2024 ICD-10-CM Diagnosis Code Q40.0

Congenital hypertrophic pyloric stenosis

ICD-10-CM Code:
Q40.0
ICD-10 Code for:
Congenital hypertrophic pyloric stenosis
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities
    (Q00-Q99)
    • Other congenital malformations of the digestive system
      (Q38-Q45)
      • Other congenital malformations of upper alimentary tract
        (Q40)

Q40.0 is a billable diagnosis code used to specify a medical diagnosis of congenital hypertrophic pyloric stenosis. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024. The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Congenital constriction of pylorus
  • Congenital hypertrophic pyloric stenosis
  • Congenital hypertrophy of pylorus
  • Congenital junctional epidermolysis bullosa
  • Congenital junctional epidermolysis bullosa-pyloric atresia syndrome
  • Congenital pyloric spasm
  • Congenital pyloric stenosis
  • Congenital stenosis of stomach
  • Congenital stenosis of stomach
  • Congenital stenosis of stomach
  • Gastric atresia
  • Generalized junctional epidermolysis bullosa
  • Intellectual disability, hypotonia, brachycephaly, pyloric stenosis, cryptorchidism syndrome
  • Pyloric antral stenosis
  • Pyloric atresia
  • Pyloric obstruction
  • Pyloric stenosis
  • Pyloric stenosis
  • Pyloric stenosis
  • Pyloric stenosis
  • Pylorospasm
  • Pylorospasm

Clinical Classification

Clinical Information

  • Pyloric Stenosis

    narrowing of the pyloric canal with varied etiology. a common form is due to muscle hypertrophy (pyloric stenosis, hypertrophic) seen in infants.
  • Pyloric Stenosis, Hypertrophic

    narrowing of the pyloric canal due to hypertrophy of the surrounding circular muscle. it is usually seen in infants or young children.
  • Hypertrophy

    general increase in bulk of a part or organ due to cell enlargement and accumulation of fluids and secretions, not due to tumor formation, nor to an increase in the number of cells (hyperplasia).

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Congenital or infantile constriction
  • Congenital or infantile hypertrophy
  • Congenital or infantile spasm
  • Congenital or infantile stenosis
  • Congenital or infantile stricture

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Present on Admission (POA)

Q40.0 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here.

CMS POA Indicator Options and Definitions

POA IndicatorReason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Convert Q40.0 to ICD-9-CM

  • ICD-9-CM Code: 750.5 - Cong pyloric stenosis

Patient Education


Stomach Disorders

Your stomach is an organ between your esophagus and small intestine. It is where digestion of protein begins. The stomach has three tasks. It stores swallowed food. It mixes the food with stomach acids. Then it sends the mixture on to the small intestine.

Most people have a problem with their stomach at one time or another. Indigestion and heartburn are common problems. You can relieve some stomach problems with over-the-counter medicines and lifestyle changes, such as avoiding fatty foods or eating more slowly. Other problems like peptic ulcers or GERD require medical attention.

You should see a doctor if you have any of the following:

  • Blood when you have a bowel movement
  • Severe abdominal pain
  • Heartburn not relieved by antacids
  • Unintended weight loss
  • Ongoing vomiting or diarrhea

NIH: National Institute of Diabetes and Digestive and Kidney Diseases


[Learn More in MedlinePlus]

Uncommon Infant and Newborn Problems

It can be scary when your baby is sick, especially when it is not an everyday problem like a cold or a fever. You may not know whether the problem is serious or how to treat it. If you have concerns about your baby's health, call your health care provider right away.

Learning information about your baby's condition can help ease your worry. Do not be afraid to ask questions about your baby's care. By working together with your health care provider, you make sure that your baby gets the best care possible.


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.