Other congenital malformations of nervous system (Q07) ICD-10-CM
The Q07 code range covers other congenital malformations of nervous system with 8 ICD-10-CM diagnosis codes. 6 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
Codes in the Q07 Range 8 codes · 6 billable
- Q07 Other congenital malformations of nervous systemNon-billable
- Q07.0 Arnold-Chiari syndromeNon-billable
- Q07.00 Arnold-Chiari syndrome without spina bifida or hydrocephalus
- Q07.01 Arnold-Chiari syndrome with spina bifida
- Q07.02 Arnold-Chiari syndrome with hydrocephalus
- Q07.03 Arnold-Chiari syndrome with spina bifida and hydrocephalus
- Q07.8 Other specified congenital malformations of nervous system
- Q07.9 Congenital malformation of nervous system, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q07 range.
Hydranencephaly
A congenital condition where the greater portions of the cerebral hemispheres and CORPUS STRIATUM are replaced by CSF and glial tissue. The meninges and the skull are well formed, which is consistent with earlier normal embryogenesis of the telencephalon. Bilateral occlusions of the internal carotid arteries in utero is a potential mechanism. Clinical features include intact brainstem reflexes without evidence of higher cortical activity. (Menkes, Textbook of Child Neurology, 5th ed, p307)
About the Q07 Code Range
The ICD-10 code Q07 series categorizes various other congenital malformations of the nervous system, including detailed subcodes for specific conditions like Arnold-Chiari syndrome and a range of other nervous system congenital anomalies. These codes assist healthcare providers in precisely identifying and coding complex congenital neurological disorders.
The code Q07.0 covers Arnold-Chiari syndrome and its variants, such as Chiari malformation type II (Q07.00 without spina bifida or hydrocephalus), and forms combined with spina bifida (Q07.01), hydrocephalus (Q07.02), or both (Q07.03). This distinction is crucial for documenting the presence or absence of related complications. The broader code Q07.8 includes various other specified congenital nervous system malformations, covering numerous rare conditions like agenesis of nerves, congenital hypomyelinating neuropathy, and congenital malformations of optic or cochlear nerves. Meanwhile, Q07.9 captures unspecified congenital nervous system anomalies and encompasses syndromes with complex neurological and systemic features, such as muscle-eye-brain disease and cortical dysplasia. Using the specific ICD-10 code for each condition ensures clear communication and accurate medical record documentation for congenital nervous system disorders.
Questions About This Page
How many billable codes are in the Q07 range?
Of the 8 codes in this range, 6 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the Q07 range classify?
The range classifies other congenital malformations of nervous system. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
