ICD-10-CM Tabular Index · Chapter 2 · FY 2027 D47

Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue (D47) ICD-10-CM

The D47 code range covers other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue with 14 ICD-10-CM diagnosis codes. 11 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.

✓ Built from the official CMS FY 2027 datasetEffective Oct 1, 2026 – Sep 30, 2027
14
Diagnosis Codes
11
Billable Codes
D47
Code Range
D37–D48
Parent Section
ICD-10-CM

Codes in the D47 Range 14 codes · 11 billable

14 of 14 shown
  • D47 Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissueNon-billable
  • D47.0 Mast cell neoplasms of uncertain behaviorNon-billable
  • D47.01 Cutaneous mastocytosis
  • D47.02 Systemic mastocytosis
  • D47.09 Other mast cell neoplasms of uncertain behavior
  • D47.1 Chronic myeloproliferative disease
  • D47.2 Monoclonal gammopathy
  • D47.3 Essential (hemorrhagic) thrombocythemia
  • D47.4 Osteomyelofibrosis
  • D47.9 Neoplasm of uncertain behavior of lymphoid, hematopoietic and related tissue, unspecified
  • D47.Z Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissueNon-billable
  • D47.Z1 Post-transplant lymphoproliferative disorder (PTLD)
  • D47.Z2 Castleman disease
  • D47.Z9 Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue

Clinical Terms in This Code Range

Definitions from the National Library of Medicine for conditions coded in the D47 range.

Castleman Disease

Large benign, hyperplastic lymph nodes. The more common hyaline vascular subtype is characterized by small hyaline vascular follicles and interfollicular capillary proliferations. Plasma cells are often present and represent another subtype with the plasma cells containing IgM and IMMUNOGLOBULIN A.

Hematopoietic and Lymphoid System Neoplasm

A benign or malignant (primary or metastatic) neoplasm that affects the hematopoietic and lymphatic system.

Mastocytoma

A solid tumor consisting of a dense infiltration of MAST CELLS. It is generally benign.

Mastocytosis

A rare neoplastic disorder characterized by a clonal proliferation of MAST CELLS, associated with KIT-D816 mutations, and accompanied by aberrant mast cell activation. The abnormal increase of MAST CELLS may occur in only the skin (MASTOCYTOSIS, CUTANEOUS), in extracutaneous tissues involving multiple organs (MASTOCYTOSIS, SYSTEMIC), or in solid tumors (MASTOCYTOMA).

Mastocytosis, Cutaneous

Skin lesions due to abnormal infiltration of MAST CELLS. Cutaneous mastocytosis is confined to the skin without the involvement of other tissues or organs, and is mostly found in children. The three major variants are: URTICARIA PIGMENTOSA; diffuse cutaneous mastocytosis; and SOLITARY MASTOCYTOMA OF SKIN.

Mastocytosis, Systemic

A group of disorders caused by the abnormal proliferation of MAST CELLS in a variety of extracutaneous tissues including bone marrow, liver, spleen, lymph nodes, and gastrointestinal tract. Systemic mastocytosis is commonly seen in adults. These diseases are categorized on the basis of clinical features, pathologic findings, and prognosis.

Myelofibrosis

A partial or complete replacement of the bone marrow stroma by fibrous tissue. It can be a primary bone marrow lesion as part of the chronic myeloproliferative disorders (chronic idiopathic myelofibrosis), a manifestation of acute myeloid leukemia (acute panmyelosis with myelofibrosis), or a secondary phenomenon due to bone marrow involvement by a metastatic tumor (e.g., metastatic breast carcinoma). --2003

Myeloproliferative Neoplasm

A group of myeloid neoplasms that includes the following: chronic myeloid leukemia, BCR-ABL1 positive; polycythemia vera; essential thrombocythemia; primary myelofibrosis; chronic neutrophilic leukemia; chronic eosinophilic leukemia, not otherwise specified; and myeloproliferative neoplasm, unclassifiable.

Post-Transplant Lymphoproliferative Disorder

Post-transplant lymphoproliferative disorder (PTLD) is a polyclonal (benign) or clonal (malignant) proliferation of lymphoid cells that develops as a consequence of immunosuppression in a recipient of a solid organ or bone marrow allograft. PTLDs comprise a spectrum ranging from early, Epstein-Barr virus (EBV)-driven polyclonal lymphoid proliferations to EBV-positive or EBV- negative lymphomas of predominantly B-cell or less often T-cell type. (WHO, 2001)

Thrombocythemia, Essential

A clinical syndrome characterized by repeated spontaneous hemorrhages and a remarkable increase in the number of circulating platelets.

About the D47 Code Range

These are growths of uncertain behavior involving lymphoid, blood-forming, or related tissue.

D47.0 separates mast cell conditions into cutaneous mastocytosis, which affects the skin, systemic mastocytosis, and other mast cell neoplasms. Other subdivisions name chronic myeloproliferative disease, monoclonal gammopathy, essential thrombocythemia, and osteomyelofibrosis.

D47.Z separates post-transplant lymphoproliferative disorder, Castleman disease, and other specified neoplasms. D47.9 identifies an unspecified neoplasm in these tissues.

Questions About This Page

How many billable codes are in the D47 range?

Of the 14 codes in this range, 11 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.

What does the D47 range classify?

The range classifies other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.

Related References

Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.