2026 ICD-10-CM Diagnosis Code E83.09Other disorders of copper metabolism

ICD-10-CM Codes›E00–E89›E70-E88›E83

ICD-10-CM E83.09
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

E83.09 is a billable ICD-10-CM diagnosis code for other disorders of copper metabolism. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified nutritional and metabolic disorders.

Code Identity

ICD-10-CM Code
E83.09
Billable Status
Yes — Valid for Submission
Code Describes
Other disorders of copper metabolism
Short Description
Other disorders of copper metabolism
Same as the full description in the CMS dataset.
Parent Code
E83.0
Disorders of copper metabolism

Code Classification

ChapterE00–E89Endocrine, nutritional and metabolic diseases
SectionE70-E88Metabolic disorders
CategoryE83Disorders of mineral metabolism
This CodeE83.09Other disorders of copper metabolism

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Copper storage associated hepatitis
  • Cryptogenic cirrhosis
  • Disorder of copper metabolism
  • Disorder of liver due to disorder of mineral metabolism
  • Familial hypoceruloplasminemia
  • Hypercupruria
  • Idiopathic copper associated cirrhosis of liver
  • Menkes kinky-hair syndrome

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Menkes' (kinky hair) (steely hair) disease

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Disorder(of)
      • metabolism NOS
        • copper
          • specified type NEC
    • Menkes' disease or syndrome

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR END016
Other specified and unspecified nutritional and metabolic disorders
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Menkes Kinky Hair Syndrome

    an inherited disorder of copper metabolism transmitted as an x-linked trait and characterized by the infantile onset of hypothermia, feeding difficulties, hypotonia, seizures, bony deformities, pili torti (twisted hair), and severely impaired intellectual development. defective copper transport across plasma and endoplasmic reticulum membranes results in copper being unavailable for the synthesis of several copper containing enzymes, including protein-lysine 6-oxidase; ceruloplasmin; and superoxide dismutase. pathologic changes include defects in arterial elastin, neuronal loss, and gliosis. (from menkes, textbook of child neurology, 5th ed, p125)

  • Cryptogenic Cirrhosis

    cirrhosis in which no causative agent can be identified.

Patient EducationClinical

Metabolic Disorders

Metabolism is the process your body uses to get or make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system break the food parts down into sugars and acids, your body's fuel.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert E83.09 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
275.1 Dis copper metabolism
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About E83.09Overview

Is E83.09 (Disorders of copper metabolism) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other disorders of copper metabolism on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What is the ICD-9 equivalent of E83.09?

Under the General Equivalence Mappings, other disorders of copper metabolism converts to ICD-9-CM 275.1 (dis copper metabolism). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.