2026 ICD-10-CM Diagnosis Code E75.19Other gangliosidosis
ICD-10-CM Codes›E00–E89›E70-E88›E75
- Billable — Valid for Submission
- Chronic Condition
E75.19 is a billable ICD-10-CM diagnosis code for other gangliosidosis. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). Coders also document this condition as adult GM1 gangliosidosis. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other nervous system disorders (often hereditary or degenerative) and Other specified and unspecified nutritional and metabolic disorders.
Code Identity
Code Classification
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Adult GM1 gangliosidosis
- GM1 gangliosidosis
- Infantile GM1 gangliosidosis
- Juvenile GM1 gangliosidosis
Tabular List NotesGuidance
Coding notes and annotation back-references applicable to this code.
Inclusion Terms
- GM1 gangliosidosis
- GM3 gangliosidosis
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
- Gangliosidosis - E75.10
External Cause of Injuries IndexGuidance
References for this code in the External Cause of Injuries Index.
- Gangliosidosis
- GM1
- Gangliosidosis
- GM3
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
GM1 Gangliosidosis
an autosomal recessive lysosomal storage disease characterized by deficiency of the enzyme acid beta-galactosidase, resulting in the accumulation of acid lipids in the nervous system. signs and symptoms include neurologic disturbances, muscle atrophy, dystonia, eye abnormalities, and formation of angiokeratomas.
Patient EducationClinical
Genetic Brain Disorders
A genetic brain disorder is caused by a variation or a mutation in a gene. A variation is a different form of a gene. A mutation is a change in a gene. Genetic brain disorders affect the development and function of the brain.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert E75.19 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About E75.19Overview
Is E75.19 (Other and unspecified gangliosidosis) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report other gangliosidosis on HIPAA-covered claims from October 1, 2025 through September 30, 2026.
What is the ICD-9 equivalent of E75.19?
Under the General Equivalence Mappings, other gangliosidosis converts to ICD-9-CM 330.1 (cerebral lipidoses). The mapping is approximate, so confirm the match fits the documentation.
Footnotes
[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:
- The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
- The condition places limitations on self-care, independent living, and social interactions.
