ICD-10-CM Code G71.0

Muscular dystrophy

Version 2020 Replaced Code Non-Billable Code

Not Valid for Submission

G71.0 is a "header" nonspecific and non-billable code code, consider using a code with a higher level of specificity for a diagnosis of muscular dystrophy. The code is NOT valid for the year 2020 for the submission of HIPAA-covered transactions.

Short Description:Muscular dystrophy
Long Description:Muscular dystrophy

Consider the following ICD-10 codes with a higher level of specificity:

  • G71.00 - ... unspecified
  • G71.01 - Duchenne or Becker muscular dystrophy
  • G71.02 - Facioscapulohumeral muscular dystrophy
  • G71.09 - Other specified muscular dystrophies

Replaced Code

This code was replaced in the 2020 ICD-10 code set with the code(s) listed below. The National Center for Health Statistics (NCHS) has published an update to the ICD-10-CM diagnosis codes which became effective October 1, 2019. This code was replaced for the FY 2020 (October 1, 2019 - September 30, 2020).

  • G71.00 - Muscular dystrophy, unspecified
  • G71.01 - Duchenne or Becker muscular dystrophy
  • G71.02 - Facioscapulohumeral muscular dystrophy
  • G71.09 - Other specified muscular dystrophies

Clinical Information

  • MUSCULAR DYSTROPHIES-. a heterogeneous group of inherited myopathies characterized by wasting and weakness of the skeletal muscle. they are categorized by the sites of muscle weakness; age of onset; and inheritance patterns.
  • MUSCULAR DYSTROPHY ANIMAL-. muscular dystrophy that occurs in vertebrate animals.
  • OPHTHALMOPLEGIA CHRONIC PROGRESSIVE EXTERNAL-. a mitochondrial myopathy characterized by slowly progressive paralysis of the levator palpebrae orbicularis oculi and extraocular muscles. ragged red fibers and atrophy are found on muscle biopsy. familial and sporadic forms may occur. disease onset is usually in the first or second decade of life and the illness slowly progresses until usually all ocular motility is lost. from adams et al. principles of neurology 6th ed p1422
  • MUSCULAR DYSTROPHY DUCHENNE-. an x linked recessive muscle disease caused by an inability to synthesize dystrophin which is involved with maintaining the integrity of the sarcolemma. muscle fibers undergo a process that features degeneration and regeneration. clinical manifestations include proximal weakness in the first few years of life pseudohypertrophy cardiomyopathy see myocardial diseases and an increased incidence of impaired mentation. becker muscular dystrophy is a closely related condition featuring a later onset of disease usually adolescence and a slowly progressive course. adams et al. principles of neurology 6th ed p1415
  • MUSCULAR DYSTROPHY EMERY DREIFUSS-. a heterogenous group of inherited muscular dystrophy without the involvement of nervous system. the disease is characterized by muscular atrophy; muscle weakness; contracture of the elbows; achilles tendon; and posterior cervical muscles; with or without cardiac features. there are several inheritance patterns including x linked x chromosome autosomal dominant and autosomal recessive gene mutations.
  • MUSCULAR DYSTROPHY FACIOSCAPULOHUMERAL-. an autosomal dominant degenerative muscle disease characterized by slowly progressive weakness of the muscles of the face upper arm and shoulder girdle. the onset of symptoms usually occurs in the first or second decade of life. affected individuals usually present with impairment of upper extremity elevation. this tends to be followed by facial weakness primarily involving the orbicularis oris and orbicularis oculi muscles. neuromuscul disord 1997;71:55 62; adams et al. principles of neurology 6th ed p1420
  • MUSCULAR DYSTROPHY OCULOPHARYNGEAL-. an autosomal dominant hereditary disease that presents in late in life and is characterized by dysphagia and progressive ptosis of the eyelids. mutations in the gene for polya binding protein ii have been associated with oculopharyngeal muscular dystrophy.
  • MUSCULAR DYSTROPHIES LIMB GIRDLE-. a heterogenous group of inherited muscular dystrophy that can be autosomal dominant or autosomal recessive. there are many forms called lgmds involving genes encoding muscle membrane proteins such as the sarcoglycan sarcoglycans complex that interacts with dystrophin. the disease is characterized by progressing wasting and weakness of the proximal muscles of arms and legs around the hips and shoulders the pelvic and shoulder girdles.
  • DISTAL MYOPATHIES-. a heterogeneous group of genetic disorders characterized by progressive muscular atrophy and muscle weakness beginning in the hands the legs or the feet. most are adult onset autosomal dominant forms. others are autosomal recessive.
  • SARCOGLYCANOPATHIES-. deficiencies or mutations in the genes for the sarcoglycan complex subunits. a variety of phenotypes are associated with these mutations including a subgroup of autosomal recessive limb girdle muscular dystrophies cardiomyopathies and respiratory deficiency.
  • WALKER WARBURG SYNDROME-. rare autosomal recessive lissencephaly type 2 associated with congenital muscular dystrophy and eye anomalies e.g. retinal detachment; cataract; microphthalmos. it is often associated with additional brain malformations such as hydrocephaly and cerebellar hypoplasia and is the most severe form of the group of related syndromes alpha dystroglycanopathies with common congenital abnormalities in the brain eye and muscle development.

