2026 ICD-10-CM Diagnosis Code G31.01Pick's disease

ICD-10-CM Codes›G00–G99›G30-G32›G31

ICD-10-CM G31.01
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

G31.01 is a billable ICD-10-CM diagnosis code for Pick's disease. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Neurocognitive disorders.

Code Identity

ICD-10-CM Code
G31.01
Billable Status
Yes — Valid for Submission
Code Describes
Pick's disease
Short Description
Pick's disease
Same as the full description in the CMS dataset.
Parent Code
G31.0
Frontotemporal dementia

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG30-G32Other degenerative diseases of the nervous system
CategoryG31Other degenerative diseases of nervous system, not elsewhere classified
This CodeG31.01Pick's disease

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Altered behavior due to Pick's disease
  • Alzheimer's disease with progressive aphasia
  • Circumscribed atrophy of brain
  • Dementia due to Pick's disease
  • Logopenic progressive aphasia
  • Pick's disease with Pick bodies
  • Pick's disease with Pick cells and no Pick bodies
  • Primary progressive non fluent aphasia
  • Progressive aphasia

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Primary progressive aphasia
  • Progressive isolated aphasia

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Aphasia(amnestic) (global) (nominal) (semantic) (syntactic)
      • primary progressive
    • Aphasia(amnestic) (global) (nominal) (semantic) (syntactic)
      • primary progressive
        • with behavioral disturbance
    • Aphasia(amnestic) (global) (nominal) (semantic) (syntactic)
      • progressive isolated
    • Aphasia(amnestic) (global) (nominal) (semantic) (syntactic)
      • progressive isolated
        • with behavioral disturbance
    • Atrophy, atrophic(of)
      • brain (cortex) (progressive)
        • frontotemporal circumscribed
    • Atrophy, atrophic(of)
      • brain (cortex) (progressive)
        • frontotemporal circumscribed
          • with behavioral disturbance
    • Dementia(degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety)
      • in (due to)
        • Pick's
    • Dementia(degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety)
      • in (due to)
        • Pick's
          • with behavioral disturbance
    • Disease, diseased
      • Pick's
    • Disease, diseased
      • Pick's
        • with behavioral disturbance
    • Disease, diseased
      • Pick's
        • brain
    • Disease, diseased
      • Pick's
        • brain
          • with behavioral disturbance
    • Pick's
      • cerebral atrophy
    • Pick's
      • cerebral atrophy
        • with behavioral disturbance
    • Pick's
      • disease or syndrome (brain)
    • Pick's
      • disease or syndrome (brain)
        • with behavioral disturbance
    • Pick's
      • disease or syndrome (brain)
        • brain
    • Pick's
      • disease or syndrome (brain)
        • brain
          • with behavioral disturbance
    • Pick's
      • syndrome
        • brain
    • Pick's
      • syndrome
        • brain
          • with behavioral disturbance

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS011
Neurocognitive disorders
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Frontotemporal Dementia

    the most common clinical form of frontotemporal lobar degeneration, this dementia presents with personality and behavioral changes often associated with disinhibition, apathy, and lack of insight.

  • Frontotemporal Lobar Degeneration

    heterogeneous group of neurodegenerative disorders characterized by frontal and temporal lobe atrophy associated with neuronal loss, gliosis, and dementia. patients exhibit progressive changes in social, behavioral, and/or language function. multiple subtypes or forms are recognized based on presence or absence of tau protein inclusions. ftld includes three clinical syndromes: frontotemporal dementia, semantic dementia, and primary progressive nonfluent aphasia.

  • Amyotrophic Lateral Sclerosis 10, with or without Frontotemporal Dementia|ALS10

    an autosomal dominant form of amyotrophic lateral sclerosis caused by mutation(s) in the tardbp gene, encoding tar dna-binding protein 43.

  • Amyotrophic Lateral Sclerosis 14, with or without Frontotemporal Dementia|ALS14

    a form of amyotrophic lateral sclerosis caused by heterozygous mutation(s) in the vcp gene, encoding transitional endoplasmic reticulum atpase.

  • Amyotrophic Lateral Sclerosis 15, with or without Frontotemporal Dementia|ALS15

    an x-linked dominant form of amyotrophic lateral sclerosis caused by mutation(s) in the ubqln2 gene, encoding ubiquilin-2.

