ICD-10-CM Code G31.89

Other specified degenerative diseases of nervous system

Version 2021 Billable Code

Valid for Submission

G31.89 is a billable code used to specify a medical diagnosis of other specified degenerative diseases of nervous system. The code is valid for the fiscal year 2021 for the submission of HIPAA-covered transactions. The ICD-10-CM code G31.89 might also be used to specify conditions or terms like 3-methylglutaconic aciduria, 3-methylglutaconic aciduria type 4, 3-methylglutaconic aciduria type iv with sensorineural deafness, encephalopathy and leigh-like syndrome, acute cerebellar syndrome, argyrophilic grain disease, arteriopathic granular atrophy of cerebral cortex, etc

Short Description:Other specified degenerative diseases of nervous system
Long Description:Other specified degenerative diseases of nervous system

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code G31.89 are found in the index:


The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • 3-Methylglutaconic aciduria
  • 3-Methylglutaconic aciduria type 4
  • 3-methylglutaconic aciduria type IV with sensorineural deafness, encephalopathy and Leigh-like syndrome
  • Acute cerebellar syndrome
  • Argyrophilic grain disease
  • Arteriopathic granular atrophy of cerebral cortex
  • Autosomal dominant striatal neurodegeneration
  • Autosomal recessive cerebral atrophy
  • Beta-propeller protein-associated neurodegeneration
  • Cerebellar ataxia associated with another disorder
  • Cerebellar deficiency syndrome
  • Cerebral degeneration in childhood
  • Chorea co-occurrent and due to dentatorubropallidoluysian degeneration
  • Chronic hepatocerebral degeneration
  • Coenzyme A synthase protein associated neurodegeneration
  • Congenital cerebellar cortical atrophy
  • Congenital microcephaly, severe encephalopathy, progressive cerebral atrophy syndrome
  • Corneal cerebellar syndrome
  • Corticostriatal-spinal degeneration
  • Cystic degeneration of brain
  • Dentatorubropallidoluysian degeneration
  • Diffuse cerebral and cerebellar atrophy, intractable seizures, progressive microcephaly syndrome
  • Disorder of valine metabolism
  • Early-onset progressive neurodegeneration, blindness, ataxia, spasticity syndrome
  • Fatal post-viral neurodegenerative disorder
  • Fatty acid hydroxylase associated neurodegeneration
  • Genetic lipodystrophy
  • Hereditary acantholytic dermatosis
  • Hereditary cerebellar atrophy
  • Hereditary cerebellar atrophy
  • Hereditary cerebellar atrophy
  • Hereditary degenerative disease of central nervous system
  • Huntington disease-like 1
  • Huntington disease-like 3
  • Huntington disease-like syndrome
  • Huntington disease-like syndrome due to C9ORF72 expansions
  • Hypomyelinating leukodystrophy with atrophy of basal ganglia and cerebellum
  • Inborn error of amino acid metabolism
  • Infantile cerebral and cerebellar atrophy with postnatal progressive microcephaly
  • Infantile neuroaxonal dystrophy
  • Infantile spasms, psychomotor retardation, progressive brain atrophy, basal ganglia disease syndrome
  • Juvenile cerebellar degeneration AND myoclonus
  • Keratosis follicularis, dwarfism, cerebral atrophy syndrome
  • Kufor Rakeb syndrome
  • Late cortical cerebellar atrophy
  • Late infantile and juvenile neuroaxonal dystrophy
  • Mitochondrial membrane protein associated neurodegeneration
  • Neuroaxonal dystrophy
  • Neurodegeneration due to 3-hydroxyisobutyryl coenzyme A hydrolase deficiency
  • Olivopontocerebellar atrophy and deafness
  • Olivopontocerebellar degeneration
  • PRKAR1B-related neurodegenerative dementia with intermediate filaments
  • Progressive encephalopathy with edema, hypsarrhythmia, and optic atrophy-like syndrome
  • Progressive neuronal degeneration of childhood
  • Progressive neuronal degeneration without liver cirrhosis
  • Severe neurodegenerative syndrome with lipodystrophy
  • Sporadic cerebellar degeneration
  • Synucleinopathy
  • TUBB4A-related leukodystrophy
  • X-linked neurodegenerative syndrome Bertini type
  • X-linked neurodegenerative syndrome Hamel type

Convert G31.89 to ICD-9

  • 331.89 - Cereb degeneration NEC (Approximate Flag)

Code Classification

  • Diseases of the nervous system (G00–G99)
    • Other degenerative diseases of the nervous system (G30-G32)
      • Oth degenerative diseases of nervous system, NEC (G31)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021

Information for Patients

Degenerative Nerve Diseases

Also called: Neurodegenerative diseases

Degenerative nerve diseases affect many of your body's activities, such as balance, movement, talking, breathing, and heart function. Many of these diseases are genetic. Sometimes the cause is a medical condition such as alcoholism, a tumor, or a stroke. Other causes may include toxins, chemicals, and viruses. Sometimes the cause is not known.

Degenerative nerve diseases include

  • Alzheimer's disease
  • Amyotrophic lateral sclerosis
  • Friedreich's ataxia
  • Huntington's disease
  • Lewy body disease
  • Parkinson's disease
  • Spinal muscular atrophy

Degenerative nerve diseases can be serious or life-threatening. It depends on the type. Most of them have no cure. Treatments may help improve symptoms, relieve pain, and increase mobility.

  • Multiple system atrophy (Medical Encyclopedia)
  • Progressive multifocal leukoencephalopathy (Medical Encyclopedia)

[Learn More]