2026 ICD-10-CM Diagnosis Code Q26.6Portal vein-hepatic artery fistula

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q26

ICD-10-CM Q26.6
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q26.6 is a billable ICD-10-CM diagnosis code for portal vein-hepatic artery fistula. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 299 through 301. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q26.6
Billable Status
Yes — Valid for Submission
Code Describes
Portal vein-hepatic artery fistula
Short Description
Portal vein-hepatic artery fistula
Same as the full description in the CMS dataset.
Parent Code
Q26
Congenital malformations of great veins

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ26Congenital malformations of great veins
This CodeQ26.6Portal vein-hepatic artery fistula

Present on Admission (POA)Billing

Q26.6 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Portal vein-hepatic artery fistula

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Fistula(cutaneous)
      • hepatic artery-portal vein, congenital
    • Fistula(cutaneous)
      • portal vein-hepatic artery, congenital
    • Malformation(congenital)
      • great
        • vein
          • portal vein-hepatic artery fistula

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Arteriovenous Malformations

Arteriovenous malformations (AVMs) are defects in your vascular system. Your vascular system is your body's network of blood vessels. It includes your:

The full article covers:

  • What are arteriovenous malformations (AVMs)?
  • What causes arteriovenous malformations (AVMs)?
  • What are the symptoms of arteriovenous malformations (AVMs)?
  • How are arteriovenous malformations (AVMs) diagnosed?
  • What are the treatments for arteriovenous malformations (AVMs)?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q26.6 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.61 Gstrontest vesl anomaly
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q26.6Overview

Is Q26.6 (Congenital malformations of great veins) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report portal vein-hepatic artery fistula on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q26.6 group to?

When portal vein-hepatic artery fistula is the principal diagnosis on an inpatient stay, it groups to MS-DRG 299, 300, 301, with relative weights from 0.7197 to 1.6327 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q26.6 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for portal vein-hepatic artery fistula on inpatient claims.

What is the ICD-9 equivalent of Q26.6?

Under the General Equivalence Mappings, portal vein-hepatic artery fistula converts to ICD-9-CM 747.61 (gstrontest vesl anomaly). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.