2027 ICD-10-CM Diagnosis Code Q23.1Congenital insufficiency of aortic valve

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q23

ICD-10-CM Q23.1
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q23.1 is a billable ICD-10-CM diagnosis code for congenital insufficiency of aortic valve. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 306 through 307. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 66 closely related codes. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q23.1
Billable Status
Yes — Valid for Submission
Code Describes
Congenital insufficiency of aortic valve
Short Description
Congenital insufficiency of aortic valve
Same as the full description in the CMS dataset.
Parent Code
Congenital malformations of aortic and mitral valves

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ23Congenital malformations of aortic and mitral valves
This CodeQ23.1Congenital insufficiency of aortic valve

Present on Admission (POA)Billing

Q23.1 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of the circulatory system (Q20-Q28).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Abnormal number of aortic valve cusps
  • Anterior-posterior orientation of bicuspid aortic valve
  • Bicuspid aortic valve
  • Bicuspid aortic valve-associated aortopathy
  • Bicuspid cardiac valve
  • Bicuspid doming of aortic cusp
  • Congenital hypoplasia of aortic valve
  • Congenital insufficiency of aortic valve
  • Congenital prolapse of aortic valve
  • Familial bicuspid aortic valve
  • Hypoplasia of aortic valve cusp
  • Laubry Pezzi syndrome
  • Patent ductus arteriosus, bicuspid aortic valve, hand anomaly syndrome
  • Right-left orientation of bicuspid aortic valve

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q23.1: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Congenital aortic insufficiency

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q23.1, its category, or a range that includes it.

Excludes2 2

These codes carry an Excludes2 note naming Q23.1: its condition is not part of those codes, and both may be reported when the patient has both.

  • I35 Nonrheumatic aortic valve disorders
    aortic valve disorder specified as congenital (Q23.0, Q23.1)
  • I08 Multiple valve diseases
    multiple valve disease specified as nonrheumatic (I34.-, I35.-, I36.-, I37.-, I38.-, Q22.-, Q23.-, Q24.8-) names Q23.-, which includes this code

Use Additional Code 1

These codes say to use an additional code from the note, and Q23.1 is one of the codes named.

  • Q87.88 CTNNB1 syndrome
    congenital heart malformations (Q20.0-Q24.9) names Q20.0-Q24.9, which includes this code

Index to Diseases and InjuriesGuidance

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Congenital Aortic Valve Insufficiency

    dysfunction of the aortic valve characterized by incomplete valve closure that is present at birth.

Patient EducationClinical

Congenital Heart Defects

Congenital heart defects (CHDs) are problems with the structure of the heart. "Congenital" means that that the problems are present at birth. These defects happen when a fetus's heart doesn't develop normally during pregnancy. Congenital heart defects are the most common type of birth defect.

The full article covers:

  • What are congenital heart defects?
  • What causes congenital heart defects?
  • Who is more likely to have a baby with a congenital heart defect?
  • What are the symptoms of congenital heart defects?
  • What other problems do congenital heart defects cause?
  • How are congenital heart defects diagnosed?
  • What are the treatments for congenital heart defects?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q23.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
746.4 Cong aorta valv insuffic
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q23.1Overview

What is the ICD-10 code for congenital insufficiency of aortic valve?

The ICD-10-CM code for congenital insufficiency of aortic valve is Q23.1 (sometimes written as Q231). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q23.1 (Congenital malformations of aortic and mitral valves) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital insufficiency of aortic valve on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q23.1 group to?

When congenital insufficiency of aortic valve is the principal diagnosis on an inpatient stay, it groups to MS-DRG 306, 307, with relative weights from 0.9146 to 1.5457 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q23.1 a CC or MCC?

CMS lists Q23.1 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 66 closely related codes in its exclusion list.

Is Q23.1 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital insufficiency of aortic valve on inpatient claims. The code appears in the Congenital malformations of the circulatory system (Q20-Q28) range of the CMS exempt list.