Other congenital malformations of spinal cord (Q06)

The ICD-10 codes Q06.0 to Q06.9 cover a range of congenital malformations of the spinal cord, including specific conditions like amyelia and diastematomyelia. These codes are used to classify rare spinal cord abnormalities present from birth that affect the development and structure of the spinal cord and related tissues.

The ICD-10 code for amyelia (Q06.0) specifically identifies the complete absence of the spinal cord. Hypoplasia and dysplasia of the spinal cord (Q06.1), also known as spinal cord hypoplasia or myelodysplasia, refer to underdeveloped or malformed spinal cord tissue. Diastematomyelia (Q06.2), a split spinal cord malformation, may be recognized by terms such as split cord malformation or faun tail syndrome, indicating a division or cleft in the spinal cord. Additional codes cover other congenital abnormalities of the cauda equina (Q06.3), hydromyelia (Q06.4), and a spectrum of other specified spinal cord malformations (Q06.8), which include diverse malformations like spinal dermal sinuses and tethered cord syndrome. For cases where a specific diagnosis is not clear, Q06.9 is used for unspecified congenital spinal cord malformations, sometimes described as anomalies of spinal meninges or other related structures. These ICD-10 codes help medical coders classify and document congenital spinal cord defects accurately for clinical and insurance purposes.