Other congenital malformations of nervous system (Q07)

• ICD-10 Index

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)

    • Congenital malformations of the nervous system (Q00-Q07)

      • Other congenital malformations of nervous system (Q07)

        • Q07 - Other congenital malformations of nervous system NON-BILLABLE CODE
        • Q07.0 - Arnold-Chiari syndrome NON-BILLABLE CODE
        • Q07.00 - Arnold-Chiari syndrome without spina bifida or hydrocephalus BILLABLE CODE
        • Q07.01 - Arnold-Chiari syndrome with spina bifida BILLABLE CODE
        • Q07.02 - Arnold-Chiari syndrome with hydrocephalus BILLABLE CODE
        • Q07.03 - Arnold-Chiari syndrome with spina bifida and hydrocephalus BILLABLE CODE
        • Q07.8 - Other specified congenital malformations of nervous system BILLABLE CODE
        • Q07.9 - Congenital malformation of nervous system, unspecified BILLABLE CODE

Clinical Information for Other congenital malformations of nervous system (Q07)

Hydranencephaly - A congenital condition where the greater portions of the cerebral hemispheres and CORPUS STRIATUM are replaced by CSF and glial tissue. The meninges and the skull are well formed, which is consistent with earlier normal embryogenesis of the telencephalon. Bilateral occlusions of the internal carotid arteries in utero is a potential mechanism. Clinical features include intact brainstem reflexes without evidence of higher cortical activity. (Menkes, Textbook of Child Neurology, 5th ed, p307)

Instructional Notations

Type 2 Excludes Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.

• congenital central alveolar hypoventilation syndrome G47.35
• familial dysautonomia [Riley-Day] G90.1
• neurofibromatosis nonmalignant Q85.0