2026 ICD-10-CM Diagnosis Code Q07.9Congenital malformation of nervous system, unspecified

ICD-10-CM Codes›Q00-Q99›Q00-Q07›Q07

ICD-10-CM Q07.9
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q07.9 is a billable ICD-10-CM diagnosis code for congenital malformation of nervous system, unspecified. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Nervous system congenital anomalies.

Code Identity

ICD-10-CM Code
Q07.9
Billable Status
Yes — Valid for Submission
Code Describes
Congenital malformation of nervous system, unspecified
Short Description
Congenital malformation of nervous system, unspecified
Same as the full description in the CMS dataset.
Parent Code
Q07
Other congenital malformations of nervous system

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ00-Q07Congenital malformations of the nervous system
CategoryQ07Other congenital malformations of nervous system
This CodeQ07.9Congenital malformation of nervous system, unspecified

Present on Admission (POA)Billing

Q07.9 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Cerebrofacial dysplasia
  • Coenzyme Q10 deficiency
  • Combined malformation of central nervous system and skeletal muscle
  • Congenital anomaly of central nervous system
  • Congenital anomaly of nervous system
  • Congenital anomaly of nervous system of head/neck
  • Congenital anomaly of neural structure of trunk
  • Congenital anomaly of peripheral nerve
  • Congenital anomaly of the peripheral nervous system
  • Congenital hepatic fibrosis
  • Congenital malformation of autonomic nervous system
  • Congenital malformation of the meninges
  • Congenital polyneuropathy
  • Cortical dysgenesis with pontocerebellar hypoplasia due to TUBB3 mutation
  • Crome syndrome
  • Cyprus facial neuromusculoskeletal syndrome
  • Ectodermal dysplasia, intellectual disability, central nervous system malformation syndrome
  • Encephalopathy, hypertrophic cardiomyopathy, renal tubular disease syndrome
  • FBLN1-related developmental delay, central nervous system anomaly, syndactyly syndrome
  • Global developmental delay, neuro-ophthalmological abnormalities, seizures, intellectual disability syndrome
  • HIVEP2-related intellectual disability
  • Hypertrophic mitochondrial cardiomyopathy
  • Hypoplasia of optic nerve due to central nervous system malformation
  • Immature autonomic system
  • Male emopamil-binding protein disorder with neurological defect
  • Muscle eye brain disease
  • Muscle-eye-brain disease, congenital muscular dystrophy
  • Navajo neurohepatopathy
  • Neural tube defect
  • Neurofaciodigitorenal syndrome
  • NPHP3-related Meckel-like syndrome
  • Pili torti
  • Pili torti with developmental delay and neurological abnormality syndrome
  • SCALP syndrome
  • Sebaceous nevus
  • Vascular malformation of the nervous system

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Congenital anomaly NOS of nervous system
  • Congenital deformity NOS of nervous system
  • Congenital disease or lesion NOS of nervous system

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Abnormal, abnormality, abnormalities
      • development, developmental
        • central nervous system
    • Anomaly, anomalous(congenital) (unspecified type)
      • gyri
    • Anomaly, anomalous(congenital) (unspecified type)
      • meningeal bands or folds
    • Anomaly, anomalous(congenital) (unspecified type)
      • meninges
    • Anomaly, anomalous(congenital) (unspecified type)
      • nerve
    • Anomaly, anomalous(congenital) (unspecified type)
      • nervous system (central)
    • Deformity
      • meninges or membrane (congenital)
    • Deformity
      • nervous system (congenital)
    • Deformity
      • spinal
        • nerve root (congenital)
    • Disease, diseased
      • nervous system
        • congenital
    • Dysplasia
      • brain
    • Encephalopathy(acute)
      • congenital
    • Lesion(s) (nontraumatic)
      • nervous system, congenital
    • Maldevelopment
      • brain
    • Malformation(congenital)
      • dura
    • Malformation(congenital)
      • meninges or membrane (congenital)
    • Malformation(congenital)
      • nervous system (central)
    • Malformation(congenital)
      • sense organs NEC

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL004
Nervous system congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • ACD Gene Mutation|ACD, Shelterin Complex Subunit and Telomerase Recruitment Factor Gene Mutation|Adrenocortical Dysplasia Homolog (Mouse) Gene Mutation|PIP1 Gene Mutation|PTOP Gene Mutation|TINT1 Gene Mutation|TPP1 Gene Mutation

    a change in the nucleotide sequence of the acd gene.

