Version 2024

2024 ICD-10-CM Diagnosis Code H47.03

Optic nerve hypoplasia

ICD-10-CM Code:
H47.03
ICD-10 Code for:
Optic nerve hypoplasia
Is Billable?
Not Valid for Submission
Code Navigator:

Code Classification

  • Diseases of the eye and adnexa
    (H00–H59)
    • Disorders of optic nerve and visual pathways
      (H46-H47)
      • Other disorders of optic [2nd] nerve and visual pathways
        (H47)

H47.03 is a non-specific and non-billable diagnosis code code, consider using a code with a higher level of specificity for a diagnosis of optic nerve hypoplasia. The code is not specific and is NOT valid for the year 2024 for the submission of HIPAA-covered transactions. Category or Header define the heading of a category of codes that may be further subdivided by the use of 4th, 5th, 6th or 7th characters.

Specific Coding Applicable to Optic nerve hypoplasia

Non-specific codes like H47.03 require more digits to indicate the appropriate level of specificity. Consider using any of the following ICD-10-CM codes with a higher level of specificity when coding for optic nerve hypoplasia:

  • Use H47.031 for Optic nerve hypoplasia, right eye - BILLABLE CODE

  • Use H47.032 for Optic nerve hypoplasia, left eye - BILLABLE CODE

  • Use H47.033 for Optic nerve hypoplasia, bilateral - BILLABLE CODE

  • Use H47.039 for Optic nerve hypoplasia, unspecified eye - BILLABLE CODE

Clinical Information

  • Optic Nerve Hypoplasia

    a group of rare genetic disorders characterized by underdeveloped optic nerves, resulting in increased incidences of vision impairment, congenital nystagmus and strabismus. it may be syndromic, and is often associated with cns malformations.

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Patient Education


Optic Nerve Disorders

The optic nerve is a bundle of more than 1 million nerve fibers that carry visual messages. You have one connecting the back of each eye (your retina) to your brain. Damage to an optic nerve can cause vision loss. The type of vision loss and how severe it is depends on where the damage occurs. It may affect one or both eyes.

There are many different types of optic nerve disorders, including:

  • Glaucoma is a group of diseases that are the leading cause of blindness in the United States. Glaucoma usually happens when the fluid pressure inside the eyes slowly rises and damages the optic nerve.
  • Optic neuritis is an inflammation of the optic nerve. Causes include infections and immune-related illnesses such as multiple sclerosis. Sometimes the cause is unknown.
  • Optic nerve atrophy is damage to the optic nerve. Causes include poor blood flow to the eye, disease, trauma, or exposure to toxic substances.
  • Optic nerve head drusen are pockets of protein and calcium salts that build up in the optic nerve over time

Contact your health care provider if you are having vision problems. Tests for optic nerve disorders may include eye exams, ophthalmoscopy (an examination of the back of your eye), and imaging tests. Treatment depends on which disorder that you have. With some optic nerve disorders, you may get your vision back. With others, there is no treatment, or treatment may only prevent further vision loss.


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.