2027 ICD-10-CM Diagnosis Code Q25.5Atresia of pulmonary artery

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q25

ICD-10-CM Q25.5
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q25.5 is a billable ICD-10-CM diagnosis code for atresia of pulmonary artery. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 306 through 307. As a secondary diagnosis, it counts as a major complication or comorbidity (MCC) and places an inpatient stay in the highest severity level of its MS-DRG family. It does not count, however, when the principal diagnosis is one of 11 closely related codes. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Q25.5 does not risk-adjust for Medicare Advantage under the CMS-HCC V28 model. It still risk-adjusts in the RxHCC Part D (V08) category 191 for payment year 2027.

Code Identity

ICD-10-CM Code
Q25.5
Billable Status
Yes — Valid for Submission
Code Describes
Atresia of pulmonary artery
Short Description
Atresia of pulmonary artery
Same as the full description in the CMS dataset.
Parent Code
Congenital malformations of great arteries

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ25Congenital malformations of great arteries
This CodeQ25.5Atresia of pulmonary artery

Present on Admission (POA)Billing

Q25.5 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of the circulatory system (Q20-Q28).

Medicare Risk Adjustment (HCC)Billing

Q25.5 does not risk-adjust for Medicare Advantage under the CMS-HCC V28 model, but it maps to payment categories in the other CMS models shown below.

CMS-HCC V28 (Medicare Advantage Payment Model)
Not mapped
no payment category in the model that pays 100% of MA risk scores
Prior Model (CMS-HCC V24)
Not mapped under V24
this diagnosis newly risk-adjusts under the V28 model
Part D (RxHCC)
RxHCC 191 — Ventricular Septal Defect and Major Congenital Heart Disorders
also risk-adjusts in the Part D prescription drug model (V08)

Source: CMS Payment Year 2027 risk adjustment mappings and model software. Weights are relative factors, not dollar amounts; a beneficiary's total RAF also includes demographics and interactions. Browse all CMS-HCC categories.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Atresia of pulmonary artery with septal defect
  • Atresia of pulmonary trunk with absent left pulmonary artery
  • Atresia of pulmonary trunk with absent right pulmonary artery
  • Confluent pulmonary arteries
  • Congenital absence of left pulmonary artery
  • Congenital absence of right pulmonary artery
  • Congenital atresia of pulmonary artery
  • Congenital atresia of pulmonary valve
  • Pulmonary atresia with absent pulmonary artery
  • Pulmonary atresia with confluent pulmonary arteries
  • Pulmonary trunk atresia
  • Solitary aortic trunk with pulmonary atresia

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q25.5: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q25.5, its category, or a range that includes it.

Excludes2 1

These codes carry an Excludes2 note naming Q25.5: its condition is not part of those codes, and both may be reported when the patient has both.

  • Q27 Other congenital malformations of peripheral vascular system
    anomalies of pulmonary artery (Q25.5-Q25.7)

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Congenital Heart Defects

Congenital heart defects (CHDs) are problems with the structure of the heart. "Congenital" means that that the problems are present at birth. These defects happen when a fetus's heart doesn't develop normally during pregnancy. Congenital heart defects are the most common type of birth defect.

The full article covers:

  • What are congenital heart defects?
  • What causes congenital heart defects?
  • Who is more likely to have a baby with a congenital heart defect?
  • What are the symptoms of congenital heart defects?
  • What other problems do congenital heart defects cause?
  • How are congenital heart defects diagnosed?
  • What are the treatments for congenital heart defects?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q25.5 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.31 Pulmon art coarct/atres
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q25.5Overview

What is the ICD-10 code for atresia of pulmonary artery?

The ICD-10-CM code for atresia of pulmonary artery is Q25.5 (sometimes written as Q255). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q25.5 (Congenital malformations of great arteries) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report atresia of pulmonary artery on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q25.5 group to?

When atresia of pulmonary artery is the principal diagnosis on an inpatient stay, it groups to MS-DRG 306, 307, with relative weights from 0.9146 to 1.5457 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q25.5 a CC or MCC?

CMS lists Q25.5 as an MCC (major complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it places the inpatient stay in the highest-weighted DRG of its severity family. It does not count when the principal diagnosis is one of the 11 closely related codes in its exclusion list.

Is Q25.5 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for atresia of pulmonary artery on inpatient claims. The code appears in the Congenital malformations of the circulatory system (Q20-Q28) range of the CMS exempt list.

Does Q25.5 risk-adjust for Medicare Advantage payment?

Not for Medicare Advantage: Q25.5 maps to no category in the CMS-HCC V28 model. It still risk-adjusts in the RxHCC Part D (V08) category 191 (Ventricular Septal Defect and Major Congenital Heart Disorders).