2026 ICD-10-CM Diagnosis Code Q89.3Situs inversus

ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q89

ICD-10-CM Q89.3
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q89.3 is a billable ICD-10-CM diagnosis code for situs inversus. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 393 through 395. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.

Code Identity

ICD-10-CM Code
Q89.3
Billable Status
Yes — Valid for Submission
Code Describes
Situs inversus
Short Description
Situs inversus
Same as the full description in the CMS dataset.
Parent Code
Q89
Other congenital malformations, not elsewhere classified

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ80-Q89Other congenital malformations
CategoryQ89Other congenital malformations, not elsewhere classified
This CodeQ89.3Situs inversus

Present on Admission (POA)Billing

Q89.3 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Agnathia, holoprosencephaly, situs inversus syndrome
  • Atrial situs inversus
  • Complete situs inversus with dextrocardia
  • Congenital malposition of heart
  • Dextrocardia
  • Dextrocardia/situs inversus finding
  • Immotile cilia syndrome
  • Kartagener syndrome
  • Laterality sequence
  • Situs inversus abdominalis
  • Situs inversus thoracis
  • Situs inversus viscerum
  • Situs inversus with levocardia

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Dextrocardia with situs inversus
  • Mirror-image atrial arrangement with situs inversus
  • Situs inversus or transversus abdominalis
  • Situs inversus or transversus thoracis
  • Transposition of abdominal viscera
  • Transposition of thoracic viscera

Type 1 Excludes

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Dextrocardia(true)
      • with
        • complete transposition of viscera
    • Dextrocardia(true)
      • with
        • situs inversus
    • Kartagener's syndrome or triad(sinusitis, bronchiectasis, situs inversus)
    • Levocardia(isolated)
      • with situs inversus
    • Malposition
      • congenital
        • heart
          • dextrocardia
            • with complete transposition of viscera
    • Sinusitis-bronchiectasis-situs inversus(syndrome) (triad)
    • Situs inversus or transversus(abdominalis) (thoracis)
    • Syndrome
      • Kartagener's
    • Syndrome
      • sinusitis-bronchiectasis-situs inversus
    • Transposition(congenital)
      • abdominal viscera
    • Transposition(congenital)
      • heart
        • with complete transposition of viscera
    • Transposition(congenital)
      • stomach
        • with general transposition of viscera
    • Transposition(congenital)
      • viscera (abdominal) (thoracic)
    • Triad
      • Kartagener's

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL010
Other specified and unspecified congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Levocardia

    congenital abnormalities in which the heart is in the normal position (levocardia) in the left side of the chest but some or all of the thorax or abdomen viscera are transposed laterally (situs inversus). it is also known as situs inversus with levocardia, or isolated levocardia. this condition is often associated with severe heart defects and splenic abnormalities such as asplenia or polysplenia.

  • Situs Inversus

    a congenital abnormality in which organs in the thorax and the abdomen are opposite to their normal positions (situs solitus) due to lateral transposition. normally the stomach and spleen are on the left, liver on the right, the three-lobed right lung is on the right, and the two-lobed left lung on the left. situs inversus has a familial pattern and has been associated with a number of genes related to microtubule-associated proteins.

  • Dextrocardia

    a congenital defect in which the heart is located on the right side of the thorax instead of on the left side (levocardia, the normal position). when dextrocardia is accompanied with inverted heart atria, a right-sided stomach, and a left-sided liver, the combination is called dextrocardia with situs inversus. dextrocardia may adversely affect other thoracic organs.

  • Kartagener Syndrome

    an autosomal recessive disorder characterized by a triad of dextrocardia; infertility; and sinusitis. the syndrome is caused by mutations of dynein genes encoding motility proteins which are components of sperm tails, and cilia in the respiratory and the reproductive tracts.

  • Kartagener Syndrome

    a rare autosomal recessive inherited syndrome characterized by situs inversus, bronchiectasis, and chronic sinusitis. there is a defect in the function of the cilia that line the respiratory tract.

  • Situs Inversus Thoracis

    a congenital condition in which there is complete right-to-left reversal of the position of the thoracic organs.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q89.3 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
759.3 Situs inversus
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q89.3Overview

Is Q89.3 (Other congenital malformations, not elsewhere classified) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report situs inversus on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q89.3 group to?

When situs inversus is the principal diagnosis on an inpatient stay, it groups to MS-DRG 393, 394, 395, with relative weights from 0.6490 to 1.5993 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q89.3 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for situs inversus on inpatient claims.

What is the ICD-9 equivalent of Q89.3?

Under the General Equivalence Mappings, situs inversus converts to ICD-9-CM 759.3 (situs inversus). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.