Convert G71.0 to ICD-9

  • 359.1 - Hered prog musc dystrphy

Code Classification

  • Diseases of the nervous system (G00–G99)
    • Diseases of myoneural junction and muscle (G70-G73)
      • Primary disorders of muscles (G71)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - Code Deleted, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Patients

Muscular Dystrophy

Muscular dystrophy (MD) is a group of more than 30 inherited diseases. They all cause muscle weakness and muscle loss. Some forms of MD appear in infancy or childhood. Others may not appear until middle age or later. The different types can vary in whom they affect, which muscles they affect, and what the symptoms are. All forms of MD grow worse as the person's muscles get weaker. Most people with MD eventually lose the ability to walk.

There is no cure for muscular dystrophy. Treatments can help with the symptoms and prevent complications. They include physical and speech therapy, orthopedic devices, surgery, and medications. Some people with MD have mild cases that worsen slowly. Others cases are disabling and severe.

NIH: National Institute of Neurological Disorders and Stroke

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Oculopharyngeal muscular dystrophy Oculopharyngeal muscular dystrophy is a genetic condition characterized by muscle weakness that begins in adulthood, typically after age 40. The term "oculopharyngeal" refers to the eyes (oculo-) and a part of the throat called the pharynx (-pharyngeal). Affected individuals usually first experience weakness of the muscles in both eyelids that causes droopy eyelids (ptosis). Ptosis can worsen over time, causing the eyelid to impair vision, and in some cases, limit eye movement. Along with ptosis, affected individuals develop weakness of the throat muscles that causes difficulty swallowing (dysphagia). Dysphagia begins with dry food, but over time, liquids can also become difficult to swallow. Dysphagia can cause saliva to accumulate and a wet-sounding voice. Many people with oculopharyngeal muscular dystrophy also have weakness and wasting (atrophy) of the tongue. These problems with food intake may cause malnutrition, choking, or a bacterial lung infection called aspiration pneumonia.Individuals with oculopharyngeal muscular dystrophy frequently have weakness in the muscles near the center of the body (proximal muscles), particularly muscles in the shoulders, upper legs, and hips (limb-girdle muscles). The weakness slowly gets worse, and people may need the aid of a cane or a walker. Rarely, affected individuals need wheelchair assistance.Rarely, individuals have a severe form of oculopharyngeal muscular dystrophy with muscle weakness that begins before age 45, and have trouble walking independently by age 60. These individuals often also have disturbances in nerve function (neuropathy), a gradual loss of intellectual functioning (cognitive decline), and psychiatric symptoms such as depression or strongly held false beliefs (delusions).
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