2026 ICD-10-CM Diagnosis Code Q07.8Other specified congenital malformations of nervous system

ICD-10-CM Codes›Q00-Q99›Q00-Q07›Q07

ICD-10-CM Q07.8
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q07.8 is a billable ICD-10-CM diagnosis code for other specified congenital malformations of nervous system. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Nervous system congenital anomalies.

Code Identity

ICD-10-CM Code
Q07.8
Billable Status
Yes — Valid for Submission
Code Describes
Other specified congenital malformations of nervous system
Short Description
Other specified congenital malformations of nervous system
Same as the full description in the CMS dataset.
Parent Code
Q07
Other congenital malformations of nervous system

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ00-Q07Congenital malformations of the nervous system
CategoryQ07Other congenital malformations of nervous system
This CodeQ07.8Other specified congenital malformations of nervous system

Present on Admission (POA)Billing

Q07.8 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Abnormality of neurogenesis
  • Adhesion of brain meninges
  • Adhesion of meninges
  • Aganglionosis of parasympathetic nerve ganglia
  • Agenesis of nerve
  • Aplasia of optic nerve
  • Brachial plexus displacement
  • Cataract, congenital heart disease, neural tube defect syndrome
  • Cerebro-oculo-facio-skeletal syndrome
  • Cerebrooculonasal syndrome
  • Cochlear nerve disorder
  • Congenital absence of myelination of peripheral nerve
  • Congenital achiasma
  • Congenital adhesions of brain meninges
  • Congenital anomaly of cochlea
  • Congenital anomaly of macula
  • Congenital anomaly of membranous labyrinth
  • Congenital anomaly of optic nerve
  • Congenital anomaly of visual system
  • Congenital deficiency of cochlear nerve
  • Congenital degeneration of nervous system
  • Congenital disorder of facial nerve
  • Congenital hypomyelinating neuropathy
  • Congenital hypoplasia of cerebral hemisphere
  • Congenital hypoplasia of corticospinal tract
  • Congenital hypoplasia of fovea centralis
  • Congenital hypoplasia of macula lutea
  • Congenital hypoplasia of olfactory tract
  • Congenital hypoplasia of optic tract
  • Congenital hypoplasia of retina
  • Congenital hypoplasia of vestibular nerve
  • Congenital indifference to pain
  • Congenital ischemic atrophy of central nervous system structure
  • Congenital malformation of the meninges
  • Congenital spastic foot
  • Deafness, encephaloneuropathy, obesity, valvulopathy syndrome
  • Developmental displacement of brachial plexus
  • Disorder of neuronal migration and differentiation
  • Disorder of optic tract
  • Ectopic glial tissue
  • FBXL4-related encephalomyopathic mitochondrial DNA depletion syndrome
  • Finding of pain tolerance
  • Foveal hypoplasia, optic nerve decussation defect, anterior segment dysgenesis syndrome
  • Hydranencephaly
  • Immature ganglionosis of large intestine
  • Indifference to pain
  • Isolated aplasia of optic nerve
  • MARCH syndrome
  • Marinesco-Sjögren syndrome
  • Mega cisterna magna
  • Mitochondrial DNA depletion syndrome encephalomyopathic form
  • Mitochondrial DNA depletion syndrome, encephalomyopathic form with variable craniofacial anomalies
  • Neuroectodermal melanolysosomal disease
  • Neuronal choristoma
  • Neuronal heterotopia
  • Polycystic lipomembranous osteodysplasia with sclerosing leukoencephalopathy
  • Port-wine nevi, mega cisterna magna, hydrocephalus syndrome
  • Port-wine stain of skin
  • RRM2B-related mitochondrial DNA depletion syndrome, encephalomyopathic form with renal tubulopathy
  • Schisis association syndrome
  • Spastic foot
  • X-linked periventricular heterotopia

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Agenesis of nerve
  • Displacement of brachial plexus
  • Jaw-winking syndrome
  • Marcus Gunn's syndrome