  • Amyotrophic Lateral Sclerosis 26, with or without Frontotemporal Dementia|ALS26

    an autosomal dominant form of amyotrophic lateral sclerosis caused by mutation(s) in the tia1 gene, encoding cytotoxic granule associated rna binding protein tia1.

  • Amyotrophic Lateral Sclerosis 6, with or without Frontotemporal Dementia|ALS6

    a form of amyotrophic lateral sclerosis caused by heterozygous mutation(s) in the fus gene, encoding rna-binding protein fus.

  • Frontotemporal Dementia and/or Amyotrophic Lateral Sclerosis 2|FTDALS2

    an autosomal dominant form of frontotemporal dementia and/or amyotrophic lateral sclerosis caused by mutation(s) in the chchd10 gene, encoding coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial.

  • Frontotemporal Dementia and/or Amyotrophic Lateral Sclerosis 4|FTDALS4

    an autosomal dominant form of frontotemporal dementia and/or amyotrophic lateral sclerosis caused by mutation(s) in the tbk1 gene, encoding serine/threonine-protein kinase tbk1.

  • Frontotemporal Dementia and/or Amyotrophic Lateral Sclerosis 7|FTDALS7

    an autosomal dominant form of frontotemporal dementia and/or amyotrophic lateral sclerosis caused by mutation(s) in the chmp2b gene, encoding charged multivesicular body protein 2b.

  • Frontotemporal Dementia-1|FTD1|FTDP17|Frontotemporal Dementia 1|Frontotemporal Dementia with Parkinsonism-17

    an autosomal dominant subtype of frontotemporal dementia caused by mutation(s) in the mapt gene, encoding microtubule-associated protein tau.

  • Amyotrophic Lateral Sclerosis 10, With or Without Frontotemporal Dementia|ALS10

    an autosomal dominant form of amyotrophic lateral sclerosis caused by mutation(s) in the tardbp gene, encoding tar dna-binding protein 43.

  • Amyotrophic Lateral Sclerosis 14, With or Without Frontotemporal Dementia|ALS14

    a form of amyotrophic lateral sclerosis caused by heterozygous mutation(s) in the vcp gene, encoding transitional endoplasmic reticulum atpase.

  • Amyotrophic Lateral Sclerosis 6, With or Without Frontotemporal Dementia|ALS6

    a form of amyotrophic lateral sclerosis caused by heterozygous mutation(s) in the fus gene, encoding rna-binding protein fus.

  • Frontotemporal Dementia

    a syndrome caused by progressive degeneration of the frontal or temporal lobes of the brain. it is manifested with personality changes and deterioration of the language skills.

  • Frontotemporal Dementia and/or Amyotrophic Lateral Sclerosis 1|FTDALS1

    an autosomal dominant condition caused by heterozygous hexanucleotide repeat expansion in a noncoding region of the c9orf72 gene , encoding guanine nucleotide exchange c9orf72. it is characterized by amyotrophic lateral sclerosis with frontotemporal dementia.

  • Inclusion Body Myopathy with Early-Onset Paget Disease with or without Frontotemporal Dementia 1|IBMPFD1

    a rare autosomal dominant inherited disorder caused by mutations in the vcp gene. it can affect the muscles, bones, and brain. patients may develop myopathy that initially involves the muscles of the hips and shoulders and as the disorder progresses it may affect the cardiac and respiratory muscles, leading to life-threatening cardiac and pulmonary failure. approximately half of the adults develop paget disease of bone, and approximately one-third develop frontotemporal dementia.

  • Other Frontotemporal Dementia|Other frontotemporal dementia

    evidence of other frontotemporal dementia not specified elsewhere.

Patient EducationClinical

Dementia

Dementia is a loss of mental functions that is severe enough to affect your daily life and activities. These functions include:

The full article covers:

  • What is dementia?
  • What are the types of dementia?
  • Who is at risk for dementia?
  • What are the symptoms of dementia?
  • How is dementia diagnosed?
  • What are the treatments for dementia?
  • Can dementia be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert G31.01 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
331.11 Pick's disease
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About G31.01Overview

Is G31.01 (Frontotemporal dementia) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report Pick's disease on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What is the ICD-9 equivalent of G31.01?

Under the General Equivalence Mappings, Pick's disease converts to ICD-9-CM 331.11 (Pick's disease). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.