Other congenital malformations of nervous system (Q07)
The ICD-10 code Q07 series categorizes various other congenital malformations of the nervous system, including detailed subcodes for specific conditions like Arnold-Chiari syndrome and a range of other nervous system congenital anomalies. These codes assist healthcare providers in precisely identifying and coding complex congenital neurological disorders.
The code Q07.0 covers Arnold-Chiari syndrome and its variants, such as Chiari malformation type II (Q07.00 without spina bifida or hydrocephalus), and forms combined with spina bifida (Q07.01), hydrocephalus (Q07.02), or both (Q07.03). This distinction is crucial for documenting the presence or absence of related complications. The broader code Q07.8 includes various other specified congenital nervous system malformations, covering numerous rare conditions like agenesis of nerves, congenital hypomyelinating neuropathy, and congenital malformations of optic or cochlear nerves. Meanwhile, Q07.9 captures unspecified congenital nervous system anomalies and encompasses syndromes with complex neurological and systemic features, such as muscle-eye-brain disease and cortical dysplasia. Using the specific ICD-10 code for each condition ensures clear communication and accurate medical record documentation for congenital nervous system disorders.
Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
Congenital malformations of the nervous system (Q00-Q07)
Q07 Other congenital malformations of nervous system
Q07.0 Arnold-Chiari syndrome
- Q07.00 Arnold-Chiari syndrome without spina bifida or hydrocephalus
- Q07.01 Arnold-Chiari syndrome with spina bifida
- Q07.02 Arnold-Chiari syndrome with hydrocephalus
- Q07.03 Arnold-Chiari syndrome with spina bifida and hydrocephalus
- Q07.8 Other specified congenital malformations of nervous system
- Q07.9 Congenital malformation of nervous system, unspecified
Other congenital malformations of nervous system (Q07)
Instructional Notations
Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
- congenital central alveolar hypoventilation syndrome G47.35
- familial dysautonomia [Riley-Day] G90.1
- neurofibromatosis nonmalignant Q85.0
Clinical Terms
The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.
Hydranencephaly
A congenital condition where the greater portions of the cerebral hemispheres and CORPUS STRIATUM are replaced by CSF and glial tissue. The meninges and the skull are well formed, which is consistent with earlier normal embryogenesis of the telencephalon. Bilateral occlusions of the internal carotid arteries in utero is a potential mechanism. Clinical features include intact brainstem reflexes without evidence of higher cortical activity. (Menkes, Textbook of Child Neurology, 5th ed, p307)
