ICD-10 Code G71.09

Other specified muscular dystrophies

Version 2019 Billable Code

Valid for Submission

G71.09 is a billable code used to specify a medical diagnosis of other specified muscular dystrophies. The code is valid for the year 2020 for the submission of HIPAA-covered transactions.

ICD-10: G71.09
Short Description:Other specified muscular dystrophies
Long Description:Other specified muscular dystrophies

Code Classification

  • Diseases of the nervous system (G00–G99)
    • Diseases of myoneural junction and muscle (G70-G73)
      • Primary disorders of muscles (G71)

Code History

  • FY 2019 - Code Added, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Medical Professionals

Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Adult onset autosomal recessive muscular dystrophy with normal dystrophin
  • Adult-onset distal myopathy due to valosin containing protein mutation
  • Autosomal dominant limb girdle muscular dystrophy type 1A
  • Autosomal dominant limb girdle muscular dystrophy type 1B
  • Autosomal dominant limb girdle muscular dystrophy type 1C
  • Autosomal dominant limb girdle muscular dystrophy type 1D
  • Autosomal dominant limb girdle muscular dystrophy type 1E
  • Autosomal dominant limb girdle muscular dystrophy type 1F
  • Autosomal dominant limb girdle muscular dystrophy type 1G
  • Autosomal dominant limb-girdle muscular dystrophy type 1H
  • Autosomal dominant muscular dystrophy not predominantly limb girdle
  • Autosomal dominant muscular dystrophy with gene located at 5q31
  • Autosomal dominant muscular dystrophy with limb girdle distribution
  • Autosomal recessive limb girdle muscular dystrophy type 2A
  • Autosomal recessive limb girdle muscular dystrophy type 2B
  • Autosomal recessive limb girdle muscular dystrophy type 2C
  • Autosomal recessive limb girdle muscular dystrophy type 2D
  • Autosomal recessive limb girdle muscular dystrophy type 2E
  • Autosomal recessive limb girdle muscular dystrophy type 2F
  • Autosomal recessive limb girdle muscular dystrophy type 2G
  • Autosomal recessive limb girdle muscular dystrophy type 2I
  • Autosomal recessive limb girdle muscular dystrophy type 2J
  • Autosomal recessive limb girdle muscular dystrophy type 2K
  • Autosomal recessive limb girdle muscular dystrophy type 2L
  • Autosomal recessive limb girdle muscular dystrophy type 2M
  • Autosomal recessive limb girdle muscular dystrophy type 2N
  • Autosomal recessive limb girdle muscular dystrophy type 2O
  • Autosomal recessive limb girdle muscular dystrophy type 2P
  • Autosomal recessive limb girdle muscular dystrophy type 2Q
  • Autosomal recessive limb girdle muscular dystrophy type 2R
  • Autosomal recessive limb girdle muscular dystrophy type 2S
  • Autosomal recessive limb girdle muscular dystrophy type 2T
  • Autosomal recessive limb girdle muscular dystrophy type 2Y
  • Autosomal recessive muscular dystrophy not predominantly limb girdle
  • Autosomal recessive muscular dystrophy with abnormal dystrophin-associated glycoprotein
  • Autosomal recessive muscular dystrophy with gene located at 15q
  • Autosomal recessive muscular dystrophy with limb girdle distribution
  • Benign congenital muscular dystrophy with finger flexion contractures
  • Benign scapuloperoneal muscular dystrophy
  • Benign scapuloperoneal muscular dystrophy with cardiomyopathy
  • Caveolin 3 related distal myopathy
  • Combined malformation of central nervous system and skeletal muscle
  • Combined malformation of central nervous system and skeletal muscle
  • Congenital muscular dystrophy due to LMNA mutation
  • Congenital muscular dystrophy type 1B
  • Congenital muscular dystrophy with arthrogryposis multiplex congenita
  • Congenital muscular dystrophy with hyperlaxity
  • Congenital muscular dystrophy with infantile cataract and hypogonadism syndrome
  • Congenital muscular dystrophy with integrin alpha-7 deficiency
  • Distal muscular dystrophy with juvenile onset
  • Distal muscular dystrophy, Miyoshi type
  • Distal myopathy 2
  • Distal myopathy Welander type
  • Distal myopathy with posterior leg and anterior hand involvement
  • Early onset myopathy with fatal cardiomyopathy
  • Eichsfeld type congenital muscular dystrophy
  • Emery-Dreifuss muscular dystrophy
  • Enlargement of skeletal muscle
  • Finnish upper limb onset distal myopathy
  • Fukuyama congenital muscular dystrophy
  • Hereditary progressive muscular dystrophy
  • Hoffman syndrome
  • Hutterite type of muscular dystrophy
  • Infantile and/or juvenile cataract
  • Infantile cataract
  • Intermediate X-linked muscular dystrophy
  • Ji muscular dystrophy
  • KLHL9-related early-onset distal myopathy
  • Laing early-onset distal myopathy
  • Late onset proximal muscular dystrophy with dysarthria
  • Late-onset distal myopathy Markesbery Griggs type
  • Manifesting female carrier of X-linked muscular dystrophy
  • Menopausal muscular dystrophy syndrome
  • Merosin deficient congenital muscular dystrophy
  • Muscle-eye-brain disease, congenital muscular dystrophy
  • Muscular dystrophy Selcen type
  • Muscular dystrophy with predominantly proximal limb girdle distribution
  • Muscular dystrophy-deafmutism syndrome
  • Myofibrillar myopathy
  • Myofibrillar myopathy
  • Myopathy of extraocular muscles
  • Nonsenile cataract
  • Oculogastrointestinal muscular dystrophy
  • Oculopharyngeal muscular dystrophy
  • Oculopharyngodistal myopathy
  • Pharyngeal paresis
  • Pseudohypertrophy of muscle
  • Reunion-Indiana Amish type muscular dystrophy
  • Scapuloperoneal muscular dystrophy
  • Severe autosomal recessive muscular dystrophy of childhood - North African type
  • Severe childhood autosomal recessive muscular dystrophy
  • Severe scapuloperoneal muscular dystrophy with cardiomyopathy
  • Type 2 lissencephaly
  • Walker-Warburg congenital muscular dystrophy
  • Western type of congenital muscular dystrophy
  • X-linked limb girdle muscular dystrophy with normal dystrophin
  • X-linked muscular dystrophy not predominantly limb girdle
  • X-linked muscular dystrophy with abnormal dystrophin
  • X-linked muscular dystrophy with limb girdle distribution

