulmonary artery converts to ICD-9-CM 747.39 (oth anom pul artery/circ). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.