Primary disorders of muscles (G71) ICD-10-CM
The G71 code range covers primary disorders of muscles with 35 ICD-10-CM diagnosis codes. 28 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
Codes in the G71 Range 35 codes · 28 billable
- G71 Primary disorders of musclesNon-billable
- G71.0 Muscular dystrophyNon-billable
- G71.00 Muscular dystrophy, unspecified
- G71.01 Duchenne or Becker muscular dystrophy
- G71.02 Facioscapulohumeral muscular dystrophy
- G71.03 Limb girdle muscular dystrophiesNon-billable
- G71.031 Autosomal dominant limb girdle muscular dystrophy
- G71.032 Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction
- G71.033 Limb girdle muscular dystrophy due to dysferlin dysfunction
- G71.034 Limb girdle muscular dystrophy due to sarcoglycan dysfunctionNon-billable
- G71.0340 Limb girdle muscular dystrophy due to sarcoglycan dysfunction, unspecified
- G71.0341 Limb girdle muscular dystrophy due to alpha sarcoglycan dysfunction
- G71.0342 Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction
- G71.0349 Limb girdle muscular dystrophy due to other sarcoglycan dysfunction
- G71.035 Limb girdle muscular dystrophy due to anoctamin-5 dysfunction
- G71.036 Limb girdle muscular dystrophy due to fukutin related protein dysfunction New
- G71.038 Other limb girdle muscular dystrophy
- G71.039 Limb girdle muscular dystrophy, unspecified
- G71.09 Other specified muscular dystrophies
- G71.1 Myotonic disordersNon-billable
- G71.11 Myotonic muscular dystrophy
- G71.12 Myotonia congenita
- G71.13 Myotonic chondrodystrophy
- G71.14 Drug induced myotonia
- G71.19 Other specified myotonic disorders
- G71.2 Congenital myopathiesNon-billable
- G71.20 Congenital myopathy, unspecified
- G71.21 Nemaline myopathy
- G71.22 Centronuclear myopathyNon-billable
- G71.220 X-linked myotubular myopathy
- G71.228 Other centronuclear myopathy
- G71.29 Other congenital myopathy
- G71.3 Mitochondrial myopathy, not elsewhere classified
- G71.8 Other primary disorders of muscles
- G71.9 Primary disorder of muscle, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the G71 range.
Isaacs Syndrome
A rare neuromuscular disorder with onset usually in late childhood or early adulthood, characterized by intermittent or continuous widespread involuntary muscle contractions; FASCICULATION; hyporeflexia; MUSCLE CRAMP; MUSCLE WEAKNESS; HYPERHIDROSIS; TACHYCARDIA; and MYOKYMIA. Involvement of pharyngeal or laryngeal muscles may interfere with speech and breathing. The continuous motor activity persists during sleep and general anesthesia (distinguishing this condition from STIFF-PERSON SYNDROME). Familial and acquired (primarily autoimmune) forms have been reported. (From Ann NY Acad Sci 1998 May 13;841:482-496; Adams et al., Principles of Neurology, 6th ed, p1491)
Myotonia
Prolonged failure of muscle relaxation after contraction. This may occur after voluntary contractions, muscle percussion, or electrical stimulation of the muscle. Myotonia is a characteristic feature of MYOTONIC DISORDERS.
Myotonia Congenita
Inherited myotonic disorders with early childhood onset MYOTONIA. Muscular hypertrophy is common and myotonia may impair ambulation and other movements. It is classified as Thomsen (autosomal dominant) or Becker (autosomal recessive) generalized myotonia mainly based on the inheritance pattern. Becker type is also clinically more severe. An autosomal dominant variant with milder symptoms and later onset is known as myotonia levior. Mutations in the voltage-dependent skeletal muscle chloride channel are associated with the disorders.
Myotonic Disorders
Diseases characterized by MYOTONIA, which may be inherited or acquired. Myotonia may be restricted to certain muscles (e.g., intrinsic hand muscles) or occur as a generalized condition.
Myotonic Dystrophy
Neuromuscular disorder characterized by PROGRESSIVE MUSCULAR ATROPHY; MYOTONIA, and various multisystem atrophies. Mild INTELLECTUAL DISABILITY may also occur. Abnormal TRINUCLEOTIDE REPEAT EXPANSION in the 3' UNTRANSLATED REGIONS of DMPK PROTEIN gene is associated with Myotonic Dystrophy 1. DNA REPEAT EXPANSION of zinc finger protein-9 gene intron is associated with Myotonic Dystrophy 2.
Myotonin-Protein Kinase
Serine/threonine protein kinase responsible for various SKELETAL MUSCLE functions; HEART CONDUCTION SYSTEM activity; calcium HOMEOSTASIS; calcium uptake by SARCOPLASMIC RETICULUM and SYNAPTIC PLASTICITY. It is encoded by the DMPK gene and its abnormal EXPANDED TRINUCLEOTIDE REPEAT of CTG in the 3'-UTR is associated with MYOTONIC DYSTROPHY 1.
Osteochondrodysplasias
Abnormal development of cartilage and bone.
About the G71 Code Range
This section of ICD-10-CM, G71, covers primary disorders of muscles, specifically various types of muscular dystrophies, myotonic disorders, congenital myopathies, mitochondrial myopathies, and other primary muscle diseases. These codes help classify specific muscle conditions for accurate diagnosis and treatment.
The ICD-10 code for muscular dystrophy (G71.0) includes several subtypes such as G71.00 for unspecified muscular dystrophy and G71.01 for Duchenne or Becker muscular dystrophy, also known as X-linked muscular dystrophy with limb girdle distribution. Limb girdle muscular dystrophies have detailed codes from G71.03 through G71.039, clarifying autosomal dominant, autosomal recessive, and protein-specific dysfunctions. The code G71.1 classifies myotonic disorders, including G71.11 for myotonic muscular dystrophy (Steinert disease) and G71.12 for myotonia congenita. Congenital myopathies (G71.2) detail conditions like nemaline myopathy and centronuclear myopathy. Mitochondrial myopathies (G71.3) cover inherited mitochondrial muscle diseases. Other primary muscle disorders and unspecified conditions fall under G71.8 and G71.9. These codes assist healthcare professionals and coders in pinpointing particular muscle disease types, improving clinical accuracy and patient care.
Questions About This Page
How many billable codes are in the G71 range?
Of the 35 codes in this range, 28 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the G71 range classify?
The range classifies primary disorders of muscles. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
