Valid for Submission
E80.5 is a billable diagnosis code used to specify a medical diagnosis of crigler-najjar syndrome. The code E80.5 is valid during the fiscal year 2021 from October 01, 2020 through September 30, 2021 for the submission of HIPAA-covered transactions.
The ICD-10-CM code E80.5 might also be used to specify conditions or terms like crigler-najjar syndrome, crigler-najjar syndrome, type i, crigler-najjar syndrome, type ii, inherited disorder of bilirubin metabolism or neonatal jaundice with crigler-najjar syndrome.
Index to Diseases and Injuries
The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code E80.5 are found in the index:
- - Crigler-Najjar disease or syndrome - E80.5
The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:
- Crigler-Najjar syndrome
- Crigler-Najjar syndrome, type I
- Crigler-Najjar syndrome, type II
- Inherited disorder of bilirubin metabolism
- Neonatal jaundice with Crigler-Najjar syndrome
- CRIGLER NAJJAR SYNDROME-. a familial form of congenital hyperbilirubinemia transmitted as an autosomal recessive trait. it is characterized by icterus and brain damage caused by a glucuronyl transferase deficiency in the liver and faulty bilirubin conjugation.
Diagnostic Related Groups - MS-DRG Mapping
Convert E80.5 to ICD-9 Code
The General Equivalency Mapping (GEM) crosswalk indicates an approximate mapping between the ICD-10 code E80.5 its ICD-9 equivalent. The approximate mapping means there is not an exact match between the ICD-10 code and the ICD-9 code and the mapped code is not a precise representation of the original code.
Information for Patients
Also called: Hepatic disease
Your liver is the largest organ inside your body. It helps your body digest food, store energy, and remove poisons.
There are many kinds of liver diseases:
- Diseases caused by viruses, such as hepatitis A, hepatitis B, and hepatitis C
- Diseases caused by drugs, poisons, or too much alcohol. Examples include fatty liver disease and cirrhosis.
- Liver cancer
- Inherited diseases, such as hemochromatosis and Wilson disease
Symptoms of liver disease can vary, but they often include swelling of the abdomen and legs, bruising easily, changes in the color of your stool and urine, and jaundice, or yellowing of the skin and eyes. Sometimes there are no symptoms. Tests such as imaging tests and liver function tests can check for liver damage and help to diagnose liver diseases.
- ALP isoenzyme test (Medical Encyclopedia)
- Ascites (Medical Encyclopedia)
- Diet - liver disease (Medical Encyclopedia)
- Hepatic encephalopathy (Medical Encyclopedia)
- Hepatomegaly (Medical Encyclopedia)
- Liver disease (Medical Encyclopedia)
- Liver scan (Medical Encyclopedia)
[Learn More in MedlinePlus]
Crigler-Najjar syndrome Crigler-Najjar syndrome is a severe condition characterized by high levels of a toxic substance called bilirubin in the blood (hyperbilirubinemia). Bilirubin is produced when red blood cells are broken down. This substance is removed from the body only after it undergoes a chemical reaction in the liver, which converts the toxic form of bilirubin (called unconjugated bilirubin) to a nontoxic form called conjugated bilirubin. People with Crigler-Najjar syndrome have a buildup of unconjugated bilirubin in their blood (unconjugated hyperbilirubinemia).Bilirubin has an orange-yellow tint, and hyperbilirubinemia causes yellowing of the skin and whites of the eyes (jaundice). In Crigler-Najjar syndrome, jaundice is apparent at birth or in infancy. Severe unconjugated hyperbilirubinemia can lead to a condition called kernicterus, which is a form of brain damage caused by the accumulation of unconjugated bilirubin in the brain and nerve tissues. Babies with kernicterus are often extremely tired (lethargic) and may have weak muscle tone (hypotonia). These babies may experience episodes of increased muscle tone (hypertonia) and arching of their backs. Kernicterus can lead to other neurological problems, including involuntary writhing movements of the body (choreoathetosis), hearing problems, or intellectual disability.Crigler-Najjar syndrome is divided into two types. Type 1 (CN1) is very severe, and affected individuals can die in childhood due to kernicterus, although with proper treatment, they may survive longer. Type 2 (CN2) is less severe. People with CN2 are less likely to develop kernicterus, and most affected individuals survive into adulthood.
[Learn More in MedlinePlus]