Other congenital malformations of nervous system (Q07) ICD-10-CM
The Q07 code range covers other congenital malformations of nervous system with 8 ICD-10-CM diagnosis codes. 6 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
Codes in the Q07 Range 8 codes · 6 billable
- Q07 Other congenital malformations of nervous systemNon-billable
- Q07.0 Arnold-Chiari syndromeNon-billable
- Q07.00 Arnold-Chiari syndrome without spina bifida or hydrocephalus
- Q07.01 Arnold-Chiari syndrome with spina bifida
- Q07.02 Arnold-Chiari syndrome with hydrocephalus
- Q07.03 Arnold-Chiari syndrome with spina bifida and hydrocephalus
- Q07.8 Other specified congenital malformations of nervous system
- Q07.9 Congenital malformation of nervous system, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q07 range.
Arnold-Chiari Malformation
A group of congenital malformations involving the brainstem, cerebellum, upper spinal cord, and surrounding bony structures. Type II is the most common, and features compression of the medulla and cerebellar tonsils into the upper cervical spinal canal and an associated MENINGOMYELOCELE. Type I features similar, but less severe malformations and is without an associated meningomyelocele. Type III has the features of type II with an additional herniation of the entire cerebellum through the bony defect involving the foramen magnum, forming an ENCEPHALOCELE. Type IV is a form a cerebellar hypoplasia. Clinical manifestations of types I-III include TORTICOLLIS; opisthotonus; HEADACHE; VERTIGO; VOCAL CORD PARALYSIS; APNEA; NYSTAGMUS, CONGENITAL; swallowing difficulties; and ATAXIA. (From Menkes, Textbook of Child Neurology, 5th ed, p261; Davis, Textbook of Neuropathology, 2nd ed, pp236-46)
About the Q07 Code Range
These are malformations of the nervous system present at birth. The category includes Arnold-Chiari syndrome and other congenital nervous system malformations.
Q07.0 identifies Arnold-Chiari syndrome. Its subdivisions distinguish whether spina bifida, hydrocephalus, both, or neither is present. Q07.8 identifies other specified malformations, while Q07.9 identifies an unspecified malformation.
Questions About This Page
How many billable codes are in the Q07 range?
Of the 8 codes in this range, 6 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the Q07 range classify?
The range classifies other congenital malformations of nervous system. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
