2026 ICD-10-CM Diagnosis Code Q44.2Atresia of bile ducts

ICD-10-CM Codes›Q00-Q99›Q38-Q45›Q44

ICD-10-CM Q44.2
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q44.2 is a billable ICD-10-CM diagnosis code for atresia of bile ducts. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 444 through 446. The code is exempt from POA reporting. Coders also document this condition as atresia of hepatic ducts. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Digestive congenital anomalies.

Code Identity

ICD-10-CM Code
Q44.2
Billable Status
Yes — Valid for Submission
Code Describes
Atresia of bile ducts
Short Description
Atresia of bile ducts
Same as the full description in the CMS dataset.
Parent Code
Q44
Congenital malformations of gallbladder, bile ducts and liver

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ38-Q45Other congenital malformations of the digestive system
CategoryQ44Congenital malformations of gallbladder, bile ducts and liver
This CodeQ44.2Atresia of bile ducts

Present on Admission (POA)Billing

Q44.2 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Atresia of hepatic ducts
  • Biliary atresia with splenic malformation syndrome
  • Congenital atresia of extrahepatic bile duct
  • Congenital biliary atresia
  • Ichthyosis congenita with biliary atresia
  • Intrahepatic biliary atresia

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Atresia, atretic
      • bile duct (common) (congenital) (hepatic)
    • Atresia, atretic
      • common duct
    • Atresia, atretic
      • cystic duct
    • Impervious(congenital)
      • bile duct

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL002
Digestive congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Bile Duct Diseases

Your liver makes a digestive juice called bile. Your gallbladder stores it between meals. When you eat, your gallbladder pushes the bile into tubes called bile ducts. They carry the bile to your small intestine. The bile helps break down fat. It also helps the liver get rid of toxins and wastes.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q44.2 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
751.61 Biliary atresia
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q44.2Overview

Is Q44.2 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report atresia of bile ducts on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q44.2 group to?

When atresia of bile ducts is the principal diagnosis on an inpatient stay, it groups to MS-DRG 444, 445, 446, with relative weights from 0.8273 to 1.6709 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q44.2 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for atresia of bile ducts on inpatient claims.

What is the ICD-9 equivalent of Q44.2?

Under the General Equivalence Mappings, atresia of bile ducts converts to ICD-9-CM 751.61 (biliary atresia). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.