2026 ICD-10-CM Diagnosis Code Q14.0Congenital malformation of vitreous humor

ICD-10-CM Codes›Q00-Q99›Q10-Q18›Q14

ICD-10-CM Q14.0
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q14.0 is a billable ICD-10-CM diagnosis code for congenital malformation of vitreous humor. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 124 through 125. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Congenital malformations of eye, ear, face, neck.

Code Identity

ICD-10-CM Code
Q14.0
Billable Status
Yes — Valid for Submission
Code Describes
Congenital malformation of vitreous humor
Short Description
Congenital malformation of vitreous humor
Same as the full description in the CMS dataset.
Parent Code
Q14
Congenital malformations of posterior segment of eye

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ10-Q18Congenital malformations of eye, ear, face and neck
CategoryQ14Congenital malformations of posterior segment of eye
This CodeQ14.0Congenital malformation of vitreous humor

Present on Admission (POA)Billing

Q14.0 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Bilateral persistent hyperplastic primary vitreous
  • Bilateral vitreous degeneration of eyes
  • Congenital malformation of vitreous humor
  • Congenital vitreous cyst
  • Congenital vitreous opacity
  • Congenital vitreous opacity of bilateral eyes
  • Congenital vitreous opacity of left eye
  • Congenital vitreous opacity of right eye
  • Fundus coloboma
  • Lenticonus
  • Microcornea
  • Microcornea, posterior megalolenticonus, persistent fetal vasculature, coloboma syndrome
  • Mittendorf dot
  • Persistent hyaloid artery
  • Persistent hyperplastic primary vitreous
  • Persistent hyperplastic primary vitreous of left eye
  • Persistent hyperplastic primary vitreous of right eye
  • Posterior lenticonus
  • Retinal dysplasia
  • Vestigial remnants of canal of Cloquet
  • Vitreoretinal dysplasia
  • Vitreous opacities
  • Vitreous opacity of bilateral eyes
  • Vitreous opacity of left eye
  • Vitreous opacity of right eye

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Congenital vitreous opacity

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Anomaly, anomalous(congenital) (unspecified type)
      • vitreous body or humor
    • Opacity, opacities
      • vitreous (humor) NEC
        • congenital
    • Persistence, persistent(congenital)
      • canal of Cloquet
    • Persistence, persistent(congenital)
      • hyaloid
        • artery (generally incomplete)
    • Persistence, persistent(congenital)
      • primary (deciduous)
        • vitreous hyperplasia
    • Remains
      • canal of Cloquet
    • Remnant
      • canal of Cloquet
    • Vestige, vestigial
      • structures in vitreous

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL005
Congenital malformations of eye, ear, face, neck
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Persistent Hyperplastic Primary Vitreous

    a developmental ocular anomaly in which the primary vitreous body and its surrounding hyaloid vasculature failed to regress. it is usually unilateral and characterized by cataract; microphthalmos (small eyeballs), and retrolenticular fibrovascular tissue. (from yanoff: ophthalmology, 2nd ed.)

  • Retinal Dysplasia

    congenital, often bilateral, retinal abnormality characterized by the arrangement of outer nuclear retinal cells in a palisading or radiating pattern surrounding a central ocular space. this disorder is sometimes hereditary.

  • Microcornea

    a congenital abnormality characterized by an abnormally small cornea. the horizontal corneal diameter is less than 10mm or less than 9mm in newborns. it is associated with an increased risk of glaucoma.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q14.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
743.51 Vitreous anomalies
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q14.0Overview

Is Q14.0 (Congenital malformations of posterior segment of eye) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital malformation of vitreous humor on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q14.0 group to?

When congenital malformation of vitreous humor is the principal diagnosis on an inpatient stay, it groups to MS-DRG 124, 125, with relative weights from 0.7678 to 1.3231 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q14.0 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital malformation of vitreous humor on inpatient claims.

What is the ICD-9 equivalent of Q14.0?

Under the General Equivalence Mappings, congenital malformation of vitreous humor converts to ICD-9-CM 743.51 (vitreous anomalies). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.