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code G71.09 are found in the index:


Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references for the code G71.09 are found in the tabular index:

  • Inclusion Terms:
    • Benign scapuloperoneal muscular dystrophy WITH early contractures [Emery-Dreifuss]
    • Congenital muscular dystrophy NOS
    • Congenital muscular dystrophy WITH specific morphological abnormalities of the muscle fiber
    • Distal muscular dystrophy
    • Limb-girdle muscular dystrophy
    • Ocular muscular dystrophy
    • Oculopharyngeal muscular dystrophy
    • Scapuloperoneal muscular dystrophy

Replacement Code

G7109 replaces the following previously assigned ICD-10 code(s):

  • G71.0 - Muscular dystrophy

Information for Patients


Muscular Dystrophy

Muscular dystrophy (MD) is a group of more than 30 inherited diseases. They all cause muscle weakness and muscle loss. Some forms of MD appear in infancy or childhood. Others may not appear until middle age or later. The different types can vary in whom they affect, which muscles they affect, and what the symptoms are. All forms of MD grow worse as the person's muscles get weaker. Most people with MD eventually lose the ability to walk.

There is no cure for muscular dystrophy. Treatments can help with the symptoms and prevent complications. They include physical and speech therapy, orthopedic devices, surgery, and medications. Some people with MD have mild cases that worsen slowly. Others cases are disabling and severe.

NIH: National Institute of Neurological Disorders and Stroke


[Learn More]

ICD-10 Footnotes

General Equivalence Map Definitions
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

  • Approximate Flag - The approximate flag is on, indicating that the relationship between the code in the source system and the code in the target system is an approximate equivalent.
  • No Map Flag - The no map flag indicates that a code in the source system is not linked to any code in the target system.
  • Combination Flag - The combination flag indicates that more than one code in the target system is required to satisfy the full equivalent meaning of a code in the source system.

Index of Diseases and Injuries Definitions

  • And - The word "and" should be interpreted to mean either "and" or "or" when it appears in a title.
  • Code also note - A "code also" note instructs that two codes may be required to fully describe a condition, but this note does not provide sequencing direction.
  • Code first - Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists, there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation.
  • Type 1 Excludes Notes - A type 1 Excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • Type 2 Excludes Notes - A type 2 Excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
  • Includes Notes - This note appears immediately under a three character code title to further define, or give examples of, the content of the category.
  • Inclusion terms - List of terms is included under some codes. These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • NEC "Not elsewhere classifiable" - This abbreviation in the Alphabetic Index represents "other specified". When a specific code is not available for a condition, the Alphabetic Index directs the coder to the "other specified” code in the Tabular List.
  • NOS "Not otherwise specified" - This abbreviation is the equivalent of unspecified.
  • See - The "see" instruction following a main term in the Alphabetic Index indicates that another term should be referenced. It is necessary to go to the main term referenced with the "see" note to locate the correct code.
  • See Also - A "see also" instruction following a main term in the Alphabetic Index instructs that there is another main term that may also be referenced that may provide additional Alphabetic Index entries that may be useful. It is not necessary to follow the "see also" note when the original main term provides the necessary code.
  • 7th Characters - Certain ICD-10-CM categories have applicable 7th characters. The applicable 7th character is required for all codes within the category, or as the notes in the Tabular List instruct. The 7th character must always be the 7th character in the data field. If a code that requires a 7th character is not 6 characters, a placeholder X must be used to fill in the empty characters.
  • With - The word "with" should be interpreted to mean "associated with" or "due to" when it appears in a code title, the Alphabetic Index, or an instructional note in the Tabular List. The word "with" in the Alphabetic Index is sequenced immediately following the main term, not in alphabetical order.