  • ACD wt Allele|ACD, Mouse, Homolog of Gene|ACD, Shelterin Complex Subunit and Telomerase Recruitment Factor wt Allele|Adrenocortical Dysplasia Homolog (Mouse) Gene|PIP1|PTOP|TPP1

    human acd wild-type allele is located in the vicinity of 16q22.1 and is approximately 3 kb in length. this allele, which encodes adrenocortical dysplasia protein homolog, is involved in telomere protection.

  • Adrenocortical Dysplasia Protein Homolog|ACD|POT1 and TIN2 Organizing Protein|POT1 and TIN2-Interacting Protein|POT1- and TIN2- Organizing Protein|POT1-Interacting Protein 1|TIN2 Interacting Protein 1|TIN2-Interacting Protein 1|Telomere Protein TPP1

    adrenocortical dysplasia protein homolog (544 aa, ~58 kda) is encoded by the human acd gene. this protein plays a role in both the elongation and maintenance of telomeres.

  • Complex Cortical Dysplasia with other Brain Malformations 5|CDCBM5|TUBB2A Tubulinopathy

    an autosomal dominant condition caused by mutation(s) in the tubb2a gene, encoding tubulin beta-2a chain. it is characterized by cortical dysplasia and is associated with impaired intellectual development, hypotonia, global developmental delay, cortical dysplasia, and dysmorphic corpus callosum.

  • Cortical Dysplasia

    malformation of the cerebral cortex due to improper migration of neurons in utero.

  • Cortical Dysplasia-Focal Epilepsy Syndrome|CDFE Syndrome

    an autosomal recessive condition caused by mutation(s) in the cntnap2 gene, encoding contactin-associated protein-like 2. it is characterized by normal development until the onset of intractable focal seizures at age 1-9. after the onset of seizures, language regression, intellectual disability, hyperactivity, and impulsive behaviors begin to occur. the majority of children eventually fulfill the criteria for autism spectrum disorder.

  • Coenzyme Q10 Deficiency

    a genetically heterogeneous condition, typically inherited in an autosomal recessive fashion, characterized by coenzyme q10 deficiency.

  • Congenital Hepatic Fibrosis

    a congenital disorder usually inherited in an autosomal recessive pattern. it affects the hepatobiliary system and the kidneys. it is characterized by liver fibrosis, portal hypertension, and renal cysts.

  • Focal Cortical Dysplasia Type 1|FCD1|FCDI|Focal Cortical Dysplasia Type I

    focal cortical dysplasia characterized by abnormal cortical layering. it is associated with mild symptoms, late onset, and changes present in the temporal lobe. it includes the following: type ia with abnormal radial migration and maturation of neurons; type ib with disruption of the six-layered tangential composition of the cortex with immature neurons; and type ic comprising both architectural abnormalities.

  • Focal Cortical Dysplasia Type 2|FCD2|FCDII|Focal Cortical Dysplasia Type II

    focal cortical dysplasia characterized by disrupted cortical lamination and specific cytological abnormalities. it includes type iia with dysmorphic neurons and type iib with dysmorphic neurons and balloon cells.

  • Focal Cortical Dysplasia Type 3|FCD3|FCDIII|Focal Cortical Dysplasia Type III

    focal cortical dysplasia characterized by different cortical dyslamination and cytological abnormalities with the main lesions located in the same area. it includes the following: type iiia with architectural distortion of cortical layer in temporal lobe with hippocampal atrophy; type iiib with architectural distortion of cortical layer adjacent to glial or glioneuronal tumor; type iiic with architectural distortion of cortical layer adjacent to vascular malformation; and type iiid with architectural distortion of cortical layer adjacent to other lesions acquired in early childhood (e.g., trauma, ischemic event, and encephalitis).

  • Focal Cortical Dysplasia|FCD

    a congenital cortical developmental abnormality characterized by focal architectural distortion of the cortical brain layers. it is associated with the presence of cytologic abnormalities including hypertrophic and dysmorphic neurons. it is caused by genetic or acquired factors and is often associated with epilepsy.

Patient EducationClinical

Brain Malformations

Most brain malformations begin long before a baby is born. Something damages the developing nervous system or causes it to develop abnormally. Sometimes it's a genetic problem. In other cases, exposure to certain medicines, infections, or radiation during pregnancy interferes with brain development.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q07.9 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
742.9 Nervous system anom NOS
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q07.9Overview

Is Q07.9 (Other congenital malformations of nervous system) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital malformation of nervous system, unspecified on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Is Q07.9 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital malformation of nervous system, unspecified on inpatient claims.

What is the ICD-9 equivalent of Q07.9?

Under the General Equivalence Mappings, congenital malformation of nervous system, unspecified converts to ICD-9-CM 742.9 (nervous system anom NOS). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.