ICD-10-CM Code Q07.0

Arnold-Chiari syndrome

Version 2020 Non-Billable Code

Not Valid for Submission

Q07.0 is a "header" nonspecific and non-billable code code, consider using a code with a higher level of specificity for a diagnosis of arnold-chiari syndrome. The code is NOT valid for the year 2020 for the submission of HIPAA-covered transactions.

ICD-10:Q07.0
Short Description:Arnold-Chiari syndrome
Long Description:Arnold-Chiari syndrome

Consider the following ICD-10 codes with a higher level of specificity:

  • Q07.00 - Arnold-Chiari syndrome without spina bifida or hydrocephalus
  • Q07.01 - Arnold-Chiari syndrome with spina bifida
  • Q07.02 - Arnold-Chiari syndrome with hydrocephalus
  • Q07.03 - Arnold-Chiari syndrome with spina bifida and hydrocephalus

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code Q07.0:

Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Arnold-Chiari syndrome, type II

Type 1 Excludes

Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • Arnold-Chiari syndrome, type III Q01
  • Arnold-Chiari syndrome, type IV Q04.8

Clinical Information

  • ARNOLD CHIARI MALFORMATION-. a group of congenital malformations involving the brainstem cerebellum upper spinal cord and surrounding bony structures. type ii is the most common and features compression of the medulla and cerebellar tonsils into the upper cervical spinal canal and an associated meningomyelocele. type i features similar but less severe malformations and is without an associated meningomyelocele. type iii has the features of type ii with an additional herniation of the entire cerebellum through the bony defect involving the foramen magnum forming an encephalocele. type iv is a form a cerebellar hypoplasia. clinical manifestations of types i iii include torticollis; opisthotonus; headache; vertigo; vocal cord paralysis; apnea; nystagmus congenital; swallowing difficulties; and ataxia. from menkes textbook of child neurology 5th ed p261; davis textbook of neuropathology 2nd ed pp236 46

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Congenital malformations of the nervous system (Q00-Q07)
      • Other congenital malformations of nervous system (Q07)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Patients


Chiari Malformation

Chiari malformations (CMs) are structural defects in the cerebellum. The cerebellum is the part of the brain that controls balance. With CM, brain tissue extends into the spinal canal. It can happen when part of the skull is too small, which pushes the brain tissue down. There are several types of CM. One type often happens in children who have neural tube defects. Some types cause no symptoms and don't need treatment. If you have symptoms, they may include

  • Neck pain
  • Balance problems
  • Numbness or other abnormal feelings in the arms or legs
  • Dizziness
  • Vision problems
  • Difficulty swallowing
  • Poor hand coordination

Doctors diagnose CM using imaging tests. Medicines may ease some symptoms, such as pain. Surgery is the only treatment available to correct or stop the progression of nerve damage.

NIH: National Institute of Neurological Disorders and Stroke


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