2026 ICD-10-CM Diagnosis Code G90.BLMNB1-related autosomal dominant leukodystrophy

ICD-10-CM Codes›G00–G99›G89-G99›G90

ICD-10-CM G90.B
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

G90.B is a billable ICD-10-CM diagnosis code for LMNB1-related autosomal dominant leukodystrophy. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other nervous system disorders (often hereditary or degenerative).

Code Identity

ICD-10-CM Code
G90.B
Billable Status
Yes — Valid for Submission
Code Describes
LMNB1-related autosomal dominant leukodystrophy
Short Description
LMNB1-related autosomal dominant leukodystrophy
Same as the full description in the CMS dataset.
Parent Code
G90
Disorders of autonomic nervous system

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG89-G99Other disorders of the nervous system
CategoryG90Disorders of autonomic nervous system
This CodeG90.BLMNB1-related autosomal dominant leukodystrophy

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Leukodystrophy
      • LMNB1-related autosomal dominant

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS006
Other nervous system disorders (often hereditary or degenerative)
Default principal diagnosis: inpatient Yes · outpatient Yes

Code History & ChangesHistory

Replacement G90.B replaces the following previously assigned code(s):

  • G90.8 - Other disorders of autonomic nervous system
FY 2024AddedAdded to the ICD-10-CM code setEffective October 1, 2023.
FY 2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About G90.BOverview

Is G90.B (Disorders of autonomic nervous system) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report LMNB1-related autosomal dominant leukodystrophy on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.