2026 ICD-10-CM Diagnosis Code G71.11Myotonic muscular dystrophy

ICD-10-CM Codes›G00–G99›G70-G73›G71

ICD-10-CM G71.11
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

G71.11 is a billable ICD-10-CM diagnosis code for myotonic muscular dystrophy. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Myopathies.

Code Identity

ICD-10-CM Code
G71.11
Billable Status
Yes — Valid for Submission
Code Describes
Myotonic muscular dystrophy
Short Description
Myotonic muscular dystrophy
Same as the full description in the CMS dataset.
Parent Code
G71.1
Myotonic disorders

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG70-G73Diseases of myoneural junction and muscle
CategoryG71Primary disorders of muscles
This CodeG71.11Myotonic muscular dystrophy

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Adult-onset Steinert myotonic dystrophy
  • Cardiomyopathy in myotonic dystrophy
  • Childhood-onset Steinert myotonic dystrophy
  • Congenital myotonic dystrophy
  • Dilated cardiomyopathy due to muscular dystrophy
  • Dilated cardiomyopathy due to myotonic dystrophy
  • Dystrophia myotonica facies
  • Juvenile-onset Steinert myotonic dystrophy
  • Late-onset Steinert myotonic dystrophy
  • Myotonic dystrophy
  • Proximal myotonic myopathy
  • Steinert myotonic dystrophy syndrome

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Dystrophia myotonica Steinert
  • Myotonia atrophica
  • Myotonic dystrophy
  • Proximal myotonic myopathy (PROMM)
  • Steinert disease

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Atrophy, atrophic(of)
      • muscle, muscular (diffuse) (general) (idiopathic) (primary)
        • myotonic
    • Atrophy, atrophic(of)
      • myotonia
    • Batten-Steinert syndrome
    • Cardiomyopathy(familial) (idiopathic)
      • due to
        • myotonia atrophica
    • Curschmann(-Batten) (-Steinert) disease or syndrome
    • Disease, diseased
      • Batten-Steinert
    • Disease, diseased
      • Curschmann
    • Disease, diseased
      • Steinert's
    • Dystrophy, dystrophia
      • muscular
        • congenital (hereditary) (progressive) (with specific morphological abnormalities of the muscle fiber)
          • myotonic
    • Dystrophy, dystrophia
      • muscular
        • myotonic
    • Dystrophy, dystrophia
      • myotonic, myotonica
    • Myocardiopathy(congestive) (constrictive) (familial) (hypertrophic nonobstructive) (idiopathic) (infiltrative) (obstructive) (primary) (restrictive) (sporadic)
      • in (due to)
        • myotonia atrophica
    • Myopathy
      • mytonic, proximal (PROMM)
    • Myopathy
      • proximal myotonic (PROMM)
    • Myotonia(acquisita) (intermittens)
      • atrophica
    • Myotonia(acquisita) (intermittens)
      • dystrophica
    • Steinert's disease
    • Syndrome
      • Batten-Steinert
    • Syndrome
      • Curschmann (-Batten) (-Steinert)

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS018
Myopathies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Myotonic Dystrophy

    neuromuscular disorder characterized by progressive muscular atrophy; myotonia, and various multisystem atrophies. mild intellectual disability may also occur. abnormal trinucleotide repeat expansion in the 3' untranslated regions of dmpk protein gene is associated with myotonic dystrophy 1. dna repeat expansion of zinc finger protein-9 gene intron is associated with myotonic dystrophy 2.

  • Myotonin-Protein Kinase

    serine/threonine protein kinase responsible for various skeletal muscle functions; heart conduction system activity; calcium homeostasis; calcium uptake by sarcoplasmic reticulum and synaptic plasticity. it is encoded by the dmpk gene and its abnormal expanded trinucleotide repeat of ctg in the 3'-utr is associated with myotonic dystrophy 1.

  • Congenital Myotonic Dystrophy

    myotonic dystrophy that is present at birth.

Patient EducationClinical

Muscular Dystrophy

Muscular dystrophy (MD) is a group of more than 30 genetic diseases. They cause weakness of the muscles. Over time, the weakness gets worse and can cause trouble walking and doing daily activities. Some types of MD can also affect other organs.

The full article covers:

  • What is muscular dystrophy (MD)?
  • What are the types of muscular dystrophy (MD)?
  • What causes muscular dystrophy (MD)?
  • How is muscular dystrophy (MD) diagnosed?
  • What are the treatments for muscular dystrophy (MD)?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert G71.11 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
359.21 Myotonic musclr dystrphy
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About G71.11Overview

Is G71.11 (Myotonic disorders) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report myotonic muscular dystrophy on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What is the ICD-9 equivalent of G71.11?

Under the General Equivalence Mappings, myotonic muscular dystrophy converts to ICD-9-CM 359.21 (myotonic musclr dystrphy). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.