2026 ICD-10-CM Diagnosis Code Q39.1Atresia of esophagus with tracheo-esophageal fistula
ICD-10-CM Codes›Q00-Q99›Q38-Q45›Q39
- Billable — Valid for Submission
- POA Exempt
- Chronic Condition
Q39.1 is a billable ICD-10-CM diagnosis code for atresia of esophagus with tracheo-esophageal fistula. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 368 through 370. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Digestive congenital anomalies.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q39.1 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Agenesis of esophagus
- Atresia of esophagus with esophagobronchial fistula
- Broncho-esophageal fistula
- Congenital absence of esophagus
- Congenital absence of esophagus with tracheo-esophageal fistula
- Congenital atresia of esophagus
- Congenital esophageal fistula
- Congenital esophagobronchial fistula
- Congenital esophagotracheal fistula
- Congenital tracheal fistula
- Esophageal atresia with tracheo-esophageal fistula
- Esophageal atresia, stenosis and fistula
- Tracheoesophageal fistula
Tabular List NotesGuidance
Coding notes and annotation back-references applicable to this code.
Inclusion Terms
- Atresia of esophagus with broncho-esophageal fistula
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
- with tracheoesophageal fistula - Q39.1
- with tracheoesophageal fistula - Q39.1
- congenital - Q39.2
- with atresia of esophagus - Q39.1
- congenital - Q39.2
- with atresia of esophagus - Q39.1
- congenital - Q39.2
- with atresia of esophagus - Q39.1
- congenital - Q39.2
- with atresia of esophagus - Q39.1
- congenital - Q39.2
- with atresia of esophagus - Q39.1
- Imperforate (congenital) - See Also: Atresia;
- with tracheoesophageal fistula - Q39.1
- Impervious (congenital) - See Also: Atresia;
- with tracheoesophageal fistula - Q39.1
External Cause of Injuries IndexGuidance
References for this code in the External Cause of Injuries Index.
- Atresia, atretic
- esophagus
- with tracheoesophageal fistula
- Atresia, atretic
- gullet
- with tracheoesophageal fistula
- Fistula(cutaneous)
- bronchoesophageal
- congenital
- with atresia of esophagus
- Fistula(cutaneous)
- esophagobronchial
- congenital
- with atresia of esophagus
- Fistula(cutaneous)
- esophagotracheal
- congenital
- with atresia of esophagus
- Fistula(cutaneous)
- esophagus
- congenital
- with atresia of esophagus
- Fistula(cutaneous)
- tracheoesophageal
- congenital
- with atresia of esophagus
- Imperfect
- closure (congenital)
- esophagus with communication to bronchus or trachea
- Imperforate(congenital)
- esophagus
- with tracheoesophageal fistula
- Impervious(congenital)
- esophagus
- with tracheoesophageal fistula
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Tracheoesophageal Fistula
abnormal passage between the esophagus and the trachea, acquired or congenital, often associated with esophageal atresia.
Patient EducationClinical
Birth Defects
A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.
The full article covers:
- What are birth defects?
- What causes birth defects?
- Who is at risk of having a baby with birth defects?
- How are birth defects diagnosed?
- What are the treatments for birth defects?
- Can birth defects be prevented?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q39.1 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q39.1Overview
Is Q39.1 (Congenital malformations of esophagus) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report atresia of esophagus with tracheo-esophageal fistula on HIPAA-covered claims from October 1, 2025 through September 30, 2026.
What MS-DRG does Q39.1 group to?
When atresia of esophagus with tracheo-esophageal fistula is the principal diagnosis on an inpatient stay, it groups to MS-DRG 368, 369, 370, with relative weights from 0.7008 to 1.5919 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q39.1 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for atresia of esophagus with tracheo-esophageal fistula on inpatient claims.
What is the ICD-9 equivalent of Q39.1?
Under the General Equivalence Mappings, atresia of esophagus with tracheo-esophageal fistula converts to ICD-9-CM 750.3 (cong esoph fistula/atres). The mapping is approximate, so confirm the match fits the documentation.
Footnotes
[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:
- The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
- The condition places limitations on self-care, independent living, and social interactions.
