2027 ICD-10-CM Diagnosis Code Q25.3Supravalvular aortic stenosis
ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q25
- Billable — Valid for Submission
- CC — Complication or Comorbidity
- POA Exempt
- Chronic Condition
Q25.3 is a billable ICD-10-CM diagnosis code for supravalvular aortic stenosis. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 306 through 307. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 55 closely related codes. The code is exempt from POA reporting. Coders also document this condition as atresia and stenosis of aorta. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q25.3 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of the circulatory system (Q20-Q28).
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Atresia and stenosis of aorta
- Coarctation of aortic arch
- Congenital stenosis of aorta
- Congenital supravalvular aortic stenosis
- Postductal aortic stenosis
- Postductal coarctation of aorta
- Preductal aortic stenosis
- Preductal coarctation of aorta
- Stenosis of thoracic aorta
- Supravalvar aortic stenosis
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to Q25.3: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
Notes
General instructions on how these codes are used.
- Codes from this chapter are not for use on maternal records
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name Q25.3, its category, or a range that includes it.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Malformation (congenital) See Also: Anomaly;
supravalvular Q25.3
Stenosis, stenotic (cicatricial) See Also: Stricture;
Stricture See Also: Stenosis;
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Aortic Stenosis, Supravalvular
a pathological constriction occurring in the region above the aortic valve. it is characterized by restricted outflow from the left ventricle into the aorta.
Patient EducationClinical
Congenital Heart Defects
Congenital heart defects (CHDs) are problems with the structure of the heart. "Congenital" means that that the problems are present at birth. These defects happen when a fetus's heart doesn't develop normally during pregnancy. Congenital heart defects are the most common type of birth defect.
The full article covers:
- What are congenital heart defects?
- What causes congenital heart defects?
- Who is more likely to have a baby with a congenital heart defect?
- What are the symptoms of congenital heart defects?
- What other problems do congenital heart defects cause?
- How are congenital heart defects diagnosed?
- What are the treatments for congenital heart defects?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q25.3 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q25.3Overview
What is the ICD-10 code for supravalvular aortic stenosis?
The ICD-10-CM code for supravalvular aortic stenosis is Q25.3 (sometimes written as Q253). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is Q25.3 (Congenital malformations of great arteries) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report supravalvular aortic stenosis on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does Q25.3 group to?
When supravalvular aortic stenosis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 306, 307, with relative weights from 0.9146 to 1.5457 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q25.3 a CC or MCC?
CMS lists Q25.3 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 55 closely related codes in its exclusion list.
Is Q25.3 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for supravalvular aortic stenosis on inpatient claims. The code appears in the Congenital malformations of the circulatory system (Q20-Q28) range of the CMS exempt list.
