2026 ICD-10-CM Diagnosis Code E74.89Other specified disorders of carbohydrate metabolism

ICD-10-CM Codes›E00–E89›E70-E88›E74

ICD-10-CM E74.89
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

E74.89 is a billable ICD-10-CM diagnosis code for other specified disorders of carbohydrate metabolism. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified nutritional and metabolic disorders.

Code Identity

ICD-10-CM Code
E74.89
Billable Status
Yes — Valid for Submission
Code Describes
Other specified disorders of carbohydrate metabolism
Short Description
Other specified disorders of carbohydrate metabolism
Same as the full description in the CMS dataset.
Parent Code
E74.8
Other specified disorders of carbohydrate metabolism

Code Classification

ChapterE00–E89Endocrine, nutritional and metabolic diseases
SectionE70-E88Metabolic disorders
CategoryE74Other disorders of carbohydrate metabolism
This CodeE74.89Other specified disorders of carbohydrate metabolism

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • ALG1 congenital disorder of glycosylation
  • ALG12-congenital disorder of glycosylation
  • ALG3 congenital disorder of glycosylation
  • ALG8 congenital disorder of glycosylation
  • ALG9 congenital disorder of glycosylation
  • CCDC115 congenital disorder of glycosylation
  • COG1 congenital disorder of glycosylation
  • COG4 congenital disorder of glycosylation
  • COG5 congenital disorder of glycosylation
  • COG7 congenital disorder of glycosylation
  • COG8 congenital disorder of glycosylation
  • Congenital disorder of glycosylation type 1c
  • Congenital disorder of glycosylation type 1cc
  • Congenital disorder of glycosylation type 1e
  • Congenital disorder of glycosylation type 1f
  • Congenital disorder of glycosylation type 1i
  • Congenital disorder of glycosylation type 1j
  • Congenital disorder of glycosylation type 1n
  • Congenital disorder of glycosylation type 1p
  • Congenital disorder of glycosylation type 1q
  • Congenital disorder of glycosylation type 1r
  • Congenital disorder of glycosylation type 1s
  • Congenital disorder of glycosylation type 1w
  • Congenital disorder of glycosylation type 1x
  • Congenital disorder of glycosylation type 1y
  • Congenital myasthenic syndrome
  • Congenital myasthenic syndrome with glycosylation defect due to ALG14 UDP-N-acetylglucosaminyltransferase subunit gene mutation
  • Deficiency of aldehyde reductase
  • Deficiency of aldonolactonase
  • Deficiency of aldose 1-epimerase
  • Deficiency of alpha-amylase
  • Deficiency of alpha-mannosidase
  • Deficiency of amylase
  • Deficiency of amylo-1,6-glucosidase
  • Deficiency of amylopectin 6-glucanohydrolase
  • Deficiency of benzaldehyde dehydrogenase
  • Deficiency of beta-amylase
  • Deficiency of beta-fructofuranosidase
  • Deficiency of beta-glucosidase
  • Deficiency of beta-glucuronidase
  • Deficiency of bisphosphoglycerate mutase
  • Deficiency of bisphosphoglycerate phosphatase
  • Deficiency of endo-1,3-beta-glucanase
  • Deficiency of glucan 1,3-alpha-glucosidase
  • Deficiency of glucokinase
  • Deficiency of gluconate 2-dehydrogenase
  • Deficiency of gluconokinase
  • Deficiency of gluconolactonase
  • Deficiency of glucosamine-6-phosphate isomerase
  • Deficiency of glucose dehydrogenase
  • Deficiency of glucose oxidase
  • Deficiency of glucose-1-phosphatase
  • Deficiency of glucose-6-phosphate isomerase
  • Deficiency of glucosyltransferase 1
  • Deficiency of glyceraldehyde-3-phosphate dehydrogenase
  • Deficiency of glycerol kinase
  • Deficiency of glycosidase
  • Deficiency of glycosulfatase
  • Deficiency of glycosyltransferase
  • Deficiency of maltose phosphorylase
  • Deficiency of mannokinase
  • Deficiency of phosphoglucokinase
  • Deficiency of phosphoglycerate kinase
  • Deficiency of phosphomannomutase 2
  • Deficiency of phosphorylase b kinase
  • Deficiency of protein kinase
  • Deficiency of rhamnulokinase
  • Deficiency of xylulokinase
  • D-Glyceric aciduria
  • Disacchariduria
  • Disorder of glucose metabolism
  • Disorder of glucose regulation
  • Disorder of glycerate metabolism
  • Disorder of glycerol metabolism
  • Essential pentosuria
  • Genetically determined myasthenia
  • Glycerol intolerance syndrome
  • Glycerol kinase deficiency - isolated
  • Glycogen storage disease due to phosphoglycerate kinase 1 deficiency
  • Hyperimmunoglobulin E syndrome
  • Mannosyl-oligosaccharide glycosidase congenital disorder of glycosylation
  • Muscle phosphoglycerate mutase deficiency
  • Nonglucosuric melituria
  • Pentose disorder
  • PGM1-related congenital disorder of glycosylation
  • PGM3-related congenital disorder of glycosylation
  • SLC35A1 congenital disorder of glycosylation
  • SLC39A8 congenital disorder of glycosylation
  • Solute carrier family 35 member A2 congenital disorder of glycosylation
  • Syndrome of carbohydrate intolerance
  • Trehalase deficiency
  • Xylosuria
  • XYLT1-CDG - xylosyltransferase 1 congenital disorder of glycosylation

