ICD-10-CM Code H47.03

Optic nerve hypoplasia

Version 2021 Non-Billable Code

Not Valid for Submission

H47.03 is a "header" nonspecific and non-billable code code, consider using a code with a higher level of specificity for a diagnosis of optic nerve hypoplasia. The code is NOT valid for the year 2021 for the submission of HIPAA-covered transactions.

ICD-10:H47.03
Short Description:Optic nerve hypoplasia
Long Description:Optic nerve hypoplasia

Consider the following ICD-10 codes with a higher level of specificity:

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code H47.03 are found in the index:


Clinical Information

  • OPTIC NERVE HYPOPLASIA-. a group of rare genetic disorders characterized by underdeveloped optic nerves resulting in increased incidences of vision impairment congenital nystagmus and strabismus. it may be syndromic and is often associated with cns malformations.

Code Classification

  • Diseases of the eye and adnexa (H00–H59)
    • Disorders of optic nerve and visual pathways (H46-H47)
      • Other disorders of optic [2nd] nerve and visual pathways (H47)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021

Information for Patients


Optic Nerve Disorders

The optic nerve is a bundle of more than 1 million nerve fibers that carry visual messages. You have one connecting the back of each eye (your retina) to your brain. Damage to an optic nerve can cause vision loss. The type of vision loss and how severe it is depends on where the damage occurs. It may affect one or both eyes.

There are many different types of optic nerve disorders, including:

  • Glaucoma is a group of diseases that are the leading cause of blindness in the United States. Glaucoma usually happens when the fluid pressure inside the eyes slowly rises and damages the optic nerve.
  • Optic neuritis is an inflammation of the optic nerve. Causes include infections and immune-related illnesses such as multiple sclerosis. Sometimes the cause is unknown.
  • Optic nerve atrophy is damage to the optic nerve. Causes include poor blood flow to the eye, disease, trauma, or exposure to toxic substances.
  • Optic nerve head drusen are pockets of protein and calcium salts that build up in the optic nerve over time

Contact your health care provider if you are having vision problems. Tests for optic nerve disorders may include eye exams, ophthalmoscopy (an examination of the back of your eye), and imaging tests. Treatment depends on which disorder that you have. With some optic nerve disorders, you may get your vision back. With others, there is no treatment, or treatment may only prevent further vision loss.

  • Optic glioma (Medical Encyclopedia)
  • Optic nerve atrophy (Medical Encyclopedia)
  • Optic neuritis (Medical Encyclopedia)

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