2026 ICD-10-CM Diagnosis Code D44.7Neoplasm of uncertain behavior of aortic body and other paraganglia

ICD-10-CM Codes›C00–D49›D37-D48›D44

ICD-10-CM D44.7
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

D44.7 is a billable ICD-10-CM diagnosis code for neoplasm of uncertain behavior of aortic body and other paraganglia. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Neoplasms of unspecified nature or uncertain behavior.

Code Identity

ICD-10-CM Code
D44.7
Billable Status
Yes — Valid for Submission
Code Describes
Neoplasm of uncertain behavior of aortic body and other paraganglia
Short Description
Neoplasm of uncrt behav of aortic body and oth paraganglia
Parent Code
D44
Neoplasm of uncertain behavior of endocrine glands

Code Classification

ChapterC00–D49Neoplasms
SectionD37-D48Neoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes
CategoryD44Neoplasm of uncertain behavior of endocrine glands
This CodeD44.7Neoplasm of uncertain behavior of aortic body and other paraganglia

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Carney Stratakis syndrome
  • Extra-adrenal paraganglioma
  • Glomus tympanicum tumor
  • Hereditary pheochromocytoma and paraganglioma
  • Multiple paraganglioma associated with polycythemia
  • Neoplasm of aortic body
  • Neoplasm of glomus jugulare
  • Neoplasm of para-aortic body
  • Neoplasm of uncertain behavior of aortic body
  • Neoplasm of uncertain behavior of autonomic nervous system
  • Neoplasm of uncertain behavior of glomus jugulare
  • Neoplasm of uncertain behavior of para-aortic body
  • Neoplasm of uncertain behavior of paraganglia
  • Non-functioning paraganglioma
  • Paraganglioma
  • Sporadic pheochromocytoma and secreting paraganglioma

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Paraganglioma
    • Paraganglioma
      • aortic body
    • Paraganglioma
      • extra-adrenal
    • Paraganglioma
      • extra-adrenal
        • unspecified site
    • Paraganglioma
      • glomus jugulare
    • Paraganglioma
      • jugular
    • Paraganglioma
      • nonchromaffin
    • Paraganglioma
      • nonchromaffin
        • unspecified site
    • Paraganglioma
      • parasympathetic
    • Paraganglioma
      • parasympathetic
        • unspecified site
    • Paraganglioma
      • sympathetic
    • Paraganglioma
      • sympathetic
        • unspecified site
    • Paraganglioma
      • unspecified site
    • Tumor
      • aortic body
    • Tumor
      • glomus
        • jugulare

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NEO072
Neoplasms of unspecified nature or uncertain behavior
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Glomus Tympanicum Tumor

    a rare paraganglioma involving the glomus tympanicum, a collection of chemoreceptor tissue adjacent to the tympanic cavity. it can cause tinnitus and conductive hearing loss (hearing loss, conductive).

  • Carotid Body Tumor

    benign paraganglioma at the bifurcation of the common carotid arteries. it can encroach on the parapharyngeal space and produce dysphagia, pain, and cranial nerve palsies.

  • Glomus Jugulare Tumor

    a paraganglioma involving the glomus jugulare, a microscopic collection of chemoreceptor tissue in the adventitia of the bulb of the jugular vein. it may cause paralysis of the vocal cords, attacks of dizziness, blackouts, and nystagmus. it is not resectable but radiation therapy is effective. it regresses slowly, but permanent control is regularly achieved. (from dorland, 27th ed; stedman, 25th ed; devita jr et al., cancer: principles & practice of oncology, 3d ed, pp1603-4)

  • Paraganglioma

    a neural crest tumor usually derived from the chromoreceptor tissue of a paraganglion, such as the carotid body, or medulla of the adrenal gland (usually called a chromaffinoma or pheochromocytoma). it is more common in women than in men. (stedman, 25th ed; from segen, dictionary of modern medicine, 1992)

  • Paraganglioma, Extra-Adrenal

    a relatively rare, usually benign neoplasm originating in the chemoreceptor tissue of the carotid body; glomus jugulare; glomus tympanicum; aortic bodies; and the female genital tract. it consists histologically of rounded or ovoid hyperchromatic cells that tend to be grouped in an alveolus-like pattern within a scant to moderate amount of fibrous stroma and a few large thin-walled vascular channels. (from stedman, 27th ed)

  • Carotid Artery, Common

    the two principal arteries supplying the structures of the head and neck. they ascend in the neck, one on each side, and at the level of the upper border of the thyroid cartilage, each divides into two branches, the external (carotid artery, external) and internal (carotid artery, internal) carotid arteries.

Table of NeoplasmsClinical

Anatomical sites in the Table of Neoplasms that reference this code family.

SiteMalig.
Primary		Malig.
Secondary		Ca
in situ		BenignUncertainUnspec.
aortic bodyC75.5C79.89–D35.6D44.7D49.7
glomus › jugularisC75.5C79.89–D35.6D44.7D49.7
organ of ZuckerkandlC75.5C79.89–D35.6D44.7D49.7
para-aortic bodyC75.5C79.89–D35.6D44.7D49.7
paraganglion NECC75.5C79.89–D35.6D44.7D49.7
Zuckerkandl organC75.5C79.89–D35.6D44.7D49.7

Patient EducationClinical

Endocrine Diseases

Your endocrine system includes eight major glands throughout your body. These glands make hormones. Hormones are chemical messengers. They travel through your bloodstream to tissues or organs. Hormones work slowly and affect body processes from head to toe. These include:

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert D44.7 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
237.3 Unc behav neo paragang
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About D44.7Overview

Is D44.7 (Neoplasm of uncertain behavior of endocrine glands) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report neoplasm of uncertain behavior of aortic body and other paraganglia on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What is the ICD-9 equivalent of D44.7?

Under the General Equivalence Mappings, neoplasm of uncertain behavior of aortic body and other paraganglia converts to ICD-9-CM 237.3 (unc behav neo paragang). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Not chronic - A diagnosis code that does not fit the criteria for chronic condition (duration, ongoing medical treatment, and limitations) is considered not chronic. Some codes designated as not chronic are acute conditions. Other diagnosis codes that indicate a possible chronic condition, but for which the duration of the illness is not specified in the code description (i.e., we do not know the condition has lasted 12 months or longer) also are considered not chronic.