2026 ICD-10-CM Diagnosis Code E83.822ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2

ICD-10-CM Codes›E00–E89›E70-E88›E83

ICD-10-CM E83.822
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

E83.822 is a billable ICD-10-CM diagnosis code for ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026).

Code Identity

ICD-10-CM Code
E83.822
Billable Status
Yes — Valid for Submission
Code Describes
ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2
Short Description
ENPP1 def cause autosom recess hypophosphate rickets type 2
Parent Code
E83.82
Disorders of pyrophosphate metabolism

Code Classification

ChapterE00–E89Endocrine, nutritional and metabolic diseases
SectionE70-E88Metabolic disorders
CategoryE83Disorders of mineral metabolism
This CodeE83.822ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Deficiency, deficient
      • ENPP1
        • causing
          • autosomal recessive hypophosphatemic rickets type 2

Code History & ChangesHistory

New Code E83.822 was added to the ICD-10-CM code set for FY 2026, effective October 1, 2025.

Replacement E83.822 replaces the following previously assigned code(s):

  • E83.89 - Other disorders of mineral metabolism
FY 2026AddedAdded to the ICD-10-CM code setEffective October 1, 2025.
FY 2026CurrentRevised in the current code setEffective October 1, 2025 through September 30, 2026.

Questions About E83.822Overview

Is E83.822 (Disorders of pyrophosphate metabolism) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2 on HIPAA-covered claims from October 1, 2025 through September 30, 2026.