2027 ICD-10-CM Diagnosis Code Q25.29Other atresia of aorta

ICD-10-CM Codes›Q00-Q99›Q20-Q28›Q25

ICD-10-CM Q25.29
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q25.29 is a billable ICD-10-CM diagnosis code for other atresia of aorta. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 306 through 307. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 55 closely related codes. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Cardiac and circulatory congenital anomalies.

Code Identity

ICD-10-CM Code
Q25.29
Billable Status
Yes — Valid for Submission
Code Describes
Other atresia of aorta
Short Description
Other atresia of aorta
Same as the full description in the CMS dataset.
Parent Code
Atresia of aorta

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ20-Q28Congenital malformations of the circulatory system
CategoryQ25Congenital malformations of great arteries
This CodeQ25.29Other atresia of aorta

Present on Admission (POA)Billing

Q25.29 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of the circulatory system (Q20-Q28).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Aortic arch hypoplasia between subclavian and common carotid arteries
  • Ascending aortic atresia
  • Atresia and stenosis of aorta
  • Atresia of aortic arch with fibrous cord
  • Atresia of aortic arch with fibrous cord between left common carotid artery and right common carotid artery
  • Atresia of aortic arch with fibrous cord between subclavian artery and common carotid artery
  • Atresia of aortic arch with fibrous cord distal to subclavian artery
  • Congenital atresia of aorta
  • Congenital atresia of aortic arch
  • Congenital hypoplasia of aortic arch
  • Congenital luminal atresia of aortic arch between left common carotid artery and right common carotid artery
  • Congenital luminal atresia of aortic arch between subclavian artery and common carotid artery
  • Congenital luminal atresia of aortic arch distal to subclavian artery
  • Congenital stenosis of aorta
  • Developmental malformation of branchial arch
  • Double aortic arch with left arch dominant
  • Double aortic arch with left arch dominant and atresia of right arch
  • Double aortic arch with right arch dominant
  • Double aortic arch with right arch dominant and atresia of left arch
  • Double aortic arch with right arch dominant and atresia of left arch and left ligament to diverticulum
  • Muscular subvalvar atresia of aorta
  • Persisting fifth aortic arch
  • Persisting fifth aortic arch with atresia of fourth arch

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q25.29: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Atresia of aorta

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL001
Cardiac and circulatory congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Congenital Heart Defects

Congenital heart defects (CHDs) are problems with the structure of the heart. "Congenital" means that that the problems are present at birth. These defects happen when a fetus's heart doesn't develop normally during pregnancy. Congenital heart defects are the most common type of birth defect.

The full article covers:

  • What are congenital heart defects?
  • What causes congenital heart defects?
  • Who is more likely to have a baby with a congenital heart defect?
  • What are the symptoms of congenital heart defects?
  • What other problems do congenital heart defects cause?
  • How are congenital heart defects diagnosed?
  • What are the treatments for congenital heart defects?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q25.29 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
747.22 Aortic atresia/stenosis
Approximate The match is approximate rather than exact.

Code History & ChangesHistory

Replacement Q25.29 replaces the following previously assigned code(s):

  • Q25.2 - Atresia of aorta
FY 2019AddedAdded to the ICD-10-CM code setEffective October 1, 2018.
FY 2020–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q25.29Overview

What is the ICD-10 code for other atresia of aorta?

The ICD-10-CM code for other atresia of aorta is Q25.29 (sometimes written as Q2529). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q25.29 (Atresia of aorta) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other atresia of aorta on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q25.29 group to?

When other atresia of aorta is the principal diagnosis on an inpatient stay, it groups to MS-DRG 306, 307, with relative weights from 0.9146 to 1.5457 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q25.29 a CC or MCC?

CMS lists Q25.29 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 55 closely related codes in its exclusion list.

Is Q25.29 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other atresia of aorta on inpatient claims. The code appears in the Congenital malformations of the circulatory system (Q20-Q28) range of the CMS exempt list.