2027 ICD-10-CM Diagnosis Code G71.11Myotonic muscular dystrophy
ICD-10-CM Codes›G00–G99›G70-G73›G71
- Billable — Valid for Submission
- Risk Adjusts — HCC 197
- Chronic Condition
G71.11 is a billable ICD-10-CM diagnosis code for myotonic muscular dystrophy. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 91 through 93. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Myopathies.
For Medicare Advantage risk adjustment, G71.11 maps to CMS-HCC Category 197 (Muscular Dystrophy) under the V28 model, adding a risk factor of about 0.426 for a community, non-dual, aged beneficiary in payment year 2027.
Code Identity
Code Classification
Medicare Risk Adjustment (HCC)Billing
G71.11 maps to a payment category in the CMS-HCC model used to risk-adjust Medicare Advantage payments. Weights are the published community factors for payment year 2027.
Source: CMS Payment Year 2027 risk adjustment mappings and model software. Weights are relative factors, not dollar amounts; a beneficiary's total RAF also includes demographics and interactions. Browse all CMS-HCC categories.
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Adult-onset Steinert myotonic dystrophy
- Cardiomyopathy in myotonic dystrophy
- Childhood-onset Steinert myotonic dystrophy
- Congenital myotonic dystrophy
- Dilated cardiomyopathy due to muscular dystrophy
- Dilated cardiomyopathy due to myotonic dystrophy
- Dystrophia myotonica facies
- Juvenile-onset Steinert myotonic dystrophy
- Late-onset Steinert myotonic dystrophy
- Myotonic dystrophy
- Proximal myotonic myopathy
- Steinert myotonic dystrophy syndrome
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to G71.11: its own notes plus those printed at G71 and Chapter 6. A note printed at a category, block or chapter applies to every code under it.
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- Dystrophia myotonica [Steinert]
- Myotonia atrophica
- Myotonic dystrophy
- Proximal myotonic myopathy (PROMM)
- Steinert disease
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name G71.11, its category, or a range that includes it.
Excludes1 1
These codes carry an Excludes1 note naming G71.11: they are not reported together with it, unless the two conditions are unrelated.
- E31 Polyglandular dysfunctiondystrophia myotonica [Steinert] (G71.11)
Excludes2 1
These codes carry an Excludes2 note naming G71.11: its condition is not part of those codes, and both may be reported when the patient has both.
- Block M60-M63 Disorders of muscles
Code First 2
These codes say to code first a condition named in the note, and G71.11 is one of the conditions named.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Batten-Steinert syndrome G71.11
Disease, diseased See Also: Syndrome;
Batten-Steinert G71.11
Curschmann G71.11
Steinert's G71.11
Myocardiopathy (congestive) (constrictive) (familial) (hypertrophic nonobstructive) (idiopathic) (infiltrative) (obstructive) (primary) (restrictive) (sporadic) See Also: Cardiomyopathy; I42.9
myotonia atrophica G71.11
mytonic, proximal (PROMM) G71.11
proximal myotonic (PROMM) G71.11
Myotonia (acquisita) (intermittens) M62.89
atrophica G71.11
dystrophica G71.11
Steinert's disease G71.11
Syndrome See Also: Disease;
Batten-Steinert G71.11
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Myotonic Dystrophy
neuromuscular disorder characterized by progressive muscular atrophy; myotonia, and various multisystem atrophies. mild intellectual disability may also occur. abnormal trinucleotide repeat expansion in the 3' untranslated regions of dmpk protein gene is associated with myotonic dystrophy 1. dna repeat expansion of zinc finger protein-9 gene intron is associated with myotonic dystrophy 2.
Patient EducationClinical
Muscular Dystrophy
Muscular dystrophy (MD) is a group of more than 30 genetic diseases. They cause weakness of the muscles. Over time, the weakness gets worse and can cause trouble walking and doing daily activities. Some types of MD can also affect other organs.
The full article covers:
- What is muscular dystrophy (MD)?
- What are the types of muscular dystrophy (MD)?
- What causes muscular dystrophy (MD)?
- How is muscular dystrophy (MD) diagnosed?
- What are the treatments for muscular dystrophy (MD)?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert G71.11 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About G71.11Overview
What is the ICD-10 code for myotonic muscular dystrophy?
The ICD-10-CM code for myotonic muscular dystrophy is G71.11 (sometimes written as G7111). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is G71.11 (Myotonic disorders) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report myotonic muscular dystrophy on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does G71.11 group to?
When myotonic muscular dystrophy is the principal diagnosis on an inpatient stay, it groups to MS-DRG 91, 92, 93, with relative weights from 0.7783 to 1.7050 depending on complications. Higher weights mean higher Medicare reimbursement.
What is the ICD-9 equivalent of G71.11?
Under the General Equivalence Mappings, myotonic muscular dystrophy converts to ICD-9-CM 359.21 (myotonic musclr dystrphy). The mapping is a direct match.
What HCC is G71.11?
G71.11 (myotonic muscular dystrophy) maps to CMS-HCC Category 197 (Muscular Dystrophy), commonly written as HCC 197, in the CMS-HCC V28 model used for Medicare Advantage risk adjustment in payment year 2027. It mapped to HCC 76 under the retired V24 model. It also maps in the PACE (CMS-HCC V22), ESRD (V21), and ESRD (V24) models. It does not map to any RxHCC in the Part D prescription drug model.
Does G71.11 risk-adjust for Medicare Advantage payment?
Yes. When documented and reported on a Medicare Advantage encounter, G71.11 adds a risk adjustment factor of about 0.426 to the beneficiary's RAF score for a community, non-dual, aged enrollee (published V28 weights range from 0.145 to 0.681 depending on the payment segment). HCC 197 sits at the top of its hierarchy, so no other condition category supersedes it. See the full factor table on the HCC 197 category page.
