2026 ICD-10-CM Diagnosis Code Q41.9Congenital absence, atresia and stenosis of small intestine, part unspecified

ICD-10-CM Codes›Q00-Q99›Q38-Q45›Q41

ICD-10-CM Q41.9
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q41.9 is a billable ICD-10-CM diagnosis code for congenital absence, atresia and stenosis of small intestine, part unspecified. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 393 through 395. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Digestive congenital anomalies.

Code Identity

ICD-10-CM Code
Q41.9
Billable Status
Yes — Valid for Submission
Code Describes
Congenital absence, atresia and stenosis of small intestine, part unspecified
Short Description
Congen absence, atresia and stenosis of sm int, part unsp
Parent Code
Q41
Congenital absence, atresia and stenosis of small intestine

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ38-Q45Other congenital malformations of the digestive system
CategoryQ41Congenital absence, atresia and stenosis of small intestine
This CodeQ41.9Congenital absence, atresia and stenosis of small intestine, part unspecified

Present on Admission (POA)Billing

Q41.9 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Complete congenital duodenal obstruction
  • Complete obstruction of intestine
  • Complete obstruction of lumen of small intestine
  • Congenital absence of intestinal tract
  • Congenital absence of small intestine
  • Congenital absence, atresia and stenosis of small intestine
  • Congenital atresia of intestinal tract
  • Congenital atresia of intestine at multiple levels
  • Congenital atresia of small intestine
  • Congenital duodenal obstruction
  • Congenital hypoplasia of gallbladder
  • Congenital hypoplasia of intestinal tract
  • Congenital hypoplasia of pancreas
  • Congenital hypoplasia of small intestine
  • Congenital obstruction of small intestine
  • Congenital stenosis of intestinal tract
  • Congenital stenosis of small intestine
  • Fetal gastrointestinal abnormality
  • Fetal intrauterine intestinal perforation with congenital atresia of intestinal tract
  • Fetal intrauterine perforation of intestine
  • Hypoplasia of pancreas, intestinal atresia, hypoplasia of gallbladder syndrome
  • Isolated multiple intestinal atresia
  • Neonatal intestinal perforation co-occurrent and due to intestinal atresia
  • Neonatal perforation of intestine due to congenital stenosis of intestine
  • Small intestine atresia and stenosis
  • Ulceration of umbilical cord and atresia of intestine syndrome

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Congenital absence, atresia and stenosis of intestine NOS

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Absence(of) (organ or part) (complete or partial)
      • intestine (acquired) (small)
        • congenital
    • Agenesis
      • intestine (small)
    • Atresia, atretic
      • intestine (small)
    • Hypoplasia, hypoplastic
      • intestine (small)
    • Impervious(congenital)
      • intestine (small)
    • Obstruction, obstructed, obstructive
      • intestine
        • congenital (small)
    • Stenosis, stenotic(cicatricial)
      • intestine
        • congenital (small)
    • Stricture
      • intestine
        • congenital (small)

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL002
Digestive congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q41.9 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
751.1 Atresia small intestine
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q41.9Overview

Is Q41.9 (Congenital absence, atresia and stenosis of small intestine) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital absence, atresia and stenosis of small intestine, part unspecified on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q41.9 group to?

When congenital absence, atresia and stenosis of small intestine, part unspecified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 393, 394, 395, with relative weights from 0.6490 to 1.5993 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q41.9 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital absence, atresia and stenosis of small intestine, part unspecified on inpatient claims.

What is the ICD-9 equivalent of Q41.9?

Under the General Equivalence Mappings, congenital absence, atresia and stenosis of small intestine, part unspecified converts to ICD-9-CM 751.1 (atresia small intestine). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.