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Accessory(congenital)
      • nervous system, part NEC
    • Adhesions, adhesive(postinfective)
      • meninges (cerebral) (spinal)
        • congenital
    • Agenesis
      • nerve
    • Agenesis
      • nervous system, part NEC
    • Agenesis
      • nuclear
    • Anomaly, anomalous(congenital) (unspecified type)
      • acoustic nerve
    • Anomaly, anomalous(congenital) (unspecified type)
      • choroid
        • plexus
    • Anomaly, anomalous(congenital) (unspecified type)
      • meningeal bands or folds
        • constriction of
    • Anomaly, anomalous(congenital) (unspecified type)
      • nerve
        • acoustic
    • Anomaly, anomalous(congenital) (unspecified type)
      • nerve
        • optic
    • Anomaly, anomalous(congenital) (unspecified type)
      • optic
        • nerve
    • Anomaly, anomalous(congenital) (unspecified type)
      • sense organs NEC
    • Anomaly, anomalous(congenital) (unspecified type)
      • spine, spinal NEC
        • nerve root
    • Deformity
      • choroid (congenital)
        • plexus
    • Displacement, displaced
      • brachial plexus (congenital)
    • Distortion(s) (congenital)
      • nerve
    • Gunn's syndrome
    • Jaw-winking phenomenon or syndrome
    • Malformation(congenital)
      • choroid (congenital)
        • plexus
    • Malformation(congenital)
      • spinal
        • nerve root
    • Malposition
      • congenital
        • brachial plexus
    • Malposition
      • congenital
        • nerve
    • Malposition
      • congenital
        • nervous system NEC
    • Marcus Gunn's syndrome
    • Phenomenon
      • jaw-winking
    • Syndrome
      • jaw-winking

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL004
Nervous system congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Hydranencephaly

    a congenital condition where the greater portions of the cerebral hemispheres and corpus striatum are replaced by csf and glial tissue. the meninges and the skull are well formed, which is consistent with earlier normal embryogenesis of the telencephalon. bilateral occlusions of the internal carotid arteries in utero is a potential mechanism. clinical features include intact brainstem reflexes without evidence of higher cortical activity. (menkes, textbook of child neurology, 5th ed, p307)

  • Multinucleated Neurons, Anhydramnios, Renal Dysplasia, Cerebellar Hypoplasia and Hydranencephaly|MARCH

    a lethal autosomal recessive condition caused by mutation(s) in the cep55 gene, encoding centrosomal protein of 55 kda. it is characterized by renal dysplasia, anhydramnios, hydrancephaly, cerebellar hypoplasia, and multinucleated neurons in remaining brain tissue.

  • Hydranencephaly

    a rare congenital brain disorder in which the cerebral hemispheres are absent and replaced by sacs that contain cerebrospinal fluid. signs and symptoms include irritability, increased muscle tone, seizures, and hydrocephalus. the prognosis is poor.

  • Multinucleated Neurons, Anhydramnios, Renal Dysplasia, Cerebellar Hypoplasia And Hydranencephaly|MARCH

    a lethal autosomal recessive condition caused by mutation(s) in the cep55 gene, encoding centrosomal protein of 55 kda. it is characterized by renal dysplasia, anhydramnios, hydrancephaly, cerebellar hypoplasia, and multinucleated neurons in remaining brain tissue.

Patient EducationClinical

Brain Malformations

Most brain malformations begin long before a baby is born. Something damages the developing nervous system or causes it to develop abnormally. Sometimes it's a genetic problem. In other cases, exposure to certain medicines, infections, or radiation during pregnancy interferes with brain development.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q07.8 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
742.8 Nervous system anom NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q07.8Overview

Is Q07.8 (Other congenital malformations of nervous system) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other specified congenital malformations of nervous system on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Is Q07.8 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other specified congenital malformations of nervous system on inpatient claims.

What is the ICD-9 equivalent of Q07.8?

Under the General Equivalence Mappings, other specified congenital malformations of nervous system converts to ICD-9-CM 742.8 (nervous system anom NEC). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.