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Essential pentosuria

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Disorder(of)
      • carbohydrate
        • metabolism (congenital)
          • specified NEC
    • Disorder(of)
      • congenital glycosylation (CDG)
    • Disorder(of)
      • metabolism NOS
        • carbohydrate
          • specified NEC
    • Pentosuria(essential)

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR END016
Other specified and unspecified nutritional and metabolic disorders
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Disacchariduria

    a laboratory test result which indicates the presence of disaccharides in the urine.

  • Congenital Myasthenic Syndrome

    a group of rare genetic neuromuscular disorders characterized by neuromuscular junction defects. the defects are classified as presynaptic, synaptic, or postsynaptic. signs and symptoms include muscle weakness, easy fatigability, feeding and respiratory difficulties, and scoliosis.

  • Congenital Myasthenic Syndrome 12|CMS12

    an autosomal recessive form of congenital myasthenic syndrome caused by mutation(s) in the gfpt1 gene, encoding glutamine--fructose-6-phosphate aminotransferase 1.

  • Congenital Myasthenic Syndrome 5|CMS5|EAD|Endplate Acetylcholinesterase Deficiency

    congenital myasthenic syndrome caused by mutation(s) in the colq gene, encoding acetylcholinesterase collagenic tail peptide. it is inherited in an autosomal recessive manner.

  • Congenital Myasthenic Syndrome-4C|CMS4C|Myasthenic Syndrome, Congenital, 4C, Associated with Acetylcholine Receptor Deficiency

    an autosomal recessive form of congenital myasthenic syndrome caused by mutation(s) in the chrne gene, encoding acetylcholine receptor subunit epsilon.

  • Presynaptic Congenital Myasthenic Syndrome 6|CMS6

    congenital myasthenic syndrome caused by mutation(s) in the chat gene, encoding choline o-acetyltransferase. it is inherited in an autosomal recessive manner.

Patient EducationClinical

Metabolic Disorders

Metabolism is the process your body uses to get or make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system break the food parts down into sugars and acids, your body's fuel.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code History & ChangesHistory

Replacement E74.89 replaces the following previously assigned code(s):

  • E74.8 - Other specified disorders of carbohydrate metabolism
FY 2021AddedAdded to the ICD-10-CM code setEffective October 1, 2020.
FY 2022–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About E74.89Overview

Is E74.89 (Other specified disorders of carbohydrate metabolism) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other specified disorders of carbohydrate metabolism on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.